{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,8,24]],"date-time":"2025-08-24T22:40:01Z","timestamp":1756075201885,"version":"3.44.0"},"reference-count":13,"publisher":"Oxford University Press (OUP)","issue":"4","license":[{"start":{"date-parts":[[2025,5,29]],"date-time":"2025-05-29T00:00:00Z","timestamp":1748476800000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2025,7,6]]},"abstract":"<jats:title>Abstract<\/jats:title>\n               <jats:p>Vulvar dermatofibrosarcoma protuberans (DFSP) is a rare pathology. So far, only limited number of cases have been reported in literature. In the present case, we discuss a 38-year-old female presented with a painful left vulvar mass. She had a prior history of a left vulvar mass excision which was histopathologically confirmed as benign spindle cell epithelioma. The current mass, extending from the left labia majora to the left gluteal fold, was assessed via contrast-enhanced magnetic resonance imaging (MRI), revealing a well-defined, lobulated lesion with proximity to the distal urethra and clitoris without definite invasion. The patient underwent a wide local excision, radical vulvectomy, and left inguinofemoral lymphadenectomy. Postoperatively, she experienced fever, vulvar swelling, and dysuria. Follow-up MRI demonstrated total resolution of the vulvar mass and collection with no recurrence. Histopathology identified the mass as DFSP, with all surgical margins negative.<\/jats:p>","DOI":"10.1093\/bjrcr\/uaaf030","type":"journal-article","created":{"date-parts":[[2025,5,29]],"date-time":"2025-05-29T12:25:44Z","timestamp":1748521544000},"source":"Crossref","is-referenced-by-count":0,"title":["Vulvar dermatofibrosarcoma protuberans, an unusual anatomical location"],"prefix":"10.1093","volume":"11","author":[{"given":"Bano","family":"Alsaleh","sequence":"first","affiliation":[{"name":"Radiology Department, King Hamad University Hospital , Busaiteen, 24343, Kingdom of","place":["Bahrain"]}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-9488-8474","authenticated-orcid":false,"given":"Ahmed","family":"Alanzi","sequence":"additional","affiliation":[{"name":"Anaesthesia and Pain Management Department, King Hamad University Hospital , Busaiteen, 24343, Kingdom of","place":["Bahrain"]}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Mohamed","family":"Alsaleh","sequence":"additional","affiliation":[{"name":"Pediatric Department, Mohammed Bin Khalifa Bin Salman Al Khalifa Specialist Cardiac Center , Al Riffa, 28743, Kingdom of","place":["Bahrain"]}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Ahmed","family":"Alsaleh","sequence":"additional","affiliation":[{"name":"Royal College of Surgeons in Ireland\u2014Bahrain , Adliya, 15503, Kingdom of","place":["Bahrain"]}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Fouad","family":"Aladel","sequence":"additional","affiliation":[{"name":"Radiology Department, King Fahad Specialist Hospital , Dammam, 15215,","place":["Kingdom of Saudi Arabia"]}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"286","published-online":{"date-parts":[[2025,5,29]]},"reference":[{"key":"2025082418261501700_uaaf030-B1","doi-asserted-by":"crossref","first-page":"126","DOI":"10.30699\/jogcr.7.2.126","article-title":"Dermatofibrosarcoma protuberans of the vulva: a report of 2 cases of unusual localization","volume":"7","author":"Allameh","year":"2021","journal-title":"J Obstet Gynecol Cancer Res"},{"key":"2025082418261501700_uaaf030-B2","first-page":"545","article-title":"Dermatofibromes progressifs et recidivants ou fibrosarcomes de la peau","volume":"5","author":"Darier","year":"1924","journal-title":"Ann Dermatol Venereol"},{"key":"2025082418261501700_uaaf030-B3","doi-asserted-by":"crossref","first-page":"222","DOI":"10.3390\/cancers16010222","article-title":"Dermatofibrosarcoma protuberans of the vulva: a review of the MITO Rare Cancer Group","volume":"16","author":"Mancari","year":"2024","journal-title":"Cancers"},{"key":"2025082418261501700_uaaf030-B4","doi-asserted-by":"crossref","first-page":"771","DOI":"10.1097\/DSS.0000000000001113","article-title":"Clinical features and treatment of dermatofibrosarcoma protuberans affecting the vulva: a literature review","volume":"43","author":"Nguyen","year":"2017","journal-title":"Dermatol Surg"},{"key":"2025082418261501700_uaaf030-B5","doi-asserted-by":"crossref","first-page":"9","DOI":"10.1016\/j.gore.2019.01.006","article-title":"Dermatofibrosarcoma protuberans: a rare and devastating tumor of the vulva","volume":"28","author":"Neff","year":"2019","journal-title":"Gynecol Oncol Rep"},{"key":"2025082418261501700_uaaf030-B6","first-page":"1289","article-title":"Giant dermatofibrosarcoma protuberans vulvae: rare clinical presentation and literature review","volume":"24","author":"Jeremic","year":"2019","journal-title":"J Buon"},{"key":"2025082418261501700_uaaf030-B7","doi-asserted-by":"crossref","first-page":"366","DOI":"10.1097\/00004347-199910000-00012","article-title":"Dermatofibrosarcoma protuberans of the vulva: clinicopathologic and immunohistochemical analysis of four cases, one with fibrosarcomatous change, and review of the literature","volume":"18","author":"Ghorbani","year":"1999","journal-title":"Int J Gynecol Pathol"},{"key":"2025082418261501700_uaaf030-B8","doi-asserted-by":"crossref","first-page":"393","DOI":"10.1097\/PAS.0b013e3181cf7fc1","article-title":"Dermatofibrosarcoma protuberans of the vulva: a clinicopathologic and immunohistochemical study of 13 cases","volume":"34","author":"Edelweiss","year":"2010","journal-title":"Am J Surg Pathol"},{"key":"2025082418261501700_uaaf030-B9","doi-asserted-by":"crossref","first-page":"651","DOI":"10.1111\/srt.13164","article-title":"Diagnosis and differential diagnosis of dermatofibrosarcoma protuberans: Utility of high-resolution dynamic contrast-enhanced (DCE) MRI","volume":"28","author":"Yu","year":"2022","journal-title":"Skin Res Technol"},{"key":"2025082418261501700_uaaf030-B10","doi-asserted-by":"crossref","first-page":"226","DOI":"10.1097\/DAD.0000000000000421","article-title":"Myxoid dermatofibrosarcoma protuberans of the vulva: case report of a rare variant in an unusual location, with unusual morphologic and immunohistochemical features","volume":"38","author":"Wiszniewska","year":"2016","journal-title":"Am J Dermatopathol"},{"key":"2025082418261501700_uaaf030-B11","first-page":"572","article-title":"Vulvar dermatofibrosarcoma protuberance in Iran and a narrative review of literature: a first case report","volume":"14","author":"Arab","year":"2023","journal-title":"Caspian J Intern Med"},{"key":"2025082418261501700_uaaf030-B12","doi-asserted-by":"crossref","first-page":"245","DOI":"10.1016\/0090-8258(91)90317-X","article-title":"Dermatofibrosarcoma protuberans of the vulva","volume":"41","author":"Leake","year":"1991","journal-title":"Gynecol Oncol"},{"key":"2025082418261501700_uaaf030-B13","first-page":"267","article-title":"Dermatofibrosarcoma protuberans of the vulva. A case report","volume":"41","author":"Karlen","year":"1996","journal-title":"J Reprod Med"}],"container-title":["BJR|Case Reports"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/academic.oup.com\/bjrcr\/advance-article-pdf\/doi\/10.1093\/bjrcr\/uaaf030\/63399900\/uaaf030.pdf","content-type":"application\/pdf","content-version":"am","intended-application":"syndication"},{"URL":"https:\/\/academic.oup.com\/bjrcr\/article-pdf\/11\/4\/uaaf030\/63399900\/uaaf030.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"syndication"},{"URL":"https:\/\/academic.oup.com\/bjrcr\/article-pdf\/11\/4\/uaaf030\/63399900\/uaaf030.pdf","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2025,8,24]],"date-time":"2025-08-24T22:26:23Z","timestamp":1756074383000},"score":1,"resource":{"primary":{"URL":"https:\/\/academic.oup.com\/bjrcr\/article\/doi\/10.1093\/bjrcr\/uaaf030\/8152871"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2025,5,29]]},"references-count":13,"journal-issue":{"issue":"4","published-print":{"date-parts":[[2025,7,6]]}},"URL":"https:\/\/doi.org\/10.1093\/bjrcr\/uaaf030","relation":{},"ISSN":["2055-7159"],"issn-type":[{"type":"electronic","value":"2055-7159"}],"subject":[],"published-other":{"date-parts":[[2025,7]]},"published":{"date-parts":[[2025,5,29]]},"article-number":"uaaf030"}}