{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,10,24]],"date-time":"2025-10-24T12:47:03Z","timestamp":1761310023998},"reference-count":30,"publisher":"Elsevier BV","issue":"20","license":[{"start":{"date-parts":[[2001,5,1]],"date-time":"2001-05-01T00:00:00Z","timestamp":988675200000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"},{"start":{"date-parts":[[2020,9,26]],"date-time":"2020-09-26T00:00:00Z","timestamp":1601078400000},"content-version":"vor","delay-in-days":7088,"URL":"http:\/\/creativecommons.org\/licenses\/by\/4.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Journal of Biological Chemistry"],"published-print":{"date-parts":[[2001,5]]},"DOI":"10.1074\/jbc.m006547200","type":"journal-article","created":{"date-parts":[[2002,7,26]],"date-time":"2002-07-26T15:08:15Z","timestamp":1027696095000},"page":"17156-17162","source":"Crossref","is-referenced-by-count":29,"title":["A G1127S Change in Calcium-binding Epidermal Growth Factor-like Domain 13 of Human Fibrillin-1 Causes Short Range Conformational Effects"],"prefix":"10.1016","volume":"276","author":[{"given":"Pat","family":"Whiteman","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Rachel S.","family":"Smallridge","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Vroni","family":"Knott","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Jemima J.","family":"Cordle","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"A. Kristina","family":"Downing","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Penny A.","family":"Handford","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"78","reference":[{"key":"10.1074\/jbc.M006547200_bib1","doi-asserted-by":"crossref","first-page":"385","DOI":"10.1016\/S0959-440X(05)80111-3","volume":"3","author":"Campbell","year":"1993","journal-title":"Curr. Opin. Struct. Biol."},{"key":"10.1074\/jbc.M006547200_bib2","doi-asserted-by":"crossref","first-page":"2053","DOI":"10.1002\/j.1460-2075.1988.tb03045.x","volume":"7","author":"Rees","year":"1988","journal-title":"EMBO J."},{"key":"10.1074\/jbc.M006547200_bib3","doi-asserted-by":"crossref","first-page":"164","DOI":"10.1038\/351164a0","volume":"351","author":"Handford","year":"1991","journal-title":"Nature"},{"key":"10.1074\/jbc.M006547200_bib4","doi-asserted-by":"crossref","first-page":"489","DOI":"10.1093\/protein\/5.6.489","volume":"5","author":"Mayhew","year":"1992","journal-title":"Protein Eng."},{"key":"10.1074\/jbc.M006547200_bib5","doi-asserted-by":"crossref","first-page":"597","DOI":"10.1016\/S0092-8674(00)81259-3","volume":"85","author":"Downing","year":"1996","journal-title":"Cell"},{"key":"10.1074\/jbc.M006547200_bib6","doi-asserted-by":"crossref","first-page":"1065","DOI":"10.1006\/jmbi.1999.3513","volume":"296","author":"Werner","year":"2000","journal-title":"J. Mol. Biol."},{"key":"10.1074\/jbc.M006547200_bib7","doi-asserted-by":"crossref","first-page":"1231","DOI":"10.1074\/jbc.272.2.1231","volume":"272","author":"Reinhardt","year":"1997","journal-title":"J. Biol. Chem."},{"key":"10.1074\/jbc.M006547200_bib8","doi-asserted-by":"crossref","first-page":"427","DOI":"10.1111\/j.1432-1033.1996.0427h.x","volume":"240","author":"Sasaki","year":"1996","journal-title":"Eur. J. Biochem."},{"key":"10.1074\/jbc.M006547200_bib9","doi-asserted-by":"crossref","first-page":"229","DOI":"10.1093\/nar\/26.1.229","volume":"26","author":"Collod-B\u00e9roud","year":"1998","journal-title":"Nucleic Acids Res."},{"key":"10.1074\/jbc.M006547200_bib10","doi-asserted-by":"crossref","first-page":"350","DOI":"10.1002\/(SICI)1096-8628(19980724)78:4<350::AID-AJMG9>3.0.CO;2-P","volume":"78","author":"Park","year":"1998","journal-title":"Am. J. Med. Genet."},{"key":"10.1074\/jbc.M006547200_bib11","doi-asserted-by":"crossref","first-page":"265","DOI":"10.1093\/nar\/26.1.265","volume":"26","author":"Giannelli","year":"1998","journal-title":"Nucleic Acids Res."},{"key":"10.1074\/jbc.M006547200_bib12","doi-asserted-by":"crossref","first-page":"248","DOI":"10.1093\/nar\/26.1.248","volume":"26","author":"Varret","year":"1998","journal-title":"Nucleic Acids Res."},{"key":"10.1074\/jbc.M006547200_bib13","doi-asserted-by":"crossref","first-page":"707","DOI":"10.1038\/383707a0","volume":"383","author":"Joutel","year":"1996","journal-title":"Nature"},{"key":"10.1074\/jbc.M006547200_bib14","doi-asserted-by":"crossref","first-page":"130","DOI":"10.1182\/blood.V85.1.130.bloodjournal851130","volume":"85","author":"Gandrille","year":"1995","journal-title":"Blood"},{"key":"10.1074\/jbc.M006547200_bib15","doi-asserted-by":"crossref","first-page":"876","DOI":"10.1055\/s-0038-1653885","volume":"73","author":"Reitsma","year":"1995","journal-title":"Thromb. Haemost."},{"key":"10.1074\/jbc.M006547200_bib16","doi-asserted-by":"crossref","first-page":"2499","DOI":"10.1083\/jcb.103.6.2499","volume":"103","author":"Sakai","year":"1986","journal-title":"J. Cell Biol."},{"key":"10.1074\/jbc.M006547200_bib17","doi-asserted-by":"crossref","first-page":"469","DOI":"10.1016\/S0945-053X(99)00038-4","volume":"18","author":"Giltay","year":"1999","journal-title":"Matrix Biol."},{"key":"10.1074\/jbc.M006547200_bib18","doi-asserted-by":"crossref","first-page":"1799","DOI":"10.1093\/hmg\/4.suppl_1.1799","volume":"4","author":"Dietz","year":"1995","journal-title":"Hum. Mol. Genet."},{"key":"10.1074\/jbc.M006547200_bib19","first-page":"1287","volume":"56","author":"Franke","year":"1995","journal-title":"Am. J. Hum. Genet."},{"key":"10.1074\/jbc.M006547200_bib20","doi-asserted-by":"crossref","first-page":"1407","DOI":"10.1182\/blood.V72.4.1407.1407","volume":"72","author":"Denton","year":"1988","journal-title":"Blood"},{"key":"10.1074\/jbc.M006547200_bib21","doi-asserted-by":"crossref","first-page":"7807","DOI":"10.1074\/jbc.273.14.7807","volume":"273","author":"Whiteman","year":"1998","journal-title":"J. Biol. Chem."},{"key":"10.1074\/jbc.M006547200_bib22","doi-asserted-by":"crossref","first-page":"961","DOI":"10.1093\/hmg\/2.7.961","volume":"2","author":"Pereira","year":"1993","journal-title":"Hum. Mol. Genet."},{"key":"10.1074\/jbc.M006547200_bib23","doi-asserted-by":"crossref","first-page":"957","DOI":"10.1093\/protein\/11.11.957","volume":"11","author":"Whiteman","year":"1998","journal-title":"Protein Eng."},{"key":"10.1074\/jbc.M006547200_bib24","doi-asserted-by":"crossref","first-page":"4546","DOI":"10.1063\/1.438208","volume":"71","author":"Jeener","year":"1979","journal-title":"J. Chem. Phys."},{"key":"10.1074\/jbc.M006547200_bib25","first-page":"259","volume":"43","author":"Macura","year":"1981","journal-title":"J. Magn. Reson."},{"key":"10.1074\/jbc.M006547200_bib26","doi-asserted-by":"crossref","first-page":"661","DOI":"10.1006\/jmbi.1998.2536","volume":"286","author":"Smallridge","year":"1999","journal-title":"J. Mol. Biol."},{"key":"10.1074\/jbc.M006547200_bib27","doi-asserted-by":"crossref","first-page":"275","DOI":"10.1006\/jmra.1995.1047","volume":"112","author":"Hwang","year":"1995","journal-title":"J. Magn. Reson."},{"key":"10.1074\/jbc.M006547200_bib28","doi-asserted-by":"crossref","first-page":"1277","DOI":"10.1006\/jmbi.1998.2368","volume":"285","author":"Kettle","year":"1999","journal-title":"J. Mol. Biol."},{"key":"10.1074\/jbc.M006547200_bib29","doi-asserted-by":"crossref","first-page":"1987","DOI":"10.1093\/hmg\/9.13.1987","volume":"9","author":"McGettrick","year":"2000","journal-title":"Hum. Mol Genet."},{"key":"10.1074\/jbc.M006547200_bib30","doi-asserted-by":"crossref","first-page":"12339","DOI":"10.1074\/jbc.275.16.12339","volume":"275","author":"Reinhardt","year":"2000","journal-title":"J. Biol. Chem."}],"container-title":["Journal of Biological Chemistry"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0021925819318952?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0021925819318952?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/syndication.highwire.org\/content\/doi\/10.1074\/jbc.M006547200","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2022,1,2]],"date-time":"2022-01-02T11:59:21Z","timestamp":1641124761000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S0021925819318952"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2001,5]]},"references-count":30,"journal-issue":{"issue":"20","published-print":{"date-parts":[[2001,5]]}},"alternative-id":["S0021925819318952"],"URL":"https:\/\/doi.org\/10.1074\/jbc.m006547200","relation":{},"ISSN":["0021-9258"],"issn-type":[{"value":"0021-9258","type":"print"}],"subject":[],"published":{"date-parts":[[2001,5]]}}}