{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,6,2]],"date-time":"2026-06-02T13:16:42Z","timestamp":1780406202222,"version":"3.54.1"},"reference-count":17,"publisher":"Elsevier BV","issue":"1","license":[{"start":{"date-parts":[[2001,1,1]],"date-time":"2001-01-01T00:00:00Z","timestamp":978307200000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["The Journal of Pediatrics"],"published-print":{"date-parts":[[2001,1]]},"DOI":"10.1067\/mpd.2001.111837","type":"journal-article","created":{"date-parts":[[2002,7,25]],"date-time":"2002-07-25T04:18:43Z","timestamp":1027570723000},"page":"S56-S61","source":"Crossref","is-referenced-by-count":55,"special_numbering":"S","title":["Long-term management of patients with urea cycle disorders"],"prefix":"10.1067","volume":"138","author":[{"given":"Gerard T.","family":"Berry","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Robert D.","family":"Steiner","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"78","reference":[{"key":"10.1067\/mpd.2001.111837_bib1","first-page":"1187","article-title":"Urea cycle enzymes","author":"Brusilow","year":"1995"},{"key":"10.1067\/mpd.2001.111837_bib2","doi-asserted-by":"crossref","first-page":"127","DOI":"10.1016\/S0065-3101(24)00072-0","article-title":"Urea cycle disorders: diagnosis, pathophysiology, and therapy","volume":"43","author":"Brusilow","year":"1996","journal-title":"Adv Pediatr"},{"key":"10.1067\/mpd.2001.111837_bib3","first-page":"211","article-title":"Urea cycle disorders","author":"Bachmann","year":"1990"},{"key":"10.1067\/mpd.2001.111837_bib4","first-page":"290","article-title":"New approaches to the diagnosis and treatment of inborn errors of urea synthesis","volume":"68","author":"Batshaw","year":"1981","journal-title":"Pediatrics"},{"key":"10.1067\/mpd.2001.111837_bib5","doi-asserted-by":"crossref","first-page":"1387","DOI":"10.1056\/NEJM198206103062303","article-title":"Treatment of inborn errors of urea synthesis: activation of alternative pathways of urea synthesis","volume":"306","author":"Batshaw","year":"1982","journal-title":"N Engl J Med"},{"key":"10.1067\/mpd.2001.111837_bib6","doi-asserted-by":"crossref","first-page":"1630","DOI":"10.1056\/NEJM198406213102503","article-title":"Treatment of episodic hyperammonemia in children with inborn errors of urea synthesis","volume":"310","author":"Brusilow","year":"1984","journal-title":"N Engl J Med"},{"key":"10.1067\/mpd.2001.111837_bib7","doi-asserted-by":"crossref","first-page":"855","DOI":"10.1056\/NEJM199609193351204","article-title":"Long-term treatment of girls with ornithine transcarbamylase deficiency","volume":"335","author":"Maestri","year":"1996","journal-title":"N Engl J Med"},{"key":"10.1067\/mpd.2001.111837_bib8","doi-asserted-by":"crossref","first-page":"101","DOI":"10.1023\/A:1005365825875","article-title":"Alternative pathway therapy for urea cycle disorders","volume":"21","author":"Feillet","year":"1998","journal-title":"J Inherit Metab Dis"},{"key":"10.1067\/mpd.2001.111837_bib9","doi-asserted-by":"crossref","first-page":"1336","DOI":"10.1016\/0026-0495(93)90135-B","article-title":"Restoration of nitrogen homeostasis in a man with ornithine transcarbamylase deficiency","volume":"42","author":"Brusilow","year":"1993","journal-title":"Metabolism"},{"key":"10.1067\/mpd.2001.111837_bib10","doi-asserted-by":"crossref","first-page":"1652","DOI":"10.1056\/NEJM199006073222307","article-title":"Hyperammonemia in women with a mutation at the ornithine carbamyltransferase locus. A cause of postpartum coma","volume":"322","author":"Arn","year":"1990","journal-title":"N Engl J Med"},{"key":"10.1067\/mpd.2001.111837_bib11","doi-asserted-by":"crossref","first-page":"259","DOI":"10.1016\/S0022-3476(05)81200-4","article-title":"Plasma glutamine concentration: a guide to the management of urea cycle disorders","volume":"121","author":"Maestri","year":"1992","journal-title":"J Pediatr"},{"key":"10.1067\/mpd.2001.111837_bib12","doi-asserted-by":"crossref","first-page":"10","DOI":"10.1006\/mgme.1998.2783","article-title":"Blood levels of ammonia and nitrogen scavenging amino acids in patients with inherited hyperammonemia","volume":"66","author":"Tuchman","year":"1999","journal-title":"Mol Genet Metab"},{"key":"10.1067\/mpd.2001.111837_bib13","doi-asserted-by":"crossref","first-page":"1500","DOI":"10.1056\/NEJM198406073102304","article-title":"Neurologic outcome in children with inborn errors of urea synthesis: outcome of urea-cycle enzymyopathies","volume":"310","author":"Msall","year":"1984","journal-title":"N Engl J Med"},{"key":"10.1067\/mpd.2001.111837_bib14","doi-asserted-by":"crossref","first-page":"151","DOI":"10.1023\/A:1005374027693","article-title":"Neurodevelopmental outcome of long-term therapy of urea cycle disorders in Japan","volume":"21","author":"Uchino","year":"1998","journal-title":"J Inherit Metab Dis"},{"key":"10.1067\/mpd.2001.111837_bib15","doi-asserted-by":"crossref","first-page":"1387","DOI":"10.1136\/adc.67.11.1387","article-title":"Intercurrent illness in inborn errors of intermediary metabolism","volume":"67","author":"Dixon","year":"1992","journal-title":"Arch Dis Child"},{"key":"10.1067\/mpd.2001.111837_bib16","doi-asserted-by":"crossref","first-page":"112","DOI":"10.1023\/A:1005317909946","article-title":"Liver transplantation for the treatment of urea cycle disorders","volume":"21","author":"Whitington","year":"1998","journal-title":"J Inherit Metab Dis"},{"key":"10.1067\/mpd.2001.111837_bib17","doi-asserted-by":"crossref","first-page":"S55","DOI":"10.1007\/PL00014323","article-title":"Liver transplantation in urea cycle disorders","volume":"158","author":"Saudubray","year":"1999","journal-title":"Eur J Pediatr"}],"container-title":["The Journal of Pediatrics"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0022347601757393?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0022347601757393?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2024,12,2]],"date-time":"2024-12-02T20:03:02Z","timestamp":1733169782000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S0022347601757393"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2001,1]]},"references-count":17,"journal-issue":{"issue":"1","published-print":{"date-parts":[[2001,1]]}},"alternative-id":["S0022347601757393"],"URL":"https:\/\/doi.org\/10.1067\/mpd.2001.111837","relation":{},"ISSN":["0022-3476"],"issn-type":[{"value":"0022-3476","type":"print"}],"subject":[],"published":{"date-parts":[[2001,1]]}}}