{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,5]],"date-time":"2026-10-05T01:06:17Z","timestamp":1791162377008,"version":"4.1.0"},"reference-count":42,"publisher":"Elsevier BV","issue":"20","license":[{"start":{"date-parts":[[2001,5,1]],"date-time":"2001-05-01T00:00:00Z","timestamp":988675200000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"},{"start":{"date-parts":[[2020,9,26]],"date-time":"2020-09-26T00:00:00Z","timestamp":1601078400000},"content-version":"vor","delay-in-days":7088,"URL":"http:\/\/creativecommons.org\/licenses\/by\/4.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Journal of Biological Chemistry"],"published-print":{"date-parts":[[2001,5]]},"DOI":"10.1074\/jbc.m100460200","type":"journal-article","created":{"date-parts":[[2002,7,26]],"date-time":"2002-07-26T15:08:15Z","timestamp":1027696095000},"page":"17286-17290","source":"Crossref","is-referenced-by-count":43,"title":["Mutations in Sialidosis Impair Sialidase Binding to the Lysosomal Multienzyme Complex"],"prefix":"10.1016","volume":"276","author":[{"given":"Kiven E.","family":"Lukong","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Karine","family":"Landry","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Marc-Andr\u00e9","family":"Elsliger","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Yuan","family":"Chang","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Stephane","family":"Lefrancois","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Carlos R.","family":"Morales","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Alexey V.","family":"Pshezhetsky","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"78","reference":[{"key":"10.1074\/jbc.M100460200_bib1","first-page":"3507","volume":"3","author":"Thomas","year":"2001"},{"key":"10.1074\/jbc.M100460200_bib2","doi-asserted-by":"crossref","first-page":"320","DOI":"10.1159\/000112180","volume":"13","author":"Federico","year":"1991","journal-title":"Dev. Neurosci.-Basel"},{"key":"10.1074\/jbc.M100460200_bib3","doi-asserted-by":"crossref","first-page":"523","DOI":"10.1007\/BF01799510","volume":"13","author":"Cantz","year":"1990","journal-title":"J. Inherit. Metab. Dis."},{"key":"10.1074\/jbc.M100460200_bib4","first-page":"391","volume":"32","author":"Durand","year":"1977","journal-title":"Helv. Paediatr. Acta"},{"key":"10.1074\/jbc.M100460200_bib5","doi-asserted-by":"crossref","first-page":"1861","DOI":"10.1016\/S0161-6420(79)35336-2","volume":"86","author":"Sogg","year":"1979","journal-title":"Ophthalmology"},{"key":"10.1074\/jbc.M100460200_bib6","doi-asserted-by":"crossref","first-page":"234","DOI":"10.1002\/ana.410030309","volume":"3","author":"Rapin","year":"1978","journal-title":"Ann. Neurol."},{"key":"10.1074\/jbc.M100460200_bib7","doi-asserted-by":"crossref","first-page":"55","DOI":"10.1111\/j.1399-0004.1978.tb02061.x","volume":"14","author":"O'Brien","year":"1979","journal-title":"Clin. Genet."},{"key":"10.1074\/jbc.M100460200_bib8","doi-asserted-by":"crossref","first-page":"157","DOI":"10.1016\/0022-510X(80)90197-5","volume":"48","author":"Federico","year":"1980","journal-title":"J. Neurol. Sci."},{"key":"10.1074\/jbc.M100460200_bib9","first-page":"40","volume":"7","author":"Till","year":"1987","journal-title":"J. Clin. Neuro-Ophthal."},{"key":"10.1074\/jbc.M100460200_bib10","doi-asserted-by":"crossref","first-page":"31","DOI":"10.1002\/ajmg.1320010105","volume":"1","author":"Kelly","year":"1977","journal-title":"Am. J. Med. Genet."},{"key":"10.1074\/jbc.M100460200_bib11","doi-asserted-by":"crossref","first-page":"341","DOI":"10.1007\/BF00295374","volume":"70","author":"Oohira","year":"1985","journal-title":"Hum. Genet."},{"key":"10.1074\/jbc.M100460200_bib12","doi-asserted-by":"crossref","first-page":"203","DOI":"10.1111\/j.1399-0004.1980.tb00873.x","volume":"18","author":"Winter","year":"1980","journal-title":"Clin. Genet."},{"key":"10.1074\/jbc.M100460200_bib13","doi-asserted-by":"crossref","first-page":"662","DOI":"10.1016\/S0022-3476(80)80734-7","volume":"96","author":"Aylsworth","year":"1980","journal-title":"J. Pediatr."},{"key":"10.1074\/jbc.M100460200_bib14","first-page":"43","volume":"32","author":"Johnson","year":"1980","journal-title":"Am. J. Hum. Genet."},{"key":"10.1074\/jbc.M100460200_bib15","doi-asserted-by":"crossref","first-page":"135","DOI":"10.1007\/BF00445802","volume":"143","author":"Beck","year":"1984","journal-title":"Eur. J Pediatr."},{"key":"10.1074\/jbc.M100460200_bib16","doi-asserted-by":"crossref","first-page":"732","DOI":"10.1016\/0006-291X(77)90363-1","volume":"74","author":"Cantz","year":"1977","journal-title":"Biochem. Biophys. Res. Commun."},{"key":"10.1074\/jbc.M100460200_bib17","doi-asserted-by":"crossref","first-page":"4535","DOI":"10.1073\/pnas.79.15.4535","volume":"79","author":"d'Azzo","year":"1982","journal-title":"Proc. Natl. Acad. Sci. U. S. A."},{"key":"10.1074\/jbc.M100460200_bib18","doi-asserted-by":"crossref","first-page":"1317","DOI":"10.1016\/S0021-9258(19)85088-3","volume":"264","author":"Van der Horst","year":"1989","journal-title":"J. Biol. Chem."},{"key":"10.1074\/jbc.M100460200_bib19","doi-asserted-by":"crossref","first-page":"28359","DOI":"10.1074\/jbc.271.45.28359","volume":"271","author":"Pshezhetsky","year":"1996","journal-title":"J. Biol. Chem."},{"key":"10.1074\/jbc.M100460200_bib20","doi-asserted-by":"crossref","first-page":"641","DOI":"10.1042\/bj3300641","volume":"330","author":"Vinogradova","year":"1998","journal-title":"Biochem. J."},{"key":"10.1074\/jbc.M100460200_bib21","doi-asserted-by":"crossref","first-page":"12143","DOI":"10.1016\/S0021-9258(17)44147-0","volume":"258","author":"Hoogeveen","year":"1983","journal-title":"J. Biol. Chem."},{"key":"10.1074\/jbc.M100460200_bib22","doi-asserted-by":"crossref","first-page":"1588","DOI":"10.1093\/emboj\/17.6.1588","volume":"17","author":"van der Spoel","year":"1998","journal-title":"EMBO J."},{"key":"10.1074\/jbc.M100460200_bib23","doi-asserted-by":"crossref","first-page":"17949","DOI":"10.1016\/S0021-9258(19)37135-2","volume":"267","author":"Morreau","year":"1992","journal-title":"J. Biol. Chem."},{"key":"10.1074\/jbc.M100460200_bib24","doi-asserted-by":"crossref","first-page":"833","DOI":"10.1042\/bj2850833","volume":"285","author":"D'Agrosa","year":"1992","journal-title":"Biochem. J."},{"key":"10.1074\/jbc.M100460200_bib25","doi-asserted-by":"crossref","first-page":"787","DOI":"10.1042\/bj3130787","volume":"313","author":"Okamura-Oho","year":"1996","journal-title":"Biochem. J."},{"key":"10.1074\/jbc.M100460200_bib26","first-page":"3811","volume":"3","author":"d'Azzo","year":"2001"},{"key":"10.1074\/jbc.M100460200_bib27","doi-asserted-by":"crossref","first-page":"3156","DOI":"10.1101\/gad.10.24.3156","volume":"10","author":"Bonten","year":"1996","journal-title":"Genes Dev."},{"key":"10.1074\/jbc.M100460200_bib28","doi-asserted-by":"crossref","first-page":"316","DOI":"10.1038\/ng0397-316","volume":"15","author":"Pshezhetsky","year":"1997","journal-title":"Nat. Genet."},{"key":"10.1074\/jbc.M100460200_bib29","doi-asserted-by":"crossref","first-page":"4549","DOI":"10.1074\/jbc.272.7.4549","volume":"272","author":"Milner","year":"1997","journal-title":"J. Biol. Chem."},{"key":"10.1074\/jbc.M100460200_bib30","doi-asserted-by":"crossref","first-page":"2715","DOI":"10.1093\/hmg\/9.18.2715","volume":"9","author":"Bonten","year":"2000","journal-title":"Hum. Mol. Genet."},{"key":"10.1074\/jbc.M100460200_bib31","doi-asserted-by":"crossref","first-page":"1075","DOI":"10.1093\/hmg\/9.7.1075","volume":"9","author":"Lukong","year":"2000","journal-title":"Hum. Mol. Genet."},{"key":"10.1074\/jbc.M100460200_bib32","doi-asserted-by":"crossref","first-page":"615","DOI":"10.1073\/pnas.95.2.621","volume":"95","author":"Rudenko","year":"1998","journal-title":"Proc. Natl. Acad. Sci. U. S. A."},{"key":"10.1074\/jbc.M100460200_bib33","doi-asserted-by":"crossref","first-page":"1002","DOI":"10.1126\/science.160.3831.1002","volume":"160","author":"Okada","year":"1968","journal-title":"Science"},{"key":"10.1074\/jbc.M100460200_bib34","doi-asserted-by":"crossref","first-page":"287","DOI":"10.1016\/0003-2697(79)90362-2","volume":"94","author":"Potier","year":"1979","journal-title":"Anal. Biochem."},{"key":"10.1074\/jbc.M100460200_bib35","doi-asserted-by":"crossref","first-page":"143","DOI":"10.1016\/0092-8674(79)90302-7","volume":"17","author":"Rome","year":"1979","journal-title":"Cell"},{"key":"10.1074\/jbc.M100460200_bib36","doi-asserted-by":"crossref","first-page":"303","DOI":"10.1006\/abio.1995.1478","volume":"230","author":"Pshezhetsky","year":"1995","journal-title":"Anal. Biochem."},{"key":"10.1074\/jbc.M100460200_bib37","doi-asserted-by":"crossref","first-page":"248","DOI":"10.1016\/0003-2697(76)90527-3","volume":"72","author":"Bradford","year":"1976","journal-title":"Anal. Biochem."},{"key":"10.1074\/jbc.M100460200_bib38","doi-asserted-by":"crossref","first-page":"680","DOI":"10.1038\/227680a0","volume":"227","author":"Laemmli","year":"1970","journal-title":"Nature"},{"key":"10.1074\/jbc.M100460200_bib39","doi-asserted-by":"crossref","first-page":"49","DOI":"10.1002\/j.1460-2075.1992.tb05026.x","volume":"11","author":"Burmeister","year":"1992","journal-title":"EMBO J."},{"key":"10.1074\/jbc.M100460200_bib40","doi-asserted-by":"crossref","first-page":"35","DOI":"10.1038\/303035a0","volume":"303","author":"Varghese","year":"1983","journal-title":"Nature"},{"key":"10.1074\/jbc.M100460200_bib41","doi-asserted-by":"crossref","first-page":"9852","DOI":"10.1073\/pnas.90.21.9852","volume":"90","author":"Crennell","year":"1993","journal-title":"Proc. Natl. Acad. Sci. U. S. A."},{"key":"10.1074\/jbc.M100460200_bib42","doi-asserted-by":"crossref","first-page":"241","DOI":"10.1007\/s100380070034","volume":"45","author":"Naganawa","year":"2000","journal-title":"J. Hum. Genet."}],"container-title":["Journal of Biological Chemistry"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S002192581931912X?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S002192581931912X?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/syndication.highwire.org\/content\/doi\/10.1074\/jbc.M100460200","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2022,1,2]],"date-time":"2022-01-02T11:59:45Z","timestamp":1641124785000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S002192581931912X"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2001,5]]},"references-count":42,"journal-issue":{"issue":"20","published-print":{"date-parts":[[2001,5]]}},"alternative-id":["S002192581931912X"],"URL":"https:\/\/doi.org\/10.1074\/jbc.m100460200","relation":{},"ISSN":["0021-9258"],"issn-type":[{"value":"0021-9258","type":"print"}],"subject":[],"published":{"date-parts":[[2001,5]]}}}