{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,15]],"date-time":"2026-08-15T00:27:34Z","timestamp":1786753654916,"version":"3.56.0"},"reference-count":8,"publisher":"Oxford University Press (OUP)","issue":"24","license":[{"start":{"date-parts":[[2019,7,2]],"date-time":"2019-07-02T00:00:00Z","timestamp":1562025600000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/academic.oup.com\/journals\/pages\/open_access\/funder_policies\/chorus\/standard_publication_model"}],"funder":[{"name":"ESID society"},{"name":"Plasma Protein Therapeutics Association Europe"},{"name":"European and National Grants"},{"name":"EURO-POLICY-PID","award":["SP23-CT-2005-006411"],"award-info":[{"award-number":["SP23-CT-2005-006411"]}]},{"DOI":"10.13039\/501100002347","name":"BMBF","doi-asserted-by":"publisher","award":["01GM0896"],"award-info":[{"award-number":["01GM0896"]}],"id":[{"id":"10.13039\/501100002347","id-type":"DOI","asserted-by":"publisher"}]},{"DOI":"10.13039\/501100002347","name":"BMBF","doi-asserted-by":"publisher","award":["01GM1111B"],"award-info":[{"award-number":["01GM1111B"]}],"id":[{"id":"10.13039\/501100002347","id-type":"DOI","asserted-by":"publisher"}]},{"DOI":"10.13039\/501100002347","name":"BMBF","doi-asserted-by":"publisher","award":["01GM1517C"],"award-info":[{"award-number":["01GM1517C"]}],"id":[{"id":"10.13039\/501100002347","id-type":"DOI","asserted-by":"publisher"}]},{"DOI":"10.13039\/501100002347","name":"BMBF","doi-asserted-by":"publisher","award":["01EO1303"],"award-info":[{"award-number":["01EO1303"]}],"id":[{"id":"10.13039\/501100002347","id-type":"DOI","asserted-by":"publisher"}]}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2019,12,15]]},"abstract":"<jats:title>Abstract<\/jats:title>\n               <jats:sec>\n                  <jats:title>Summary<\/jats:title>\n                  <jats:p>Primary Immunodeficiencies (PIDs) belong to the group of rare diseases. The European Society for Immunodeficiencies (ESID) operates an international research database application for continuous long-term documentation of patient data. The system is a web application which runs in a standard browser. Therefore, the system is easy to access from any location. Technically, the system is based on Gails backed by MariaDB with high standard security features to comply with the demands of a modern research platform.<\/jats:p>\n               <\/jats:sec>\n               <jats:sec>\n                  <jats:title>Availability and implementation<\/jats:title>\n                  <jats:p>The ESID Online Database is accessible via the official website: https:\/\/esid.org\/Working-Parties\/Registry-Working-Party\/ESID-Registry. A demo system is available via: https:\/\/cci-esid-reg-demo-app.uniklinik-freiburg.de\/EERS with user demouser and password Demo-2019.<\/jats:p>\n               <\/jats:sec>","DOI":"10.1093\/bioinformatics\/btz525","type":"journal-article","created":{"date-parts":[[2019,6,28]],"date-time":"2019-06-28T19:11:00Z","timestamp":1561749060000},"page":"5367-5369","source":"Crossref","is-referenced-by-count":23,"title":["The NEW ESID online database network"],"prefix":"10.1093","volume":"35","author":[{"ORCID":"https:\/\/orcid.org\/0000-0003-2067-5569","authenticated-orcid":false,"given":"Raphael","family":"Scheible","sequence":"first","affiliation":[{"name":"Institute of Medical Biometry and Statistics"},{"name":"Institute for Immunodeficiency, Center for Chronic Immunodeficiency (CCI)"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Stephan","family":"Rusch","sequence":"additional","affiliation":[{"name":"Institute for Immunodeficiency, Center for Chronic Immunodeficiency (CCI)"},{"name":"Central Facility Biobanking , Faculty of Medicine, Medical Center \u2013 University of Freiburg, Freiburg, Germany"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-7005-4467","authenticated-orcid":false,"given":"David","family":"Guzman","sequence":"additional","affiliation":[{"name":"Department of Computer Science, University College London , London, UK"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Nizar","family":"Mahlaoui","sequence":"additional","affiliation":[{"name":"French National Reference Center for Primary Immune Deficiencies (CEREDIH) , Necker Enfants Malades University Hospital, Assistance Publique-H\u00f4pitaux de Paris, Paris, France"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Stephan","family":"Ehl","sequence":"additional","affiliation":[{"name":"Institute for Immunodeficiency, Center for Chronic Immunodeficiency (CCI)"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Gerhard","family":"Kindle","sequence":"additional","affiliation":[{"name":"Institute for Immunodeficiency, Center for Chronic Immunodeficiency (CCI)"},{"name":"Central Facility Biobanking , Faculty of Medicine, Medical Center \u2013 University of Freiburg, Freiburg, Germany"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"286","published-online":{"date-parts":[[2019,7,2]]},"reference":[{"key":"2023013108411574200_btz525-B7","doi-asserted-by":"crossref","first-page":"129","DOI":"10.1007\/s10875-017-0465-8","article-title":"The 2017 IUIS phenotypic classification for primary immunodeficiencies","volume":"38","author":"Bousfiha","year":"2018","journal-title":"J. Clin. Immunol."},{"key":"2023013108411574200_btz525-B1","doi-asserted-by":"crossref","first-page":"116","DOI":"10.1016\/j.jaci.2013.12.1077","article-title":"Clinical picture and treatment of 2212 patients with common variable immunodeficiency","volume":"134","author":"Gathmann","year":"2014","journal-title":"J. Allergy Clin. Immunol"},{"key":"2023013108411574200_btz525-B2","doi-asserted-by":"crossref","first-page":"654","DOI":"10.1093\/bioinformatics\/btl675","article-title":"The ESID online database network","volume":"23","author":"Guzman","year":"2007","journal-title":"Bioinformatics"},{"key":"2023013108411574200_btz525-B3","doi-asserted-by":"crossref","first-page":"2","DOI":"10.1186\/s12911-014-0123-5","article-title":"A RESTful interface to pseudonymization services in modern web applications","volume":"15","author":"Lablans","year":"2015","journal-title":"BMC Med. Inf. 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