{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,2,21]],"date-time":"2025-02-21T19:43:01Z","timestamp":1740166981344,"version":"3.37.3"},"reference-count":33,"publisher":"Georg Thieme Verlag KG","issue":"01","license":[{"start":{"date-parts":[[2023,10,6]],"date-time":"2023-10-06T00:00:00Z","timestamp":1696550400000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Int Arch Otorhinolaryngol"],"published-print":{"date-parts":[[2024,1]]},"abstract":"<jats:title>Abstract<\/jats:title><jats:p>\n               Introduction\u2003Turner syndrome (TS) affects \u223c 1 in 2,500 live births. The presence of hearing alterations is one of the comorbidities found in this syndrome.<\/jats:p><jats:p>\n               Objective\u2003The present study aimed to evaluate the central auditory abilities in TS and to associate the alterations found with the cytogenetic pattern of the syndrome.<\/jats:p><jats:p>\n               Methods\u2003We included children and adults aged 9 to 39 years old, diagnosed with TS, with numerical or structural alterations of sex chromosomes in their karyotype. A battery of behavioral tests of central auditory processing (CAP) was performed, including a test within the modalities: monoaural low-redundancy, dichotic listening, binaural interaction, and temporal processing (resolution and ordering). We studied auditory skills in the total sample and in the sample stratified by age, divided into groups: G1 (9 to 13 years old), G2 (14 to 19 years old), and G3 (20 to 31 years old). For the association of the cytogenetic pattern, the division was T1 (chromosome monosomy X), and T2 (other TS cytogenetic patterns). Statistical analysis presented data expressed as median and interquartile range for numerical data and as frequency and percentage for categorical data.<\/jats:p><jats:p>\n               Results\u2003We found alterations in four auditory skills in the three age groups, but there was a statistically significant difference between the age groups only in the Gaps in Noise Test (GIN) (p-value\u2009=\u20090.009). Regarding karyotype, a greater number of alterations in the T1 cytogenetic pattern (chromosome monosomy X) was observed in four auditory skills, but without a statistically significant difference.<\/jats:p><jats:p>\n               Conclusion\u2003The alterations found point to an impairment in CAP in TS.<\/jats:p>","DOI":"10.1055\/s-0043-1768141","type":"journal-article","created":{"date-parts":[[2023,10,6]],"date-time":"2023-10-06T22:54:19Z","timestamp":1696632859000},"page":"e50-e56","source":"Crossref","is-referenced-by-count":0,"title":["Behavioral Assessment of Central Auditory Processing in Turner Syndrome"],"prefix":"10.1055","volume":"28","author":[{"ORCID":"https:\/\/orcid.org\/0000-0003-4802-6472","authenticated-orcid":false,"given":"Adriana Fernandes Duarte dos","family":"Santos","sequence":"additional","affiliation":[{"name":"Programa de P\u00f3s-Gradua\u00e7\u00e3o em Cl\u00ednica M\u00e9dica, Faculdade de Medicina UFRJ, Rio de Janeiro, RJ, Brazil"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-8035-6039","authenticated-orcid":false,"given":"Martha Marcela Matos","family":"Bazilio","sequence":"additional","affiliation":[{"name":"Department of Speech Therapy, Faculdade de Medicina UFRJ, Rio de Janeiro, RJ, Brazil"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-3439-9681","authenticated-orcid":false,"given":"Silvana","family":"Frota","sequence":"additional","affiliation":[{"name":"Department of Speech Therapy, Faculdade de Medicina UFRJ, Rio de Janeiro, RJ, Brazil"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-7831-354X","authenticated-orcid":false,"given":"Marilia","family":"Guimar\u00e3es","sequence":"additional","affiliation":[{"name":"Endocrinology Service, Faculdade de Medicina URFJ, Rio de Janeiro, RJ, Brazil"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-8906-0189","authenticated-orcid":false,"given":"Marcia Gon\u00e7alves","family":"Ribeiro","sequence":"additional","affiliation":[{"name":"Pediatrics Department, Faculdade de Medicina UFRJ, Rio de Janeiro, RJ, Brazil"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"194","published-online":{"date-parts":[[2023,10,6]]},"reference":[{"volume-title":"Thompson & Thompson \u2013 Gen\u00e9tica M\u00e9dica. 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Cient."},{"issue":"01","key":"ref32","first-page":"39","article-title":"Auditory processing in children with dyslexia: electrophysiological and behavior evaluation","volume":"25","author":"J C Oliveira","year":"2013","journal-title":"CoDAS"},{"issue":"02","key":"ref33","doi-asserted-by":"crossref","first-page":"65","DOI":"10.7874\/jao.2019.00521","article-title":"Masking Level Difference: Performance of School children aged 7-12 years","volume":"25","author":"N G de Carvalho","year":"2021","journal-title":"J Audiol Otol"},{"key":"ref34","doi-asserted-by":"crossref","first-page":"155","DOI":"10.1016\/j.ijporl.2019.04.010","article-title":"Effect of age on Gaps-In-Noise test in pediatric population","volume":"122","author":"N M Ismaail","year":"2019","journal-title":"Int J Pediatr Otorhinolaryngol"},{"issue":"02","key":"ref35","doi-asserted-by":"crossref","first-page":"226","DOI":"10.1044\/1059-0889(2013\/11-0027)","article-title":"Audiological abnormalities in patients with Turner syndrome","volume":"22","author":"C S Oliveira","year":"2013","journal-title":"Am J Audiol"},{"issue":"09","key":"ref36","doi-asserted-by":"crossref","first-page":"779","DOI":"10.1007\/BF03349257","article-title":"Hearing loss in Turner syndrome: results of a multicentric study","volume":"31","author":"R Bergamaschi","year":"2008","journal-title":"J Endocrinol Invest"}],"container-title":["International Archives of Otorhinolaryngology"],"original-title":[],"language":"en","link":[{"URL":"http:\/\/www.thieme-connect.de\/products\/ejournals\/pdf\/10.1055\/s-0043-1768141.pdf","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2024,11,5]],"date-time":"2024-11-05T14:28:30Z","timestamp":1730816910000},"score":1,"resource":{"primary":{"URL":"http:\/\/www.thieme-connect.de\/DOI\/DOI?10.1055\/s-0043-1768141"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2023,10,6]]},"references-count":33,"journal-issue":{"issue":"01","published-online":{"date-parts":[[2024,2,5]]},"published-print":{"date-parts":[[2024,1]]}},"URL":"https:\/\/doi.org\/10.1055\/s-0043-1768141","archive":["Portico","CLOCKSS"],"relation":{},"ISSN":["1809-9777","1809-4864"],"issn-type":[{"type":"print","value":"1809-9777"},{"type":"electronic","value":"1809-4864"}],"subject":[],"published":{"date-parts":[[2023,10,6]]}}}