{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,7,30]],"date-time":"2025-07-30T15:16:06Z","timestamp":1753888566017},"reference-count":10,"publisher":"Georg Thieme Verlag KG","issue":"01","license":[{"start":{"date-parts":[[2020,11,9]],"date-time":"2020-11-09T00:00:00Z","timestamp":1604880000000},"content-version":"vor","delay-in-days":313,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["European J Pediatr Surg Rep"],"published-print":{"date-parts":[[2020,1]]},"abstract":"<jats:title>Abstract<\/jats:title><jats:p>\n          Introduction\u2003Congenital choledochal malformations (CCMs) are characterized by intra- and\/or extrahepatic bile duct dilatation. Five basic types (1\u20135) are recognized in Todani's classification and its modifications, of which types 1 and 4 typically have an associated anomalous pancreatobiliary junction and common channel (CC). We describe two cases with previously undescribed features.<\/jats:p><jats:p>\n          Case Report\u20031 Antenatal detection of a cyst at porta hepatis was made in an otherwise normal girl of Iranian parentage. She was confirmed to be a CCM (20\u2009mm diameter), postnatally, with no evidence of obstruction. Surgical exploration was performed at 12 weeks. She had an isolated cystic dilatation of the right-hepatic duct only. The left-hepatic duct and common bile duct (CBD) were normal without a CC. Histology of the resected specimen showed stratified squamous epithelium.<\/jats:p><jats:p>\n          Case Report 2\u2003A preterm (31 weeks of gestation) boy of Nigerian parentage was presented. His mother was HIV\u2009+\u2009ve and he was treated with nucleoside reverse transcriptase inhibitors following birth. He had persistent cholestatic jaundice and a dilated (10\u2009mm) bile duct from birth. Although the jaundice resolved, the dilatation persisted and increased, coming to surgery aged 2.5 years. This showed cystic dilatation confined to the common hepatic duct, and otherwise normal distal common bile duct and no CC.<\/jats:p><jats:p>\n          Result\u2003Both underwent resection with the Roux-en-Y hepaticojejunostomy reconstruction to the transected right-hepatic duct alone in case 1, leaving the preserved left duct and CBD in continuity, and to the transected common hepatic duct in case 2.<\/jats:p><jats:p>\n          Conclusions\u2003Neither choledochal anomaly fitted into the usual choledochal classification and case 1 appears unique in the literature.<\/jats:p>","DOI":"10.1055\/s-0039-1693998","type":"journal-article","created":{"date-parts":[[2020,11,10]],"date-time":"2020-11-10T00:22:10Z","timestamp":1604967730000},"page":"e86-e89","source":"Crossref","is-referenced-by-count":1,"title":["When It Doesn't Fit: Congenital Anomalies of the Choledochus"],"prefix":"10.1055","volume":"08","author":[{"given":"Helena","family":"Reusens","sequence":"additional","affiliation":[{"name":"Department of Paediatric Surgery, King's College Hospital, London, United Kingdom"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Mark","family":"Davenport","sequence":"additional","affiliation":[{"name":"Department of Paediatric Surgery, King's College Hospital, London, United Kingdom"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"194","published-online":{"date-parts":[[2020,11,9]]},"reference":[{"issue":"09","key":"ref1","doi-asserted-by":"crossref","first-page":"1319","DOI":"10.1002\/bjs.7588","article-title":"Role of pressure and pancreatic reflux in the aetiology of choledochal malformation","volume":"98","author":"C Turowski","year":"2011","journal-title":"Br J Surg"},{"key":"ref2","first-page":"474","article-title":"Atypical cyst of the right ductus hepaticus","volume":"108","author":"I Prekop","year":"2007","journal-title":"Bratisl Lek Listy"},{"key":"ref3","first-page":"788","article-title":"An unusual type of biliar cyst: a case report","volume":"15","author":"A D Gidi","year":"2016","journal-title":"Ann Hepatol"},{"issue":"12","key":"ref4","doi-asserted-by":"crossref","first-page":"e31","DOI":"10.1016\/j.jpedsurg.2005.08.038","article-title":"Management of an epidermoid cyst of the intrahepatic ducts","volume":"40","author":"B Chiu","year":"2005","journal-title":"J Pediatr Surg"},{"issue":"07","key":"ref5","doi-asserted-by":"crossref","first-page":"619","DOI":"10.1177\/1066896917710717","article-title":"Primary epidermoid cyst of biliary duct presenting as choledochal cyst","volume":"25","author":"D H Kwon","year":"2017","journal-title":"Int J Surg Pathol"},{"issue":"10","key":"ref6","doi-asserted-by":"crossref","first-page":"2822","DOI":"10.1007\/s10620-007-0182-x","article-title":"Squamous cell carcinoma arising within a choledochal cyst","volume":"53","author":"L Price","year":"2008","journal-title":"Dig Dis Sci"},{"issue":"09","key":"ref7","doi-asserted-by":"crossref","first-page":"1068","DOI":"10.1002\/bjs.1800780912","article-title":"Spontaneous perforation of the bile duct in infants","volume":"78","author":"M Davenport","year":"1991","journal-title":"Br J Surg"},{"issue":"05","key":"ref8","doi-asserted-by":"crossref","first-page":"465","DOI":"10.1007\/s00383-006-1638-3","article-title":"Idiopathic biliary perforation in a 10-year-old boy","volume":"22","author":"E Makin","year":"2006","journal-title":"Pediatr Surg Int"},{"issue":"09","key":"ref9","doi-asserted-by":"crossref","first-page":"1445","DOI":"10.1016\/j.jpedsurg.2016.03.012","article-title":"Congenital choledochal malformation: search for a marker of epithelial instability","volume":"51","author":"E La Pergola","year":"2016","journal-title":"J Pediatr Surg"},{"issue":"01","key":"ref10","doi-asserted-by":"crossref","first-page":"117","DOI":"10.1007\/s00383-017-4203-3","article-title":"Choledochal malformation: terminology and aetiology","volume":"34","author":"F Parolini","year":"2018","journal-title":"Pediatr Surg Int"}],"container-title":["European Journal of Pediatric Surgery Reports"],"original-title":[],"language":"en","link":[{"URL":"http:\/\/www.thieme-connect.de\/products\/ejournals\/pdf\/10.1055\/s-0039-1693998.pdf","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2020,11,10]],"date-time":"2020-11-10T00:22:18Z","timestamp":1604967738000},"score":1,"resource":{"primary":{"URL":"http:\/\/www.thieme-connect.de\/DOI\/DOI?10.1055\/s-0039-1693998"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2020,1]]},"references-count":10,"journal-issue":{"issue":"01","published-online":{"date-parts":[[2020,1,28]]},"published-print":{"date-parts":[[2020,1]]}},"URL":"https:\/\/doi.org\/10.1055\/s-0039-1693998","relation":{},"ISSN":["2194-7619","2194-7627"],"issn-type":[{"type":"print","value":"2194-7619"},{"type":"electronic","value":"2194-7627"}],"subject":[],"published":{"date-parts":[[2020,1]]}}}