{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,5,15]],"date-time":"2026-05-15T15:21:55Z","timestamp":1778858515626,"version":"3.51.4"},"reference-count":69,"publisher":"Elsevier BV","issue":"9","license":[{"start":{"date-parts":[[2004,2,1]],"date-time":"2004-02-01T00:00:00Z","timestamp":1075593600000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"},{"start":{"date-parts":[[2020,10,14]],"date-time":"2020-10-14T00:00:00Z","timestamp":1602633600000},"content-version":"vor","delay-in-days":6100,"URL":"http:\/\/creativecommons.org\/licenses\/by\/4.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Journal of Biological Chemistry"],"published-print":{"date-parts":[[2004,2]]},"DOI":"10.1074\/jbc.m309232200","type":"journal-article","created":{"date-parts":[[2004,2,20]],"date-time":"2004-02-20T22:08:01Z","timestamp":1077314881000},"page":"7462-7469","source":"Crossref","is-referenced-by-count":113,"title":["Cytochrome c Oxidase Subassemblies in Fibroblast Cultures from Patients Carrying Mutations in COX10, SCO1, or SURF1"],"prefix":"10.1016","volume":"279","author":[{"given":"Si\u00f4n L.","family":"Williams","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Isabelle","family":"Valnot","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Pierre","family":"Rustin","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Jan-Willem","family":"Taanman","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"78","reference":[{"key":"10.1074\/jbc.M309232200_bib1","doi-asserted-by":"crossref","first-page":"325","DOI":"10.1016\/0968-0004(94)90071-X","volume":"19","author":"Calhoun","year":"1994","journal-title":"Trends Biochem. Sci."},{"key":"10.1074\/jbc.M309232200_bib2","doi-asserted-by":"crossref","first-page":"329","DOI":"10.1146\/annurev.biophys.27.1.329","volume":"27","author":"Michel","year":"1998","journal-title":"Annu. Rev. Biophys. Biomol. Struct."},{"key":"10.1074\/jbc.M309232200_bib3","doi-asserted-by":"crossref","first-page":"331","DOI":"10.1017\/S0033583500005588","volume":"23","author":"Saraste","year":"1990","journal-title":"Q. Rev. Biophys."},{"key":"10.1074\/jbc.M309232200_bib4","doi-asserted-by":"crossref","first-page":"1136","DOI":"10.1126\/science.272.5265.1136","volume":"272","author":"Tsukihara","year":"1996","journal-title":"Science"},{"key":"10.1074\/jbc.M309232200_bib5","doi-asserted-by":"crossref","first-page":"151","DOI":"10.1023\/A:1022638013825","volume":"29","author":"Taanman","year":"1997","journal-title":"J. Bioenerg. Biomembr."},{"key":"10.1074\/jbc.M309232200_bib6","doi-asserted-by":"crossref","first-page":"111","DOI":"10.1016\/S0378-1119(01)00385-7","volume":"267","author":"H\u00fcttemann","year":"2001","journal-title":"Gene (Amst.)"},{"key":"10.1074\/jbc.M309232200_bib7","doi-asserted-by":"crossref","first-page":"95","DOI":"10.1016\/S0378-1119(03)00604-8","volume":"312","author":"H\u00fcttemann","year":"2003","journal-title":"Gene (Amst.)"},{"key":"10.1074\/jbc.M309232200_bib8","doi-asserted-by":"crossref","first-page":"8","DOI":"10.1002\/mrd.10327","volume":"66","author":"H\u00fcttemann","year":"2003","journal-title":"Mol. Reprod. Dev."},{"key":"10.1074\/jbc.M309232200_bib9","doi-asserted-by":"crossref","first-page":"53","DOI":"10.1016\/S0378-1119(01)00803-4","volume":"286","author":"Barrientos","year":"2002","journal-title":"Gene (Amst.)"},{"key":"10.1074\/jbc.M309232200_bib10","doi-asserted-by":"crossref","first-page":"309","DOI":"10.1021\/ar0200807","volume":"36","author":"Carr","year":"2003","journal-title":"Acc. Chem. Res."},{"key":"10.1074\/jbc.M309232200_bib11","doi-asserted-by":"crossref","first-page":"2533","DOI":"10.1093\/hmg\/8.13.2533","volume":"8","author":"Tiranti","year":"1999","journal-title":"Hum. Mol. Genet."},{"key":"10.1074\/jbc.M309232200_bib12","doi-asserted-by":"crossref","first-page":"2541","DOI":"10.1093\/hmg\/8.13.2541","volume":"8","author":"Yao","year":"1999","journal-title":"Hum. Mol. Genet."},{"key":"10.1074\/jbc.M309232200_bib13","doi-asserted-by":"crossref","first-page":"337","DOI":"10.1038\/3804","volume":"20","author":"Zhu","year":"1998","journal-title":"Nat. Genet."},{"key":"10.1074\/jbc.M309232200_bib14","doi-asserted-by":"crossref","first-page":"1609","DOI":"10.1086\/302150","volume":"63","author":"Tiranti","year":"1998","journal-title":"Am. J. Hum. Genet."},{"key":"10.1074\/jbc.M309232200_bib15","doi-asserted-by":"crossref","first-page":"374","DOI":"10.1002\/humu.1112","volume":"17","author":"P\u00e9quignot","year":"2001","journal-title":"Hum. Mutat."},{"key":"10.1074\/jbc.M309232200_bib16","doi-asserted-by":"crossref","first-page":"399","DOI":"10.1093\/hmg\/ddg038","volume":"12","author":"Agostino","year":"2003","journal-title":"Hum. Mol. Genet."},{"key":"10.1074\/jbc.M309232200_bib17","doi-asserted-by":"crossref","first-page":"43","DOI":"10.1093\/emboj\/21.1.43","volume":"21","author":"Barrientos","year":"2002","journal-title":"EMBO J."},{"key":"10.1074\/jbc.M309232200_bib18","doi-asserted-by":"crossref","first-page":"333","DOI":"10.1038\/15513","volume":"23","author":"Papadopoulou","year":"1999","journal-title":"Nat. Genet."},{"key":"10.1074\/jbc.M309232200_bib19","doi-asserted-by":"crossref","first-page":"28802","DOI":"10.1074\/jbc.M002741200","volume":"275","author":"Mattatall","year":"2000","journal-title":"J. Biol. Chem."},{"key":"10.1074\/jbc.M309232200_bib20","doi-asserted-by":"crossref","first-page":"10","DOI":"10.1016\/S0014-5793(02)02532-2","volume":"518","author":"McEwan","year":"2002","journal-title":"FEBS Lett."},{"key":"10.1074\/jbc.M309232200_bib21","doi-asserted-by":"crossref","first-page":"65","DOI":"10.1016\/S0014-5793(99)00266-5","volume":"447","author":"Paret","year":"1999","journal-title":"FEBS Lett."},{"key":"10.1074\/jbc.M309232200_bib22","doi-asserted-by":"crossref","first-page":"413","DOI":"10.1007\/BF00267464","volume":"229","author":"Buchwald","year":"1991","journal-title":"Mol. Gen. Genet."},{"key":"10.1074\/jbc.M309232200_bib23","doi-asserted-by":"crossref","first-page":"20531","DOI":"10.1074\/jbc.271.34.20531","volume":"271","author":"Glerum","year":"1996","journal-title":"J. Biol. Chem."},{"key":"10.1074\/jbc.M309232200_bib24","doi-asserted-by":"crossref","first-page":"33191","DOI":"10.1074\/jbc.272.52.33191","volume":"272","author":"Beers","year":"1997","journal-title":"J. Biol. Chem."},{"key":"10.1074\/jbc.M309232200_bib25","doi-asserted-by":"crossref","first-page":"42520","DOI":"10.1074\/jbc.M107077200","volume":"276","author":"Nittis","year":"2001","journal-title":"J. Biol. Chem."},{"key":"10.1074\/jbc.M309232200_bib26","doi-asserted-by":"crossref","first-page":"26780","DOI":"10.1016\/S0021-9258(19)61443-2","volume":"275","author":"Dickinson","year":"2000","journal-title":"J. Biol. Chem."},{"key":"10.1074\/jbc.M309232200_bib27","doi-asserted-by":"crossref","first-page":"19","DOI":"10.1016\/S0014-5793(00)02176-1","volume":"485","author":"Lode","year":"2000","journal-title":"FEBS Lett."},{"key":"10.1074\/jbc.M309232200_bib28","doi-asserted-by":"crossref","first-page":"619","DOI":"10.1074\/jbc.275.1.619","volume":"275","author":"Hiser","year":"2000","journal-title":"J. Biol. Chem."},{"key":"10.1074\/jbc.M309232200_bib29","doi-asserted-by":"crossref","first-page":"31237","DOI":"10.1074\/jbc.M204854200","volume":"277","author":"Carr","year":"2002","journal-title":"J. Biol. Chem."},{"key":"10.1074\/jbc.M309232200_bib30","doi-asserted-by":"crossref","first-page":"795","DOI":"10.1093\/hmg\/9.5.795","volume":"9","author":"Jaksch","year":"2000","journal-title":"Hum. Mol. Genet."},{"key":"10.1074\/jbc.M309232200_bib31","doi-asserted-by":"crossref","first-page":"1440","DOI":"10.1212\/WNL.57.8.1440","volume":"57","author":"Jaksch","year":"2001","journal-title":"Neurology"},{"key":"10.1074\/jbc.M309232200_bib32","first-page":"1104","volume":"67","author":"Valnot","year":"2000","journal-title":"Am. J. Hum. Genet."},{"key":"10.1074\/jbc.M309232200_bib33","doi-asserted-by":"crossref","first-page":"26041","DOI":"10.1016\/S0021-9258(19)74272-0","volume":"268","author":"Saiki","year":"1993","journal-title":"J. Biol. Chem."},{"key":"10.1074\/jbc.M309232200_bib34","first-page":"593","volume":"31","author":"Tzagoloff","year":"1993","journal-title":"Biochem. Mol. Biol. Int."},{"key":"10.1074\/jbc.M309232200_bib35","doi-asserted-by":"crossref","first-page":"133","DOI":"10.1016\/S0014-5793(01)02249-9","volume":"492","author":"Barros","year":"2001","journal-title":"FEBS Lett."},{"key":"10.1074\/jbc.M309232200_bib36","doi-asserted-by":"crossref","first-page":"14220","DOI":"10.1016\/S0021-9258(18)77289-X","volume":"265","author":"Nobrega","year":"1990","journal-title":"J. Biol. Chem."},{"key":"10.1074\/jbc.M309232200_bib37","doi-asserted-by":"crossref","first-page":"19088","DOI":"10.1074\/jbc.272.30.19088","volume":"272","author":"Glerum","year":"1997","journal-title":"J. Biol. Chem."},{"key":"10.1074\/jbc.M309232200_bib38","doi-asserted-by":"crossref","first-page":"1245","DOI":"10.1093\/hmg\/9.8.1245","volume":"9","author":"Valnot","year":"2000","journal-title":"Hum. Mol. Genet."},{"key":"10.1074\/jbc.M309232200_bib39","doi-asserted-by":"crossref","first-page":"2693","DOI":"10.1093\/hmg\/ddg284","volume":"12","author":"Antonicka","year":"2003","journal-title":"Hum. Mol. Genet."},{"key":"10.1074\/jbc.M309232200_bib40","doi-asserted-by":"crossref","first-page":"340","DOI":"10.1006\/mgme.2001.3206","volume":"73","author":"Williams","year":"2001","journal-title":"Mol. Genet. Metab."},{"key":"10.1074\/jbc.M309232200_bib41","doi-asserted-by":"crossref","first-page":"1069","DOI":"10.1038\/labinvest.3780319","volume":"81","author":"Williams","year":"2001","journal-title":"Lab. Investig."},{"key":"10.1074\/jbc.M309232200_bib42","doi-asserted-by":"crossref","first-page":"500","DOI":"10.1126\/science.2814477","volume":"246","author":"King","year":"1989","journal-title":"Science"},{"key":"10.1074\/jbc.M309232200_bib43","doi-asserted-by":"crossref","first-page":"1839","DOI":"10.1093\/hmg\/ddg192","volume":"12","author":"Taanman","year":"2003","journal-title":"Hum. Mol. Genet."},{"key":"10.1074\/jbc.M309232200_bib44","doi-asserted-by":"crossref","first-page":"218","DOI":"10.1006\/abio.1995.1523","volume":"231","author":"Klement","year":"1995","journal-title":"Anal. Biochem."},{"key":"10.1074\/jbc.M309232200_bib45","doi-asserted-by":"crossref","first-page":"16","DOI":"10.1016\/S0006-291X(05)80769-7","volume":"186","author":"Bourgeron","year":"1992","journal-title":"Biochem. Biophys. Res. Commun."},{"key":"10.1074\/jbc.M309232200_bib46","doi-asserted-by":"crossref","first-page":"3","DOI":"10.1016\/0076-6879(69)13005-0","volume":"13","author":"Srere","year":"1969","journal-title":"Methods Enzymol."},{"key":"10.1074\/jbc.M309232200_bib47","doi-asserted-by":"crossref","first-page":"245","DOI":"10.1016\/0076-6879(67)10048-7","volume":"10","author":"Wharton","year":"1967","journal-title":"Methods Enzymol."},{"key":"10.1074\/jbc.M309232200_bib48","doi-asserted-by":"crossref","first-page":"2059","DOI":"10.1002\/elps.1150181131","volume":"18","author":"Zerbetto","year":"1997","journal-title":"Electrophoresis"},{"key":"10.1074\/jbc.M309232200_bib49","doi-asserted-by":"crossref","first-page":"199","DOI":"10.1016\/0925-4439(95)00127-1","volume":"1315","author":"Taanman","year":"1996","journal-title":"Biochim. Biophys. Acta"},{"key":"10.1074\/jbc.M309232200_bib50","doi-asserted-by":"crossref","first-page":"18754","DOI":"10.1016\/S0021-9258(17)46694-4","volume":"268","author":"Taanman","year":"1993","journal-title":"J. Biol. Chem."},{"key":"10.1074\/jbc.M309232200_bib51","doi-asserted-by":"crossref","first-page":"95","DOI":"10.1016\/0925-4439(93)90128-N","volume":"1225","author":"Taanman","year":"1993","journal-title":"Biochim. Biophys. Acta"},{"key":"10.1074\/jbc.M309232200_bib52","doi-asserted-by":"crossref","first-page":"145","DOI":"10.1016\/S0925-4439(97)00061-6","volume":"1362","author":"Marusich","year":"1997","journal-title":"Biochim. Biophys. Acta"},{"key":"10.1074\/jbc.M309232200_bib53","doi-asserted-by":"crossref","first-page":"680","DOI":"10.1038\/227680a0","volume":"227","author":"Laemmli","year":"1970","journal-title":"Nature"},{"key":"10.1074\/jbc.M309232200_bib54","doi-asserted-by":"crossref","first-page":"709","DOI":"10.1002\/elps.1150170415","volume":"17","author":"Sch\u00e4gger","year":"1996","journal-title":"Electrophoresis"},{"key":"10.1074\/jbc.M309232200_bib55","doi-asserted-by":"crossref","first-page":"763","DOI":"10.1002\/elps.11501601125","volume":"16","author":"Sch\u00e4gger","year":"1995","journal-title":"Electrophoresis"},{"key":"10.1074\/jbc.M309232200_bib56","doi-asserted-by":"crossref","first-page":"117","DOI":"10.1016\/0076-6879(95)60134-1","volume":"260","author":"Capaldi","year":"1996","journal-title":"Methods Enzymol."},{"key":"10.1074\/jbc.M309232200_bib57","doi-asserted-by":"crossref","first-page":"1125","DOI":"10.1515\/bchm2.1976.357.2.1125","volume":"357","author":"Steffens","year":"1976","journal-title":"Hoppe Seylers. Z. Physiol. Chem."},{"key":"10.1074\/jbc.M309232200_bib58","doi-asserted-by":"crossref","first-page":"935","DOI":"10.1093\/hmg\/6.6.935","volume":"6","author":"Taanman","year":"1997","journal-title":"Hum. Mol. Genet."},{"key":"10.1074\/jbc.M309232200_bib59","doi-asserted-by":"crossref","first-page":"12996","DOI":"10.1021\/bi000884z","volume":"39","author":"Musatov","year":"2000","journal-title":"Biochemistry"},{"key":"10.1074\/jbc.M309232200_bib60","doi-asserted-by":"crossref","first-page":"13","DOI":"10.1007\/BF00321109","volume":"18","author":"Krummeck","year":"1990","journal-title":"Curr. Genet."},{"key":"10.1074\/jbc.M309232200_bib61","doi-asserted-by":"crossref","first-page":"89","DOI":"10.1016\/S0167-4889(02)00267-7","volume":"1592","author":"Arnold","year":"2002","journal-title":"Biochim. Biophys. Acta"},{"key":"10.1074\/jbc.M309232200_bib62","doi-asserted-by":"crossref","first-page":"1723","DOI":"10.1126\/science.280.5370.1723","volume":"280","author":"Yoshikawa","year":"1998","journal-title":"Science"},{"key":"10.1074\/jbc.M309232200_bib63","doi-asserted-by":"crossref","first-page":"16296","DOI":"10.1074\/jbc.M011162200","volume":"276","author":"Hanson","year":"2001","journal-title":"J. Biol. Chem."},{"key":"10.1074\/jbc.M309232200_bib64","doi-asserted-by":"crossref","first-page":"829","DOI":"10.1042\/bj2120829","volume":"212","author":"Wielburski","year":"1983","journal-title":"Biochem. J."},{"key":"10.1074\/jbc.M309232200_bib65","doi-asserted-by":"crossref","first-page":"389","DOI":"10.1046\/j.1432-1327.1998.2540389.x","volume":"254","author":"Nijtmans","year":"1998","journal-title":"Eur. J. Biochem."},{"key":"10.1074\/jbc.M309232200_bib66","doi-asserted-by":"crossref","first-page":"101","DOI":"10.1086\/345489","volume":"72","author":"Antonicka","year":"2003","journal-title":"Am. J. Hum. Genet."},{"key":"10.1074\/jbc.M309232200_bib67","doi-asserted-by":"crossref","first-page":"416","DOI":"10.1016\/S0014-5793(99)01571-9","volume":"462","author":"Poyau","year":"1999","journal-title":"FEBS Lett."},{"key":"10.1074\/jbc.M309232200_bib68","doi-asserted-by":"crossref","first-page":"46","DOI":"10.1016\/S0014-5793(01)02447-4","volume":"498","author":"Nijtmans","year":"2001","journal-title":"FEBS Lett."},{"key":"10.1074\/jbc.M309232200_bib69","doi-asserted-by":"crossref","first-page":"446","DOI":"10.1042\/bst0290446","volume":"29","author":"Taanman","year":"2001","journal-title":"Biochem. Soc. Trans."}],"container-title":["Journal of Biological Chemistry"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0021925818444419?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0021925818444419?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/syndication.highwire.org\/content\/doi\/10.1074\/jbc.M309232200","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2021,12,18]],"date-time":"2021-12-18T06:57:45Z","timestamp":1639810665000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S0021925818444419"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2004,2]]},"references-count":69,"journal-issue":{"issue":"9","published-print":{"date-parts":[[2004,2]]}},"alternative-id":["S0021925818444419"],"URL":"https:\/\/doi.org\/10.1074\/jbc.m309232200","relation":{},"ISSN":["0021-9258"],"issn-type":[{"value":"0021-9258","type":"print"}],"subject":[],"published":{"date-parts":[[2004,2]]}}}