{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,6]],"date-time":"2026-10-06T09:48:37Z","timestamp":1791280117452,"version":"4.1.0"},"reference-count":47,"publisher":"Elsevier BV","issue":"18","license":[{"start":{"date-parts":[[2006,5,1]],"date-time":"2006-05-01T00:00:00Z","timestamp":1146441600000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"},{"start":{"date-parts":[[2020,9,30]],"date-time":"2020-09-30T00:00:00Z","timestamp":1601424000000},"content-version":"vor","delay-in-days":5266,"URL":"http:\/\/creativecommons.org\/licenses\/by\/4.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Journal of Biological Chemistry"],"published-print":{"date-parts":[[2006,5]]},"DOI":"10.1074\/jbc.m511528200","type":"journal-article","created":{"date-parts":[[2006,2,21]],"date-time":"2006-02-21T22:42:34Z","timestamp":1140561754000},"page":"12888-12895","source":"Crossref","is-referenced-by-count":153,"title":["Murine Model of the Ehlers-Danlos Syndrome"],"prefix":"10.1016","volume":"281","author":[{"given":"Richard J.","family":"Wenstrup","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Jane B.","family":"Florer","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Jeffrey M.","family":"Davidson","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Charlotte L.","family":"Phillips","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Brent J.","family":"Pfeiffer","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Diana W.","family":"Menezes","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Inna","family":"Chervoneva","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"David E.","family":"Birk","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"78","reference":[{"key":"10.1074\/jbc.M511528200_bib1","series-title":"McKusick's Heritable Disorders of Connective Tissue","first-page":"189","author":"Beighton","year":"1992"},{"key":"10.1074\/jbc.M511528200_bib2","doi-asserted-by":"crossref","first-page":"31","DOI":"10.1002\/(SICI)1096-8628(19980428)77:1<31::AID-AJMG8>3.0.CO;2-O","volume":"77","author":"Beighton","year":"1998","journal-title":"Am. J. Med. Genet."},{"key":"10.1074\/jbc.M511528200_bib3","series-title":"Connective Tissue and Its Heritable Disorders","first-page":"431","author":"Steinmann","year":"2002"},{"key":"10.1074\/jbc.M511528200_bib4","first-page":"201","volume":"40","author":"Vogel","year":"1979","journal-title":"Lab. Investig."},{"key":"10.1074\/jbc.M511528200_bib5","doi-asserted-by":"crossref","first-page":"394","DOI":"10.1007\/BF00201664","volume":"93","author":"Hausser","year":"1994","journal-title":"Hum. Genet."},{"key":"10.1074\/jbc.M511528200_bib6","doi-asserted-by":"crossref","first-page":"1733","DOI":"10.1093\/hmg\/5.11.1733","volume":"5","author":"Wenstrup","year":"1996","journal-title":"Hum. Mol. Genet."},{"key":"10.1074\/jbc.M511528200_bib7","doi-asserted-by":"crossref","first-page":"846","DOI":"10.1136\/jmg.35.10.846","volume":"35","author":"Richards","year":"1998","journal-title":"J. Med. Genet."},{"key":"10.1074\/jbc.M511528200_bib8","doi-asserted-by":"crossref","first-page":"361","DOI":"10.1038\/ng0796-361","volume":"13","author":"Toriello","year":"1996","journal-title":"Nat. Genet."},{"key":"10.1074\/jbc.M511528200_bib9","doi-asserted-by":"crossref","first-page":"249","DOI":"10.1093\/hmg\/7.2.249","volume":"7","author":"Michalickova","year":"1998","journal-title":"Hum. Mol. Genet."},{"key":"10.1074\/jbc.M511528200_bib10","doi-asserted-by":"crossref","first-page":"2461","DOI":"10.1093\/hmg\/ddh262","volume":"13","author":"Ugalde","year":"2004","journal-title":"Hum. Mol. Genet."},{"key":"10.1074\/jbc.M511528200_bib11","doi-asserted-by":"crossref","first-page":"940","DOI":"10.1136\/jmg.33.11.940","volume":"33","author":"Nicholls","year":"1996","journal-title":"J. Med. Genet."},{"key":"10.1074\/jbc.M511528200_bib12","first-page":"547","volume":"60","author":"De Paepe","year":"1997","journal-title":"Am. J. Hum. Genet."},{"key":"10.1074\/jbc.M511528200_bib13","doi-asserted-by":"crossref","first-page":"174","DOI":"10.1111\/j.1365-2230.1997.tb01055.x","volume":"22","author":"Burrows","year":"1997","journal-title":"Clin. Exp. Dermatol."},{"key":"10.1074\/jbc.M511528200_bib14","doi-asserted-by":"crossref","first-page":"1273","DOI":"10.1111\/1523-1747.ep12348978","volume":"106","author":"Burrows","year":"1996","journal-title":"J. Investig. Dermatol."},{"key":"10.1074\/jbc.M511528200_bib15","doi-asserted-by":"crossref","first-page":"13356","DOI":"10.1074\/jbc.M011742200","volume":"276","author":"Bouma","year":"2001","journal-title":"J. Biol. Chem."},{"key":"10.1074\/jbc.M511528200_bib16","doi-asserted-by":"crossref","first-page":"1757","DOI":"10.1086\/302933","volume":"66","author":"Schwarze","year":"2000","journal-title":"Am. J. Hum. Genet."},{"key":"10.1074\/jbc.M511528200_bib17","doi-asserted-by":"crossref","first-page":"1766","DOI":"10.1086\/302930","volume":"66","author":"Wenstrup","year":"2000","journal-title":"Am. J. Hum. Genet."},{"key":"10.1074\/jbc.M511528200_bib18","doi-asserted-by":"crossref","first-page":"28","DOI":"10.1002\/humu.20107","volume":"25","author":"Malfait","year":"2005","journal-title":"Hum. Mutat."},{"key":"10.1074\/jbc.M511528200_bib19","doi-asserted-by":"crossref","first-page":"24354","DOI":"10.1016\/S0021-9258(19)51090-0","volume":"269","author":"Lees","year":"1994","journal-title":"J. Biol. Chem."},{"key":"10.1074\/jbc.M511528200_bib20","doi-asserted-by":"crossref","first-page":"24352","DOI":"10.1074\/jbc.M101182200","volume":"276","author":"Chanut-Delalande","year":"2001","journal-title":"J. Biol. Chem."},{"key":"10.1074\/jbc.M511528200_bib21","doi-asserted-by":"crossref","first-page":"223","DOI":"10.1016\/S0968-4328(00)00043-3","volume":"32","author":"Birk","year":"2001","journal-title":"Micron"},{"key":"10.1074\/jbc.M511528200_bib22","doi-asserted-by":"crossref","first-page":"999","DOI":"10.1083\/jcb.106.3.999","volume":"106","author":"Birk","year":"1988","journal-title":"J. Cell Biol."},{"key":"10.1074\/jbc.M511528200_bib23","doi-asserted-by":"crossref","first-page":"304","DOI":"10.1016\/0167-4838(93)90099-D","volume":"1203","author":"Niyibizi","year":"1993","journal-title":"Biochim. Biophys. Acta"},{"key":"10.1074\/jbc.M511528200_bib24","doi-asserted-by":"crossref","first-page":"1415","DOI":"10.1083\/jcb.135.5.1415","volume":"135","author":"Marchant","year":"1996","journal-title":"J. Cell Biol."},{"key":"10.1074\/jbc.M511528200_bib25","doi-asserted-by":"crossref","first-page":"113","DOI":"10.1002\/jcb.20024","volume":"92","author":"Wenstrup","year":"2004","journal-title":"J. Cell. Biochem."},{"key":"10.1074\/jbc.M511528200_bib26","doi-asserted-by":"crossref","first-page":"53331","DOI":"10.1074\/jbc.M409622200","volume":"279","author":"Wenstrup","year":"2004","journal-title":"J. Biol. Chem."},{"key":"10.1074\/jbc.M511528200_bib27","doi-asserted-by":"crossref","first-page":"6049","DOI":"10.1128\/MCB.24.13.6049-6057.2004","volume":"24","author":"Chanut-Delalande","year":"2004","journal-title":"Mol. Cell. Biol."},{"key":"10.1074\/jbc.M511528200_bib28","doi-asserted-by":"crossref","first-page":"372","DOI":"10.1016\/0076-6879(82)82074-0","volume":"82","author":"Berg","year":"1982","journal-title":"Methods Enzymol."},{"key":"10.1074\/jbc.M511528200_bib29","doi-asserted-by":"crossref","first-page":"1263","DOI":"10.1067\/mva.2001.113579","volume":"33","author":"Vouyouka","year":"2001","journal-title":"J. Vasc. Surg."},{"key":"10.1074\/jbc.M511528200_bib30","doi-asserted-by":"crossref","first-page":"1468","DOI":"10.1172\/JCI2131","volume":"101","author":"Liaw","year":"1998","journal-title":"J. Clin. Investig."},{"key":"10.1074\/jbc.M511528200_bib31","doi-asserted-by":"crossref","first-page":"2024","DOI":"10.1083\/jcb.99.6.2024","volume":"99","author":"Birk","year":"1984","journal-title":"J. Cell Biol."},{"key":"10.1074\/jbc.M511528200_bib32","doi-asserted-by":"crossref","first-page":"43081","DOI":"10.1074\/jbc.M304998200","volume":"278","author":"Antonicka","year":"2003","journal-title":"J. Biol. Chem."},{"key":"10.1074\/jbc.M511528200_bib33","series-title":"Linear and Nonlinear Models for the Analysis of Repeated Measures","author":"Vonesh","year":"1997"},{"key":"10.1074\/jbc.M511528200_bib34","doi-asserted-by":"crossref","first-page":"112","DOI":"10.1097\/00125817-200205000-00003","volume":"4","author":"Wenstrup","year":"2002","journal-title":"Genet. Med."},{"key":"10.1074\/jbc.M511528200_bib35","series-title":"The Basic Science of Vascular Disease","first-page":"69","author":"Dobrin","year":"1997"},{"key":"10.1074\/jbc.M511528200_bib36","doi-asserted-by":"crossref","first-page":"19","DOI":"10.1161\/01.ATV.5.1.19","volume":"5","author":"Clark","year":"1985","journal-title":"Arteriosclerosis"},{"key":"10.1074\/jbc.M511528200_bib37","doi-asserted-by":"crossref","first-page":"405","DOI":"10.1001\/archsurg.1984.01390160041009","volume":"119","author":"Dobrin","year":"1984","journal-title":"Arch. Surg."},{"key":"10.1074\/jbc.M511528200_bib38","doi-asserted-by":"crossref","first-page":"553","DOI":"10.1083\/jcb.200312071","volume":"165","author":"Canty","year":"2004","journal-title":"J. Cell Biol."},{"key":"10.1074\/jbc.M511528200_bib39","doi-asserted-by":"crossref","first-page":"111","DOI":"10.1016\/S0945-053X(96)90152-3","volume":"15","author":"Birk","year":"1996","journal-title":"Matrix Biol."},{"key":"10.1074\/jbc.M511528200_bib40","doi-asserted-by":"crossref","first-page":"229","DOI":"10.1002\/aja.1002020303","volume":"202","author":"Birk","year":"1995","journal-title":"Dev. Dyn."},{"key":"10.1074\/jbc.M511528200_bib41","doi-asserted-by":"crossref","first-page":"359","DOI":"10.1016\/S0945-053X(00)00082-2","volume":"19","author":"Kadler","year":"2000","journal-title":"Matrix Biol."},{"key":"10.1074\/jbc.M511528200_bib42","doi-asserted-by":"crossref","first-page":"18843","DOI":"10.1074\/jbc.274.27.18843","volume":"274","author":"Iozzo","year":"1999","journal-title":"J. Biol. Chem."},{"key":"10.1074\/jbc.M511528200_bib43","doi-asserted-by":"crossref","first-page":"107R","DOI":"10.1093\/glycob\/cwf065","volume":"12","author":"Ameye","year":"2002","journal-title":"Glycobiology"},{"key":"10.1074\/jbc.M511528200_bib44","doi-asserted-by":"crossref","first-page":"37377","DOI":"10.1074\/jbc.M206286200","volume":"277","author":"Velling","year":"2002","journal-title":"J. Biol. Chem."},{"key":"10.1074\/jbc.M511528200_bib45","doi-asserted-by":"crossref","first-page":"419","DOI":"10.1083\/jcb.140.2.419","volume":"140","author":"Kyriakides","year":"1998","journal-title":"J. Cell Biol."},{"key":"10.1074\/jbc.M511528200_bib46","doi-asserted-by":"crossref","first-page":"565","DOI":"10.1167\/iovs.05-0771","volume":"4","author":"Segev","year":"2006","journal-title":"Invest. Ophthal. Vis. Sci."},{"key":"10.1074\/jbc.M511528200_bib47","doi-asserted-by":"crossref","first-page":"73","DOI":"10.1016\/1047-8477(91)90064-4","volume":"106","author":"Ploetz","year":"1991","journal-title":"J. Struct. Biol."}],"container-title":["Journal of Biological Chemistry"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0021925819466246?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0021925819466246?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/syndication.highwire.org\/content\/doi\/10.1074\/jbc.M511528200","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2022,1,2]],"date-time":"2022-01-02T13:29:48Z","timestamp":1641130188000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S0021925819466246"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2006,5]]},"references-count":47,"journal-issue":{"issue":"18","published-print":{"date-parts":[[2006,5]]}},"alternative-id":["S0021925819466246"],"URL":"https:\/\/doi.org\/10.1074\/jbc.m511528200","relation":{},"ISSN":["0021-9258"],"issn-type":[{"value":"0021-9258","type":"print"}],"subject":[],"published":{"date-parts":[[2006,5]]}}}