{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,24]],"date-time":"2026-10-24T16:32:26Z","timestamp":1792859546531,"version":"4.5.0"},"reference-count":112,"publisher":"Oxford University Press (OUP)","issue":"9","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2011,9]]},"DOI":"10.1093\/brain\/awr189","type":"journal-article","created":{"date-parts":[[2011,8,13]],"date-time":"2011-08-13T00:35:32Z","timestamp":1313195732000},"page":"2478-2492","source":"Crossref","is-referenced-by-count":209,"title":["The clinical diagnosis of early-onset dementias: diagnostic accuracy and clinicopathological relationships"],"prefix":"10.1093","volume":"134","author":[{"given":"Julie S.","family":"Snowden","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Jennifer C.","family":"Thompson","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Cheryl L.","family":"Stopford","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Anna M. T.","family":"Richardson","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Alex","family":"Gerhard","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"David","family":"Neary","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"David M. A.","family":"Mann","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"286","published-online":{"date-parts":[[2011,8,11]]},"reference":[{"key":"key\n\t\t\t\t20170522090100_awr189-B1","doi-asserted-by":"crossref","first-page":"2636","DOI":"10.1093\/brain\/awm213","article-title":"Focal cortical presentations of Alzheimer\u2019s disease","volume":"130","author":"Alladi","year":"2007","journal-title":"Brain"},{"key":"key\n\t\t\t\t20170522090100_awr189-B2","doi-asserted-by":"crossref","first-page":"435","DOI":"10.1002\/ana.21154","article-title":"TDP-43 immunoreactivity in hippocampal sclerosis and Alzheimer\u2019s disease","volume":"61","author":"Amador-Ortiz","year":"2007","journal-title":"Ann Neurol"},{"key":"key\n\t\t\t\t20170522090100_awr189-B3","doi-asserted-by":"crossref","first-page":"77","DOI":"10.1155\/2006\/260734","article-title":"An overview of primary progressive aphasia and its variants","volume":"17","author":"Amici","year":"2006","journal-title":"Behav Neurol"},{"key":"key\n\t\t\t\t20170522090100_awr189-B4","doi-asserted-by":"crossref","first-page":"125","DOI":"10.1007\/s00401-008-0480-1","article-title":"Phosphorylated TDP-43 in Alzheimer\u2019s disease and dementia with Lewy bodies","volume":"117","author":"Arai","year":"2009","journal-title":"Acta Neuropathol"},{"key":"key\n\t\t\t\t20170522090100_awr189-B5","doi-asserted-by":"crossref","first-page":"916","DOI":"10.1038\/nature05016","article-title":"Mutations in Progranulin cause tau-negative frontotemporal dementia linked to chromosome 17","volume":"442","author":"Baker","year":"2006","journal-title":"Nature"},{"key":"key\n\t\t\t\t20170522090100_awr189-B6","doi-asserted-by":"crossref","first-page":"367","DOI":"10.1034\/j.1600-0404.2001.2000236.x","article-title":"Behaviour in frontotemporal dementia, Alzheimer\u2019s disease and vascular dementia","volume":"103","author":"Bathgate","year":"2001","journal-title":"Acta Neurol Scand"},{"key":"key\n\t\t\t\t20170522090100_awr189-B7","doi-asserted-by":"crossref","first-page":"239","DOI":"10.1007\/BF00308809","article-title":"Neuropathological stageing of Alzheimer-related changes","volume":"82","author":"Braak","year":"1991","journal-title":"Acta Neuropathol"},{"key":"key\n\t\t\t\t20170522090100_awr189-B8","doi-asserted-by":"crossref","first-page":"664","DOI":"10.1097\/JGP.0b013e3181a6516e","article-title":"Clinicopathological concordance in dementia diagnostics","volume":"17","author":"Brunnstr\u00f6m","year":"2009","journal-title":"Am J Geriatr Psychiatry"},{"key":"key\n\t\t\t\t20170522090100_awr189-B9","doi-asserted-by":"crossref","first-page":"146","DOI":"10.1016\/j.archger.2008.06.005","article-title":"Prevalence of dementia subtypes: a 30-year retrospective survey of neuropathological reports","volume":"49","author":"Brunnstr\u00f6m","year":"2009","journal-title":"Arch Gerontol Geriatr"},{"key":"key\n\t\t\t\t20170522090100_awr189-B10","doi-asserted-by":"crossref","first-page":"459","DOI":"10.1111\/j.1750-3639.1995.tb00625.x","article-title":"Neuropathological diagnostic criteria for Creutzfeldt-Jakob disease and other human spongiform encephalopathies (prion diseases)","volume":"5","author":"Budka","year":"1995","journal-title":"Brain Pathol"},{"key":"key\n\t\t\t\t20170522090100_awr189-B11","doi-asserted-by":"crossref","first-page":"2","DOI":"10.1007\/s00401-007-0237-2","article-title":"Neuropathologic diagnostic and nosologic criteria for frontotemporal lobar degeneration: consensus of the Consortium for Frontotemporal Lobar Degeneration","volume":"114","author":"Cairns","year":"2007","journal-title":"Acta Neuropathol"},{"key":"key\n\t\t\t\t20170522090100_awr189-B12","doi-asserted-by":"crossref","first-page":"186","DOI":"10.1002\/ana.410120210","article-title":"Biopsy-proved Alzheimer\u2019s disease presenting as a right parietal syndrome","volume":"12","author":"Crystal","year":"1982","journal-title":"Ann Neurol"},{"key":"key\n\t\t\t\t20170522090100_awr189-B13","doi-asserted-by":"crossref","first-page":"42","DOI":"10.1212\/WNL.0b013e3181c7198e","article-title":"Prediction of pathology in primary progressive language and speech disorders","volume":"74","author":"Deramecourt","year":"2010","journal-title":"Neurology"},{"key":"key\n\t\t\t\t20170522090100_awr189-B14","first-page":"101","article-title":"Slowly progressive apraxia","volume":"2","author":"Dick","year":"1989","journal-title":"Behav Neurol"},{"key":"key\n\t\t\t\t20170522090100_awr189-B15","doi-asserted-by":"crossref","first-page":"935","DOI":"10.1093\/jnen\/61.11.935","article-title":"Office of Rare Diseases neuropathologic criteria for corticobasal degeneration","volume":"61","author":"Dickson","year":"2002","journal-title":"J Neuropathol Exp Neurol"},{"key":"key\n\t\t\t\t20170522090100_awr189-B16","doi-asserted-by":"crossref","first-page":"526","DOI":"10.1002\/ana.410430418","article-title":"A permanent pure amnestic syndrome of insidious onset related to Alzheimer\u2019s disease","volume":"43","author":"Didic","year":"1998","journal-title":"Ann Neurol"},{"key":"key\n\t\t\t\t20170522090100_awr189-B17","doi-asserted-by":"crossref","first-page":"602","DOI":"10.1136\/jnnp.72.5.602","article-title":"Qualitative performance characteristics differentiate dementia with Lewy bodies and Alzheimer\u2019s disease","volume":"72","author":"Doubleday","year":"2002","journal-title":"J Neurol Neurosurg Psychiatry"},{"key":"key\n\t\t\t\t20170522090100_awr189-B18","doi-asserted-by":"crossref","first-page":"734","DOI":"10.1016\/S1474-4422(07)70178-3","article-title":"Research criteria for the diagnosis of Alzheimer\u2019s disease: revising the NINCDS-ADRDA criteria","volume":"6","author":"Dubois","year":"2007","journal-title":"Lancet Neurol"},{"key":"key\n\t\t\t\t20170522090100_awr189-B19","doi-asserted-by":"crossref","first-page":"349","DOI":"10.1080\/01688639608408993","article-title":"Neuropsychological subgroups of patients with Alzheimer\u2019s disease","volume":"18","author":"Fisher","year":"1996","journal-title":"J Clin Exp Neuropsychol"},{"key":"key\n\t\t\t\t20170522090100_awr189-B20","doi-asserted-by":"crossref","first-page":"488","DOI":"10.1076\/jcen.21.4.488.887","article-title":"Neuropsychological subgroups of patients with Alzheimer\u2019s disease: an examination of the first 10 years of CERAD data","volume":"21","author":"Fisher","year":"1999","journal-title":"J Clin Exp Neuropsychol"},{"key":"key\n\t\t\t\t20170522090100_awr189-B21","doi-asserted-by":"crossref","first-page":"952","DOI":"10.1002\/ana.20873","article-title":"Frontotemporal dementia: clinicopathological correlations","volume":"59","author":"Forman","year":"2006","journal-title":"Ann Neurol"},{"key":"key\n\t\t\t\t20170522090100_awr189-B22","doi-asserted-by":"crossref","first-page":"961","DOI":"10.1212\/WNL.33.8.961","article-title":"Alzheimer\u2019s disease: focal cortical changes shown by positron emission tomography","volume":"33","author":"Foster","year":"1983","journal-title":"Neurology"},{"key":"key\n\t\t\t\t20170522090100_awr189-B23","doi-asserted-by":"crossref","first-page":"482","DOI":"10.1046\/j.1365-2990.2003.00486.x","article-title":"Neuronal and astrocytic responses involving the serotonergic system in human spongiform encephalopathies","volume":"29","author":"Fraser","year":"2003","journal-title":"Neuropathol Appl Neurobiol"},{"key":"key\n\t\t\t\t20170522090100_awr189-B24","doi-asserted-by":"crossref","first-page":"484","DOI":"10.1093\/brain\/123.3.484","article-title":"Atypical and typical presentations of Alzheimer\u2019s disease: a clinical, neuropsychological, neuroimaging and pathological study of 13 cases","volume":"123","author":"Galton","year":"2000","journal-title":"Brain"},{"key":"key\n\t\t\t\t20170522090100_awr189-B25","doi-asserted-by":"crossref","first-page":"1238","DOI":"10.1001\/archneurol.2010.254","article-title":"Pathological 43-kDa transactivation response DNA-binding protein in older adult with and without severe mental illness","volume":"67","author":"Geser","year":"2010","journal-title":"Arch Neurol"},{"key":"key\n\t\t\t\t20170522090100_awr189-B26","doi-asserted-by":"crossref","first-page":"1227","DOI":"10.1212\/01.wnl.0000320506.79811.da","article-title":"The logopenic\/phonological variant of primary progressive aphasia","volume":"71","author":"Gorno-Tempini","year":"2008","journal-title":"Neurology"},{"key":"key\n\t\t\t\t20170522090100_awr189-B27","doi-asserted-by":"crossref","first-page":"335","DOI":"10.1002\/ana.10825","article-title":"Cognition and anatomy of three variants of primary progressive aphasia","volume":"55","author":"Gorno-Tempini","year":"2004","journal-title":"Ann Neurol"},{"key":"key\n\t\t\t\t20170522090100_awr189-B28","doi-asserted-by":"crossref","first-page":"312","DOI":"10.1136\/jnnp.59.3.312","article-title":"Slowly progressive apraxia in Alzheimer\u2019s disease","volume":"59","author":"Green","year":"1995","journal-title":"J Neurol Neurosurg Psychiatry"},{"key":"key\n\t\t\t\t20170522090100_awr189-B29","doi-asserted-by":"crossref","first-page":"88","DOI":"10.1038\/nrneurol.2009.216","article-title":"Primary progressive aphasia: clinicopathological correlations","volume":"6","author":"Grossman","year":"2010","journal-title":"Nat Rev Neurol"},{"key":"key\n\t\t\t\t20170522090100_awr189-B30","doi-asserted-by":"crossref","first-page":"476","DOI":"10.1159\/000258100","article-title":"Patterns of cortical thickness according to APOE genotype in Alzheimer\u2019s disease","volume":"28","author":"Gutierrez-Galve","year":"2009","journal-title":"Dement Geriatr Cogn Disord"},{"key":"key\n\t\t\t\t20170522090100_awr189-B31","doi-asserted-by":"crossref","first-page":"1461","DOI":"10.1212\/WNL.57.8.1461","article-title":"Apolipoprotein E epsilon 4 and the pattern of regional brain atrophy in Alzheimer\u2019s disease","volume":"57","author":"Hashimoto","year":"2001","journal-title":"Neurology"},{"key":"key\n\t\t\t\t20170522090100_awr189-B32","doi-asserted-by":"crossref","first-page":"208","DOI":"10.1016\/j.parkreldis.2009.11.013","article-title":"Symmetric corticobasal degeneration (S-CBD)","volume":"16","author":"Hassan","year":"2010","journal-title":"Parkinsonism Relat Disord"},{"key":"key\n\t\t\t\t20170522090100_awr189-B33","doi-asserted-by":"crossref","first-page":"1783","DOI":"10.1093\/brain\/115.6.1783","article-title":"Semantic dementia. Progressive fluent aphasia with temporal lobe atrophy","volume":"115","author":"Hodges","year":"1992","journal-title":"Brain"},{"key":"key\n\t\t\t\t20170522090100_awr189-B34","doi-asserted-by":"crossref","first-page":"215","DOI":"10.1007\/BF00304135","article-title":"Posterior cortical atrophy in Alzheimer\u2019s disease \u2013 analysis of a new case and re-evaluation of a historical report","volume":"86","author":"Hof","year":"1993","journal-title":"Acta Neuropathol"},{"key":"key\n\t\t\t\t20170522090100_awr189-B35","doi-asserted-by":"crossref","first-page":"168","DOI":"10.1097\/00005072-199003000-00008","article-title":"Selective disconnection of specific visual association pathways in cases of Alzheimer\u2019s disease presenting with Balint\u2019s syndrome","volume":"49","author":"Hof","year":"1990","journal-title":"J Neuropath Exp Neurol"},{"key":"key\n\t\t\t\t20170522090100_awr189-B36","doi-asserted-by":"crossref","first-page":"45","DOI":"10.1192\/bjp.174.1.45","article-title":"Validity of current clinical criteria for Alzheimer\u2019s disease, vascular dementia and dementia with Lewy bodies","volume":"174","author":"Holmes","year":"1999","journal-title":"Br J Psychiatry"},{"key":"key\n\t\t\t\t20170522090100_awr189-B37","doi-asserted-by":"crossref","first-page":"215","DOI":"10.1007\/s00401-008-0400-4","article-title":"Temporal lobar predominance of TDP-43 neuronal cytoplasmic inclusions in Alzheimer\u2019s disease","volume":"116","author":"Hu","year":"2008","journal-title":"Acta Neuropathol"},{"key":"key\n\t\t\t\t20170522090100_awr189-B38","doi-asserted-by":"crossref","first-page":"1375","DOI":"10.1002\/mds.22574","article-title":"Alzheimer\u2019s disease and corticobasal degeneration presenting as corticobasal syndrome","volume":"24","author":"Hu","year":"2009","journal-title":"Mov Disord"},{"key":"key\n\t\t\t\t20170522090100_awr189-B39","doi-asserted-by":"crossref","first-page":"909","DOI":"10.1212\/WNL.38.6.909","article-title":"Longitudinal studies of regional cerebral metabolism in Alzheimer\u2019s disease","volume":"38","author":"Jagust","year":"1988","journal-title":"Neurology"},{"key":"key\n\t\t\t\t20170522090100_awr189-B40","doi-asserted-by":"crossref","first-page":"61","DOI":"10.3233\/JAD-2006-9S308","article-title":"Clinicopathological analysis of dementia disorders in the elderly \u2013 an update","volume":"9","author":"Jellinger","year":"2006","journal-title":"J Alzheimers Dis"},{"key":"key\n\t\t\t\t20170522090100_awr189-B41","doi-asserted-by":"crossref","first-page":"1233","DOI":"10.1001\/archneur.56.10.1233","article-title":"Clinical and pathological evidence for a frontal variant of Alzheimer\u2019s disease","volume":"56","author":"Johnson","year":"1999","journal-title":"Arch Neurol"},{"key":"key\n\t\t\t\t20170522090100_awr189-B42","doi-asserted-by":"crossref","first-page":"1385","DOI":"10.1093\/brain\/awl078","article-title":"Clinicopathological and imaging correlates of progressive aphasia and apraxia of speech","volume":"129","author":"Josephs","year":"2006","journal-title":"Brain"},{"key":"key\n\t\t\t\t20170522090100_awr189-B43","doi-asserted-by":"crossref","first-page":"137","DOI":"10.1007\/s00401-011-0839-6","article-title":"Neuropathological background of phenotypical variability in frontotemporal dementia","volume":"122","author":"Josephs","year":"2011","journal-title":"Acta Neuropathol"},{"key":"key\n\t\t\t\t20170522090100_awr189-B44","doi-asserted-by":"crossref","first-page":"41","DOI":"10.1212\/01.wnl.0000191307.69661.c3","article-title":"Clinicopathologic analysis of frontotemporal and corticobasal degenerations and PSP","volume":"66","author":"Josephs","year":"2006","journal-title":"Neurology"},{"key":"key\n\t\t\t\t20170522090100_awr189-B45","doi-asserted-by":"crossref","first-page":"349","DOI":"10.1007\/s00401-009-0547-7","article-title":"Evaluation of subcortical pathology and clinical correlations in FTLD-U subtypes","volume":"118","author":"Josephs","year":"2009","journal-title":"Acta Neuropathol"},{"key":"key\n\t\t\t\t20170522090100_awr189-B46","doi-asserted-by":"crossref","first-page":"311","DOI":"10.1097\/01.nrl.0000094943.84390.cf","article-title":"Pick complex: an integrative approach to frontotemporal dementia: primary progressive aphasia, corticobasal degeneration and progressive supranuclear palsy","volume":"9","author":"Kertesz","year":"2003","journal-title":"Neurologist"},{"key":"key\n\t\t\t\t20170522090100_awr189-B47","doi-asserted-by":"crossref","first-page":"1996","DOI":"10.1093\/brain\/awh598","article-title":"The evolution and pathology of frontotemporal dementia","volume":"128","author":"Kertesz","year":"2005","journal-title":"Brain"},{"key":"key\n\t\t\t\t20170522090100_awr189-B48","doi-asserted-by":"crossref","first-page":"156","DOI":"10.1002\/ana.20700","article-title":"Clinical and pathological characterization of progressive aphasia","volume":"59","author":"Knibb","year":"2006","journal-title":"Ann Neurol"},{"key":"key\n\t\t\t\t20170522090100_awr189-B49","doi-asserted-by":"crossref","first-page":"480","DOI":"10.1002\/ana.20425","article-title":"Antemortem diagnosis of frontotemporal lobar degeneration","volume":"57","author":"Knopman","year":"2005","journal-title":"Ann Neurol"},{"key":"key\n\t\t\t\t20170522090100_awr189-B50","doi-asserted-by":"crossref","first-page":"1364","DOI":"10.1212\/WNL.40.9.1364","article-title":"The validity of three clinical diagnostic criteria for Alzheimer\u2019s disease","volume":"40","author":"Kukull","year":"1990","journal-title":"Neurology"},{"key":"key\n\t\t\t\t20170522090100_awr189-B51","doi-asserted-by":"crossref","first-page":"65","DOI":"10.1016\/0306-4522(95)00014-A","article-title":"Volumes of hippocampus, amygdala and frontal-lobe in Alzheimer patients with different apolipoprotein-E genotypes","volume":"67","author":"Lehtovirta","year":"1995","journal-title":"Neuroscience"},{"key":"key\n\t\t\t\t20170522090100_awr189-B52","doi-asserted-by":"crossref","first-page":"305","DOI":"10.1212\/WNL.43.2.305","article-title":"The visual variant of Alzheimer\u2019s disease","volume":"43","author":"Levine","year":"1993","journal-title":"Neurology"},{"key":"key\n\t\t\t\t20170522090100_awr189-B53","doi-asserted-by":"crossref","first-page":"2045","DOI":"10.1093\/brain\/awq123","article-title":"Does corticobasal degeneration exist? A clinicopathological re-evaluation","volume":"133","author":"Ling","year":"2010","journal-title":"Brain"},{"key":"key\n\t\t\t\t20170522090100_awr189-B54","doi-asserted-by":"crossref","first-page":"467","DOI":"10.1002\/mds.10459","article-title":"SIC task force appraisal of clinical diagnostic criteria for parkinsonian disorders","volume":"18","author":"Litvan","year":"2003","journal-title":"Mov Disord"},{"key":"key\n\t\t\t\t20170522090100_awr189-B55","doi-asserted-by":"crossref","first-page":"1","DOI":"10.1007\/BF03161075","article-title":"Clinical features differentiating patients with postmortem confirmed progressive supranuclear palsy and corticobasal degeneration","volume":"246","author":"Litvan","year":"1999","journal-title":"J Neurol"},{"key":"key\n\t\t\t\t20170522090100_awr189-B56","doi-asserted-by":"crossref","first-page":"488","DOI":"10.1007\/s00415-008-0565-8","article-title":"Clinicopathological and genetic correlates of frontotemporal lobar degeneration and corticobasal degeneration","volume":"255","author":"Llado","year":"2008","journal-title":"J Neurol"},{"key":"key\n\t\t\t\t20170522090100_awr189-B57","first-page":"416","article-title":"Consensus on clinical and neuropathological criteria for fronto-temporal dementia","volume":"4","author":"Lund and Manchester groups","year":"1994","journal-title":"J Neurol Neurosurg Psychiatry"},{"key":"key\n\t\t\t\t20170522090100_awr189-B58","doi-asserted-by":"crossref","first-page":"539","DOI":"10.1007\/s00401-006-0138-9","article-title":"Heterogeneity of ubiquitin pathology in frontotemporal lobar degeneration: classification and relation to clinical phenotype","volume":"112","author":"Mackenzie","year":"2006","journal-title":"Acta Neuropathol"},{"key":"key\n\t\t\t\t20170522090100_awr189-B59","doi-asserted-by":"crossref","first-page":"111","DOI":"10.1007\/s00401-011-0845-8","article-title":"A harmonized classification system for FTLD-TDP pathology","volume":"122","author":"Mackenzie","year":"2011","journal-title":"Acta Neuropathol"},{"key":"key\n\t\t\t\t20170522090100_awr189-B60","doi-asserted-by":"crossref","first-page":"15","DOI":"10.1007\/s00401-008-0460-5","article-title":"Nomenclature for neuropathologic subtypes of frontotemporal lobar degeneration: consensus recommendations","volume":"117","author":"Mackenzie","year":"2009","journal-title":"Acta Neuropathol"},{"key":"key\n\t\t\t\t20170522090100_awr189-B61","doi-asserted-by":"crossref","first-page":"1","DOI":"10.1007\/s00401-009-0612-2","article-title":"Nomenclature for neuropathologic subtypes of frontotemporal lobar degeneration: consensus recommendations: an update","volume":"119","author":"Mackenzie","year":"2010","journal-title":"Acta Neuropathol"},{"key":"key\n\t\t\t\t20170522090100_awr189-B62","first-page":"143","article-title":"Neuropsychology of Alzheimer\u2019s disease: the case for subgroups","volume-title":"Modular deficits in Alzheimer-type dementia","author":"Martin","year":"1990"},{"key":"key\n\t\t\t\t20170522090100_awr189-B63","doi-asserted-by":"crossref","first-page":"594","DOI":"10.1080\/01688638608405178","article-title":"Towards a behavioral typology of Alzheimer\u2019s patients","volume":"8","author":"Martin","year":"1986","journal-title":"J Clin Exp Neuropsychol"},{"key":"key\n\t\t\t\t20170522090100_awr189-B64","doi-asserted-by":"crossref","first-page":"1863","DOI":"10.1212\/01.wnl.0000187889.17253.b1","article-title":"Diagnosis and management of dementia with Lewy bodies. Third report of the DLB consortium","volume":"65","author":"McKeith","year":"2005","journal-title":"Neurology"},{"key":"key\n\t\t\t\t20170522090100_awr189-B65","doi-asserted-by":"crossref","first-page":"1113","DOI":"10.1212\/WNL.47.5.1113","article-title":"Consensus guidelines for the clinical and pathologic diagnosis of dementia with Lewy bodies (DLB)","volume":"47","author":"McKeith","year":"1996","journal-title":"Neurology"},{"key":"key\n\t\t\t\t20170522090100_awr189-B66","doi-asserted-by":"crossref","first-page":"939","DOI":"10.1212\/WNL.34.7.939","article-title":"Clinical diagnosis of Alzheimer\u2019s disease: report of the NINCDS-ADRDA work group under the auspices of department of health and human services task force on Alzheimer\u2019s disease","volume":"34","author":"McKhann","year":"1984","journal-title":"Neurology"},{"key":"key\n\t\t\t\t20170522090100_awr189-B67","doi-asserted-by":"crossref","first-page":"350","DOI":"10.1136\/jnnp.2006.106054","article-title":"Accuracy of SPECT in differentiating frontotemporal dementia from Alzheimer\u2019s disease","volume":"78","author":"McNeill","year":"2007","journal-title":"J Neurol Neurosurg Psychiatry"},{"key":"key\n\t\t\t\t20170522090100_awr189-B68","doi-asserted-by":"crossref","first-page":"592","DOI":"10.1002\/ana.410110607","article-title":"Slowly progressive aphasia without generalized dementia","volume":"11","author":"Mesulam","year":"1982","journal-title":"Ann Neurol"},{"key":"key\n\t\t\t\t20170522090100_awr189-B69","doi-asserted-by":"crossref","first-page":"425","DOI":"10.1002\/ana.91","article-title":"Primary progressive aphasia","volume":"49","author":"Mesulam","year":"2001","journal-title":"Ann Neurol"},{"key":"key\n\t\t\t\t20170522090100_awr189-B70","doi-asserted-by":"crossref","first-page":"709","DOI":"10.1002\/ana.21388","article-title":"Alzheimer and frontotemporal pathology in subsets of primary progressive aphasia","volume":"63","author":"Mesulam","year":"2008","journal-title":"Ann Neurol"},{"key":"key\n\t\t\t\t20170522090100_awr189-B71","doi-asserted-by":"crossref","first-page":"1545","DOI":"10.1001\/archneurol.2009.288","article-title":"Quantitative template for subtyping primary progressive aphasia","volume":"66","author":"Mesulam","year":"2009","journal-title":"Arch Neurol"},{"key":"key\n\t\t\t\t20170522090100_awr189-B72","doi-asserted-by":"crossref","first-page":"1374","DOI":"10.1212\/WNL.41.9.1374","article-title":"Frontal lobe degeneration: clinical, neuropsychological and SPECT characteristics","volume":"41","author":"Miller","year":"1991","journal-title":"Neurology"},{"key":"key\n\t\t\t\t20170522090100_awr189-B73","doi-asserted-by":"crossref","first-page":"85","DOI":"10.1002\/ana.410420114","article-title":"Metabolic reduction in the posterior cingulate cortex in very early Alzheimer\u2019s disease","volume":"42","author":"Minoshima","year":"1997","journal-title":"Ann Neurol"},{"key":"key\n\t\t\t\t20170522090100_awr189-B74","doi-asserted-by":"crossref","first-page":"479","DOI":"10.1212\/WNL.41.4.479","article-title":"The consortium to establish a registry for Alzheimer\u2019s disease. Part II. Standardization of the neuropathologic assessment of Alzheimer\u2019s disease","volume":"41","author":"Mirra","year":"1991","journal-title":"Neurology"},{"key":"key\n\t\t\t\t20170522090100_awr189-B75","doi-asserted-by":"crossref","first-page":"163","DOI":"10.1136\/jnnp.49.2.163","article-title":"Neuropsychological syndromes in presenile dementia due to cerebral atrophy","volume":"49","author":"Neary","year":"1986","journal-title":"J Neurol Neurosurg Psychiatry"},{"key":"key\n\t\t\t\t20170522090100_awr189-B76","doi-asserted-by":"crossref","first-page":"1546","DOI":"10.1212\/WNL.51.6.1546","article-title":"Frontotemporal lobar degeneration. A consensus on clinical diagnostic criteria","volume":"51","author":"Neary","year":"1998","journal-title":"Neurology"},{"key":"key\n\t\t\t\t20170522090100_awr189-B77","doi-asserted-by":"crossref","first-page":"771","DOI":"10.1016\/S1474-4422(05)70223-4","article-title":"Frontotemporal dementia","volume":"4","author":"Neary","year":"2005","journal-title":"Lancet Neurol"},{"key":"key\n\t\t\t\t20170522090100_awr189-B78","doi-asserted-by":"crossref","first-page":"23","DOI":"10.1136\/jnnp.53.1.23","article-title":"Frontal lobe dementia and motor neurone disease","volume":"53","author":"Neary","year":"1990","journal-title":"J Neurol Neurosurg Psychiatry"},{"key":"key\n\t\t\t\t20170522090100_awr189-B79","doi-asserted-by":"crossref","first-page":"353","DOI":"10.1136\/jnnp.51.3.353","article-title":"Dementia of frontal lobe type","volume":"51","author":"Neary","year":"1988","journal-title":"J Neurol Neurosurg Psychiatry"},{"key":"key\n\t\t\t\t20170522090100_awr189-B80","doi-asserted-by":"crossref","first-page":"1101","DOI":"10.1136\/jnnp.50.9.1101","article-title":"Single photon emission tomography using 99mTc-HM-PAO in the investigation of dementia","volume":"50","author":"Neary","year":"1987","journal-title":"J Neurol Neurosurg Psychiatry"},{"key":"key\n\t\t\t\t20170522090100_awr189-B81","doi-asserted-by":"crossref","first-page":"140","DOI":"10.1111\/j.1440-1789.2009.01062.x","article-title":"Alzheimer\u2019s disease: report of two autopsy cases with a clinical diagnosis of corticobasal degeneration","volume":"30","author":"Okazaki","year":"2010","journal-title":"Neuropathology"},{"key":"key\n\t\t\t\t20170522090100_awr189-B82","doi-asserted-by":"crossref","first-page":"2441","DOI":"10.1093\/brain\/awh265","article-title":"Frontotemporal lobar degeneration with ubiquitin-only-immunoreactive neuronal changes: broadening the clinical picture to include progressive supranuclear palsy","volume":"127","author":"Paviour","year":"2004","journal-title":"Brain"},{"key":"key\n\t\t\t\t20170522090100_awr189-B83","doi-asserted-by":"crossref","first-page":"2277","DOI":"10.1212\/WNL.54.12.2277","article-title":"Differentiating frontal and temporal variant frontotemporal dementia from Alzheimer\u2019s disease","volume":"54","author":"Perry","year":"2000","journal-title":"Neurology"},{"key":"key\n\t\t\t\t20170522090100_awr189-B84","doi-asserted-by":"crossref","first-page":"721","DOI":"10.1093\/brain\/awm331","article-title":"Frequency and clinical characteristics of progranulin mutation carriers in the Manchester Frontotemporal Lobar Degeneration cohort: comparison to patients with MAPT and no known mutations","volume":"131","author":"Pickering-Brown","year":"2008","journal-title":"Brain"},{"key":"key\n\t\t\t\t20170522090100_awr189-B85","first-page":"181","article-title":"Alzheimer\u2019s disease presenting as slowly progressive aphasia","volume":"67","author":"Pogacar","year":"1984","journal-title":"R I Med J"},{"key":"key\n\t\t\t\t20170522090100_awr189-B86","doi-asserted-by":"crossref","first-page":"931","DOI":"10.1001\/archneur.1993.00540090038008","article-title":"Neuropsychological patterns and language deficits in 20 consecutive cases of autopsy-confirmed Alzheimer\u2019s disease","volume":"50","author":"Price","year":"1993","journal-title":"Arch Neurol"},{"key":"key\n\t\t\t\t20170522090100_awr189-B87","doi-asserted-by":"crossref","first-page":"388","DOI":"10.1002\/ana.21451","article-title":"A\u03b2 Amyloid and glucose metabolism in three variants of primary progressive aphasia","volume":"64","author":"Rabinovici","year":"2008","journal-title":"Ann Neurol"},{"key":"key\n\t\t\t\t20170522090100_awr189-B88","doi-asserted-by":"crossref","first-page":"474","DOI":"10.1177\/1533317507308779","article-title":"Distinct MRI atrophy patterns in autopsy-proven Alzheimer\u2019s disease and frontotemporal lobar degeneration","volume":"22","author":"Rabinovici","year":"2007","journal-title":"Am J Alzheimers dis other demen"},{"key":"key\n\t\t\t\t20170522090100_awr189-B89","doi-asserted-by":"crossref","first-page":"984","DOI":"10.1016\/j.neuroimage.2009.08.002","article-title":"Progressive logopenic\/phonological aphasia: erosion of the language network","volume":"49","author":"Rohrer","year":"2010","journal-title":"Neuroimage"},{"key":"key\n\t\t\t\t20170522090100_awr189-B90","doi-asserted-by":"crossref","first-page":"388","DOI":"10.1136\/jnnp.61.4.388","article-title":"Progressive biparietal atrophy: an atypical presentation of Alzheimer\u2019s disease","volume":"61","author":"Ross","year":"1996","journal-title":"J Neurol Neurosurg Psychiatry"},{"key":"key\n\t\t\t\t20170522090100_awr189-B91","doi-asserted-by":"crossref","first-page":"1343","DOI":"10.2353\/ajpath.2006.060438","article-title":"Pathological heterogeneity of frontotemporal lobar degeneration with ubiquitin-positive inclusions delineated by ubiquitin immunohistochemistry and novel monoclonal antibodies","volume":"169","author":"Sampathu","year":"2006","journal-title":"Am J Pathol"},{"key":"key\n\t\t\t\t20170522090100_awr189-B92","doi-asserted-by":"crossref","first-page":"S21","DOI":"10.1002\/mds.20536","article-title":"Progressive supranuclear palsy and corticobasal degeneration: lumping versus splitting","volume":"20","author":"Scaravilli","year":"2005","journal-title":"Mov Disord"},{"key":"key\n\t\t\t\t20170522090100_awr189-B93","doi-asserted-by":"crossref","first-page":"155","DOI":"10.1001\/archneur.63.1.155","article-title":"Apolipoprotein E genotype modifies the phenotype of Alzheimer\u2019s disease","volume":"63","author":"Schott","year":"2006","journal-title":"Arch Neurol"},{"key":"key\n\t\t\t\t20170522090100_awr189-B94","doi-asserted-by":"crossref","first-page":"1593","DOI":"10.1002\/mds.22558","article-title":"Is the pathology of corticobasal syndrome predictable in life?","volume":"24","author":"Shelley","year":"2009","journal-title":"Mov Disord"},{"key":"key\n\t\t\t\t20170522090100_awr189-B95","doi-asserted-by":"crossref","first-page":"323","DOI":"10.1136\/jnnp.70.3.323","article-title":"Distinct behavioural profiles in frontotemporal dementia and semantic dementia","volume":"70","author":"Snowden","year":"2001","journal-title":"J Neurol Neurosurg Psychiatry"},{"key":"key\n\t\t\t\t20170522090100_awr189-B96","doi-asserted-by":"crossref","first-page":"167","DOI":"10.1155\/1989\/124043","article-title":"Semantic dementia: a form of circumscribed cerebral atrophy","volume":"2","author":"Snowden","year":"1989","journal-title":"Behav Neurol"},{"key":"key\n\t\t\t\t20170522090100_awr189-B97","doi-asserted-by":"crossref","DOI":"10.1007\/s00401-011-0816-0","article-title":"The most common type of FTLD-FUS (aFTLD-U) pathology is associated with a distinct clinical form of frontotemporal dementia but is not related to mutations in the FUS gene","author":"Snowden","year":"2011","journal-title":"Acta Neuropathol"},{"key":"key\n\t\t\t\t20170522090100_awr189-B98","doi-asserted-by":"crossref","first-page":"27","DOI":"10.1076\/neur.9.1.27.14368","article-title":"Progressive anomia with preserved oral spelling and automatic speech","volume":"9","author":"Snowden","year":"2003","journal-title":"Neurocase"},{"key":"key\n\t\t\t\t20170522090100_awr189-B99","volume-title":"Frontotemporal lobar degeneration: frontotemporal dementia, progressive aphasia and semantic dementia","author":"Snowden","year":"1996"},{"key":"key\n\t\t\t\t20170522090100_awr189-B100","doi-asserted-by":"crossref","first-page":"31","DOI":"10.1007\/s00401-007-0236-3","article-title":"Frontotemporal lobar degeneration: clinical and pathological relationships","volume":"114","author":"Snowden","year":"2007","journal-title":"Acta Neuropathol"},{"key":"key\n\t\t\t\t20170522090100_awr189-B101","doi-asserted-by":"crossref","first-page":"174","DOI":"10.1002\/ana.410310208","article-title":"Progressive language disorder due to lobar atrophy","volume":"31","author":"Snowden","year":"1992","journal-title":"Ann Neurol"},{"key":"key\n\t\t\t\t20170522090100_awr189-B102","doi-asserted-by":"crossref","first-page":"366","DOI":"10.1080\/13554790701851510","article-title":"Progressive anomia revisited: focal degeneration associated with progranulin gene mutation","volume":"13","author":"Snowden","year":"2007","journal-title":"Neurocase"},{"key":"key\n\t\t\t\t20170522090100_awr189-B103","doi-asserted-by":"crossref","first-page":"835","DOI":"10.1016\/S0010-9452(08)70683-X","article-title":"Cognitive phenotypes in Alzheimer\u2019s disease and genetic risk","volume":"43","author":"Snowden","year":"2007","journal-title":"Cortex"},{"key":"key\n\t\t\t\t20170522090100_awr189-B104","doi-asserted-by":"crossref","first-page":"846","DOI":"10.1016\/S0010-9452(08)70684-1","article-title":"Distinct memory profiles in Alzheimer\u2019s disease","volume":"43","author":"Stopford","year":"2007","journal-title":"Cortex"},{"key":"key\n\t\t\t\t20170522090100_awr189-B105","doi-asserted-by":"crossref","first-page":"185","DOI":"10.1016\/j.cortex.2005.11.002","article-title":"Variability in cognitive presentation of Alzheimer\u2019s disease","volume":"44","author":"Stopford","year":"2008","journal-title":"Cortex"},{"key":"key\n\t\t\t\t20170522090100_awr189-B106","doi-asserted-by":"crossref","first-page":"579","DOI":"10.1007\/BF00868810","article-title":"The contribution of single photon emission tomography to the clinical differentiation of degenerative cortical brain disorders","volume":"242","author":"Talbot","year":"1995","journal-title":"J Neurol"},{"key":"key\n\t\t\t\t20170522090100_awr189-B107","doi-asserted-by":"crossref","first-page":"365","DOI":"10.1007\/s00401-009-0605-1","article-title":"Sporadic corticobasal syndrome due to FTLD-TDP","volume":"119","author":"Tartaglia","year":"2011","journal-title":"Acta Neuropathol"},{"key":"key\n\t\t\t\t20170522090100_awr189-B108","doi-asserted-by":"crossref","first-page":"920","DOI":"10.1136\/jnnp.2003.033779","article-title":"Qualitative neuropsychological performance characteristics in frontotemporal dementia and Alzheimer\u2019s disease","volume":"76","author":"Thompson","year":"2005","journal-title":"J Neurol Neurosurg Psychiatry"},{"key":"key\n\t\t\t\t20170522090100_awr189-B109","doi-asserted-by":"crossref","first-page":"555","DOI":"10.1097\/NEN.0b013e31817713b5","article-title":"Concomitant TAR-DNA-binding protein 43 pathology is present in Alzheimer disease and corticobasal degeneration but not in other tauopathies","volume":"67","author":"Uryu","year":"2008","journal-title":"J Neuropathol Exp Neurol"},{"key":"key\n\t\t\t\t20170522090100_awr189-B110","volume-title":"Visual Object and Space Perception Battery (VOSP)","author":"Warrington","year":"1991"},{"key":"key\n\t\t\t\t20170522090100_awr189-B111","doi-asserted-by":"crossref","first-page":"1480","DOI":"10.1093\/brain\/awh560","article-title":"Apraxia in movement disorders","volume":"128","author":"Zadikoff","year":"2005","journal-title":"Brain"},{"key":"key\n\t\t\t\t20170522090100_awr189-B112","doi-asserted-by":"crossref","first-page":"2659","DOI":"10.1093\/brain\/awp191","article-title":"Updated clinical diagnostic criteria for sporadic Creutzfeldt-Jakob disease","volume":"132","author":"Zerr","year":"2009","journal-title":"Brain"}],"container-title":["Brain"],"original-title":[],"language":"en","link":[{"URL":"http:\/\/academic.oup.com\/brain\/article-pdf\/134\/9\/2478\/17346636\/awr189.pdf","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2021,11,30]],"date-time":"2021-11-30T10:34:32Z","timestamp":1638268472000},"score":1,"resource":{"primary":{"URL":"https:\/\/academic.oup.com\/brain\/article-lookup\/doi\/10.1093\/brain\/awr189"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2011,8,11]]},"references-count":112,"journal-issue":{"issue":"9","published-online":{"date-parts":[[2011,8,11]]},"published-print":{"date-parts":[[2011,9]]}},"URL":"https:\/\/doi.org\/10.1093\/brain\/awr189","relation":{},"ISSN":["1460-2156","0006-8950"],"issn-type":[{"value":"1460-2156","type":"electronic"},{"value":"0006-8950","type":"print"}],"subject":[],"published":{"date-parts":[[2011,8,11]]}}}