{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,6]],"date-time":"2026-10-06T23:40:01Z","timestamp":1791330001481,"version":"4.3.1"},"reference-count":70,"publisher":"Oxford University Press (OUP)","issue":"9","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2011,9]]},"DOI":"10.1093\/brain\/awr195","type":"journal-article","created":{"date-parts":[[2011,8,13]],"date-time":"2011-08-13T00:35:32Z","timestamp":1313195732000},"page":"2582-2594","source":"Crossref","is-referenced-by-count":329,"title":["Motor Neuron dysfunction in frontotemporal dementia"],"prefix":"10.1093","volume":"134","author":[{"given":"James R.","family":"Burrell","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Matthew C.","family":"Kiernan","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Steve","family":"Vucic","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"John R.","family":"Hodges","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"286","published-online":{"date-parts":[[2011,8,11]]},"reference":[{"key":"key\n\t\t\t\t20170624055815_awr195-B1","doi-asserted-by":"crossref","first-page":"275","DOI":"10.1111\/j.1600-0404.2008.01017.x","article-title":"The contribution of TMS to frontotemporal dementia variants","volume":"118","author":"Alberici","year":"2008","journal-title":"Acta Neurol Scand"},{"key":"key\n\t\t\t\t20170624055815_awr195-B2","doi-asserted-by":"crossref","first-page":"103","DOI":"10.1093\/brain\/124.1.103","article-title":"Selective impairment of verb processing associated with pathological changes in Brodmann areas 44 and 45 in the motoneurone disease\u2013dementia\u2013aphasia syndrome","volume":"124","author":"Bak","year":"2001","journal-title":"Brain"},{"key":"key\n\t\t\t\t20170624055815_awr195-B3","doi-asserted-by":"crossref","first-page":"470","DOI":"10.1002\/ana.21612","article-title":"TARDBP mutations in motoneuron disease with frontotemporal lobar degeneration","volume":"65","author":"Benajiba","year":"2009","journal-title":"Ann Neurol"},{"key":"key\n\t\t\t\t20170624055815_awr195-B4","doi-asserted-by":"crossref","first-page":"639","DOI":"10.1136\/jnnp.2009.194399","article-title":"FUS mutations in amyotrophic lateral sclerosis: clinical, pathological, neurophysiological and genetic analysis","volume":"81","author":"Blair","year":"2010","journal-title":"J Neurol Neurosurg Psychiatr"},{"key":"key\n\t\t\t\t20170624055815_awr195-B5","doi-asserted-by":"crossref","first-page":"E974","DOI":"10.1002\/humu.21100","article-title":"Mutation within TARDBP leads to frontotemporal dementia without motoneuron disease","volume":"30","author":"Borroni","year":"2009","journal-title":"Hum Mutat"},{"key":"key\n\t\t\t\t20170624055815_awr195-B6","doi-asserted-by":"crossref","first-page":"196","DOI":"10.1136\/jnnp.2009.204081","article-title":"Clinical, neuroimaging and neuropathological features of a new chromosome 9p-linked FTD-ALS family","volume":"82","author":"Boxer","year":"2011","journal-title":"J Neurol Neurosurg Psychiatry"},{"key":"key\n\t\t\t\t20170624055815_awr195-B7","doi-asserted-by":"crossref","first-page":"293","DOI":"10.1080\/146608200300079536","article-title":"El Escorial revisited: revised criteria for the diagnosis of amyotrophic lateral sclerosis","volume":"1","author":"Brooks","year":"2000","journal-title":"Amyotroph Lateral Scler Other Motoneuron Disord"},{"key":"key\n\t\t\t\t20170624055815_awr195-B8","doi-asserted-by":"crossref","first-page":"283","DOI":"10.3109\/17482968.2011.551940","article-title":"Isolated bulbar phenotype of amyotrophic lateral sclerosis","volume":"12","author":"Burrell","year":"2011","journal-title":"Amyotroph Lateral Scler"},{"key":"key\n\t\t\t\t20170624055815_awr195-B9","doi-asserted-by":"crossref","first-page":"5","DOI":"10.1007\/s00401-007-0237-2","article-title":"Neuropathologic diagnostic and nosologic criteria for frontotemporal lobar degeneration: consensus of the Consortium for Frontotemporal Lobar Degeneration","volume":"114","author":"Cairns","year":"2007","journal-title":"Acta Neuropathol"},{"key":"key\n\t\t\t\t20170624055815_awr195-B10","doi-asserted-by":"crossref","first-page":"1951","DOI":"10.1212\/WNL.42.10.1951","article-title":"Magnetic brain stimulation: the silent period after the motor evoked potential","volume":"42","author":"Cantello","year":"1992","journal-title":"Neurology"},{"key":"key\n\t\t\t\t20170624055815_awr195-B11","doi-asserted-by":"crossref","first-page":"13","DOI":"10.1016\/S0022-510X(99)00210-5","article-title":"The ALSFRS-R: a revised ALS functional rating scale that incorporates assessments of respiratory function. BDNF ALS Study Group (Phase III)","volume":"169","author":"Cedarbaum","year":"1999","journal-title":"J Neurol Sci"},{"key":"key\n\t\t\t\t20170624055815_awr195-B12","doi-asserted-by":"crossref","first-page":"75","DOI":"10.1212\/01.wnl.0000167602.38643.29","article-title":"A voxel-based morphometry study of patterns of brain atrophy in ALS and ALS\/FTLD","volume":"65","author":"Chang","year":"2005","journal-title":"Neurology"},{"key":"key\n\t\t\t\t20170624055815_awr195-B13","doi-asserted-by":"crossref","first-page":"504","DOI":"10.1016\/j.clinph.2007.10.014","article-title":"The clinical diagnostic utility of transcranial magnetic stimulation: report of an IFCN committee","volume":"119","author":"Chen","year":"2008","journal-title":"Clin Neurophysiol"},{"key":"key\n\t\t\t\t20170624055815_awr195-B14","doi-asserted-by":"crossref","first-page":"489","DOI":"10.1001\/archneur.63.4.489","article-title":"Frontotemporal lobar degeneration with motoneuron disease: a clinical and pathological spectrum","volume":"63","author":"Clark","year":"2006","journal-title":"Arch Neurol"},{"key":"key\n\t\t\t\t20170624055815_awr195-B15","doi-asserted-by":"crossref","first-page":"1125","DOI":"10.1002\/mus.880131207","article-title":"Central motor conduction: method and normal results","volume":"13","author":"Claus","year":"1990","journal-title":"Muscle Nerve"},{"key":"key\n\t\t\t\t20170624055815_awr195-B16","doi-asserted-by":"crossref","first-page":"1984","DOI":"10.1093\/brain\/awh582","article-title":"The pathological basis of semantic dementia","volume":"128","author":"Davies","year":"2005","journal-title":"Brain"},{"key":"key\n\t\t\t\t20170624055815_awr195-B17","doi-asserted-by":"crossref","first-page":"1627","DOI":"10.1001\/archneur.63.11.1627","article-title":"Progression in frontotemporal dementia: identifying a benign behavioral variant by magnetic resonance imaging","volume":"63","author":"Davies","year":"2006","journal-title":"Arch Neurol"},{"key":"key\n\t\t\t\t20170624055815_awr195-B18","doi-asserted-by":"crossref","first-page":"497","DOI":"10.1016\/j.clinph.2007.09.143","article-title":"Electrodiagnostic criteria for diagnosis of ALS","volume":"119","author":"de Carvalho","year":"2008","journal-title":"Clin Neurophysiol"},{"key":"key\n\t\t\t\t20170624055815_awr195-B19","doi-asserted-by":"crossref","first-page":"630","DOI":"10.1002\/mus.10469","article-title":"Clinical and neurophysiological evaluation of progression in amyotrophic lateral sclerosis","volume":"28","author":"de Carvalho","year":"2003","journal-title":"Muscle Nerve"},{"key":"key\n\t\t\t\t20170624055815_awr195-B20","doi-asserted-by":"crossref","first-page":"208","DOI":"10.1002\/mus.21495","article-title":"Sensitivity of electrophysiological tests for upper and lower motoneuron dysfunction in ALS: a six-month longitudinal study","volume":"41","author":"de Carvalho","year":"2010","journal-title":"Muscle Nerve"},{"key":"key\n\t\t\t\t20170624055815_awr195-B21","doi-asserted-by":"crossref","first-page":"219","DOI":"10.1002\/mus.880150215","article-title":"Amyotrophic lateral sclerosis (ALS): a phylogenetic disease of the corticomotoneuron?","volume":"15","author":"Eisen","year":"1992","journal-title":"Muscle Nerve"},{"key":"key\n\t\t\t\t20170624055815_awr195-B22","doi-asserted-by":"crossref","first-page":"146","DOI":"10.1002\/mus.880130211","article-title":"Cortical magnetic stimulation in amyotrophic lateral sclerosis","volume":"13","author":"Eisen","year":"1990","journal-title":"Muscle Nerve"},{"key":"key\n\t\t\t\t20170624055815_awr195-B23","doi-asserted-by":"crossref","first-page":"240","DOI":"10.1007\/s00221-001-0988-2","article-title":"Two phases of intracortical inhibition revealed by transcranial magnetic threshold tracking","volume":"143","author":"Fisher","year":"2002","journal-title":"Exp Brain Res"},{"key":"key\n\t\t\t\t20170624055815_awr195-B24","doi-asserted-by":"crossref","first-page":"498","DOI":"10.1212\/01.wnl.0000341933.97883.a4","article-title":"Transcranial magnetic stimulation in ALS: utility of central motor conduction tests","volume":"72","author":"Floyd","year":"2009","journal-title":"Neurology"},{"key":"key\n\t\t\t\t20170624055815_awr195-B25","doi-asserted-by":"crossref","first-page":"272","DOI":"10.1016\/S1388-2457(02)00340-1","article-title":"Paired transcranial magnetic stimulation for the early diagnosis of corticobasal degeneration","volume":"114","author":"Frasson","year":"2003","journal-title":"Clin Neurophysiol"},{"key":"key\n\t\t\t\t20170624055815_awr195-B26","doi-asserted-by":"crossref","first-page":"180","DOI":"10.1001\/archneurol.2008.558","article-title":"Clinical and Pathological Continuum of Multisystem TDP-43 Proteinopathies","volume":"66","author":"Geser","year":"2009","journal-title":"Arch Neurol"},{"key":"key\n\t\t\t\t20170624055815_awr195-B27","doi-asserted-by":"crossref","first-page":"1227","DOI":"10.1212\/01.wnl.0000320506.79811.da","article-title":"The logopenic\/phonological variant of primary progressive aphasia","volume":"71","author":"Gorno-Tempini","year":"2008","journal-title":"Neurology"},{"key":"key\n\t\t\t\t20170624055815_awr195-B28","doi-asserted-by":"crossref","first-page":"335","DOI":"10.1002\/ana.10825","article-title":"Cognition and anatomy in three variants of primary progressive aphasia","volume":"55","author":"Gorno-Tempini","year":"2004","journal-title":"Ann Neurol"},{"key":"key\n\t\t\t\t20170624055815_awr195-B29","doi-asserted-by":"crossref","first-page":"1006","DOI":"10.1212\/WNL.0b013e31821103e6","article-title":"Classification of primary progressive aphasia and its variants","volume":"76","author":"Gorno-Tempini","year":"2011","journal-title":"Neurology"},{"key":"key\n\t\t\t\t20170624055815_awr195-B30","doi-asserted-by":"crossref","first-page":"594","DOI":"10.1002\/gps.885","article-title":"Predictors of mortality in frontotemporal dementia: a retrospective study of the prognostic influence of pre-diagnostic features","volume":"18","author":"Gr\u00e4sbeck","year":"2003","journal-title":"Int J Geriatr Psychiatry"},{"key":"key\n\t\t\t\t20170624055815_awr195-B31","doi-asserted-by":"crossref","first-page":"17","DOI":"10.1186\/1471-2377-6-17","article-title":"Widespread sensorimotor and frontal cortical atrophy in Amyotrophic Lateral Sclerosis","volume":"6","author":"Grosskreutz","year":"2006","journal-title":"BMC Neurol"},{"key":"key\n\t\t\t\t20170624055815_awr195-B32","doi-asserted-by":"crossref","first-page":"399","DOI":"10.1002\/ana.20203","article-title":"Clinicopathological correlates in frontotemporal dementia","volume":"56","author":"Hodges","year":"2004","journal-title":"Ann Neurol"},{"key":"key\n\t\t\t\t20170624055815_awr195-B33","doi-asserted-by":"crossref","first-page":"349","DOI":"10.1212\/01.WNL.0000078928.20107.52","article-title":"Survival in frontotemporal dementia","volume":"61","author":"Hodges","year":"2003","journal-title":"Neurology"},{"key":"key\n\t\t\t\t20170624055815_awr195-B34","doi-asserted-by":"crossref","first-page":"528","DOI":"10.1212\/01.wnl.0000299186.72374.19","article-title":"Evaluation of corticospinal tracts in ALS with diffusion tensor MRI and brainstem stimulation","volume":"70","author":"Iwata","year":"2008","journal-title":"Neurology"},{"key":"key\n\t\t\t\t20170624055815_awr195-B35","doi-asserted-by":"crossref","first-page":"1385","DOI":"10.1093\/brain\/awl078","article-title":"Clinicopathological and imaging correlates of progressive aphasia and apraxia of speech","volume":"129","author":"Josephs","year":"2006","journal-title":"Brain"},{"key":"key\n\t\t\t\t20170624055815_awr195-B36","doi-asserted-by":"crossref","first-page":"506","DOI":"10.1001\/archneur.63.4.506","article-title":"Clinically undetected motoneuron disease in pathologically proven frontotemporal lobar degeneration with motoneuron disease","volume":"63","author":"Josephs","year":"2006","journal-title":"Arch Neurol"},{"key":"key\n\t\t\t\t20170624055815_awr195-B37","doi-asserted-by":"crossref","first-page":"41","DOI":"10.1212\/01.wnl.0000191307.69661.c3","article-title":"Clinicopathologic analysis of frontotemporal and corticobasal degenerations and PSP","volume":"66","author":"Josephs","year":"2006","journal-title":"Neurology"},{"key":"key\n\t\t\t\t20170624055815_awr195-B38","doi-asserted-by":"crossref","first-page":"138","DOI":"10.1016\/j.jns.2009.08.036","article-title":"Behavior and cognition in corticobasal degeneration and progressive supranuclear palsy","volume":"289","author":"Kertesz","year":"2010","journal-title":"J Neurol Sci"},{"key":"key\n\t\t\t\t20170624055815_awr195-B39","doi-asserted-by":"crossref","first-page":"942","DOI":"10.1016\/S0140-6736(10)61156-7","article-title":"Amyotrophic lateral sclerosis","volume":"377","author":"Kiernan Matthew","year":"2011","journal-title":"Lancet"},{"key":"key\n\t\t\t\t20170624055815_awr195-B40","doi-asserted-by":"crossref","first-page":"1639","DOI":"10.1212\/WNL.38.10.1639","article-title":"Treatment of Guillain-Barr\u00e9 syndrome with high-dose gammaglobulin","volume":"38","author":"Kleyweg","year":"1988","journal-title":"Neurology"},{"key":"key\n\t\t\t\t20170624055815_awr195-B41","doi-asserted-by":"crossref","first-page":"426","DOI":"10.1002\/mus.20949","article-title":"Dissociated small hand muscle atrophy in amyotrophic lateral sclerosis: frequency, extent, and specificity","volume":"37","author":"Kuwabara","year":"2008","journal-title":"Muscle Nerve"},{"key":"key\n\t\t\t\t20170624055815_awr195-B42","doi-asserted-by":"crossref","first-page":"978","DOI":"10.1016\/S1474-4422(10)70184-8","article-title":"Chromosome 9p21 in amyotrophic lateral sclerosis in Finland: a genome-wide association study","volume":"9","author":"Laaksovirta","year":"2010","journal-title":"Lancet Neurol"},{"key":"key\n\t\t\t\t20170624055815_awr195-B43","doi-asserted-by":"crossref","first-page":"1669","DOI":"10.1212\/WNL.0b013e3181a55f1c","article-title":"Chromosome 9p-linked families with frontotemporal dementia associated with motoneuron disease","volume":"72","author":"Le Ber","year":"2009","journal-title":"Neurology"},{"key":"key\n\t\t\t\t20170624055815_awr195-B44","doi-asserted-by":"crossref","first-page":"826","DOI":"10.1001\/archneurol.2010.146","article-title":"Neurobehavioral features in frontotemporal dementia with amyotrophic lateral sclerosis","volume":"67","author":"Lillo","year":"2010","journal-title":"Arch Neurol"},{"key":"key\n\t\t\t\t20170624055815_awr195-B45","doi-asserted-by":"crossref","first-page":"488","DOI":"10.1007\/s00415-008-0565-8","article-title":"Clinicopathological and genetic correlates of frontotemporal lobar degeneration and corticobasal degeneration","volume":"255","author":"Llad\u00f3","year":"2008","journal-title":"J Neurol"},{"key":"key\n\t\t\t\t20170624055815_awr195-B46","doi-asserted-by":"crossref","first-page":"1077","DOI":"10.1212\/WNL.59.7.1077","article-title":"The overlap of amyotrophic lateral sclerosis and frontotemporal dementia","volume":"59","author":"Lomen-Hoerth","year":"2002","journal-title":"Neurology"},{"key":"key\n\t\t\t\t20170624055815_awr195-B47","doi-asserted-by":"crossref","first-page":"1094","DOI":"10.1212\/01.WNL.0000055861.95202.8D","article-title":"Are amyotrophic lateral sclerosis patients cognitively normal?","volume":"60","author":"Lomen-Hoerth","year":"2003","journal-title":"Neurology"},{"key":"key\n\t\t\t\t20170624055815_awr195-B48","doi-asserted-by":"crossref","first-page":"995","DOI":"10.1016\/S1474-4422(10)70195-2","article-title":"TDP-43 and FUS in amyotrophic lateral sclerosis and frontotemporal dementia","volume":"9","author":"Mackenzie","year":"2010","journal-title":"Lancet Neurol"},{"key":"key\n\t\t\t\t20170624055815_awr195-B49","doi-asserted-by":"crossref","first-page":"672","DOI":"10.1111\/j.1440-1789.2009.01029.x","article-title":"TDP-43 is consistently co-localized with ubiquitinated inclusions in sporadic and Guam amyotrophic lateral sclerosis but not in familial amyotrophic lateral sclerosis with and without SOD1 mutations","volume":"29","author":"Maekawa","year":"2009","journal-title":"Neuropathology"},{"key":"key\n\t\t\t\t20170624055815_awr195-B50","first-page":"255","article-title":"Whole-brain and regional brain atrophy in amyotrophic lateral sclerosis","volume":"28","author":"Mezzapesa","year":"2007","journal-title":"Am J Neuroradiol"},{"key":"key\n\t\t\t\t20170624055815_awr195-B51","doi-asserted-by":"crossref","first-page":"82","DOI":"10.1016\/S0022-510X(98)00148-8","article-title":"Peripheral and central motor conduction in amyotrophic lateral sclerosis","volume":"159","author":"Mills","year":"1998","journal-title":"J Neurol Sci"},{"key":"key\n\t\t\t\t20170624055815_awr195-B52","doi-asserted-by":"crossref","first-page":"1078","DOI":"10.1002\/gps.1610","article-title":"The Addenbrooke's Cognitive Examination Revised (ACE-R): a brief cognitive test battery for dementia screening","volume":"21","author":"Mioshi","year":"2006","journal-title":"Int J Geriatr Psychiatry"},{"key":"key\n\t\t\t\t20170624055815_awr195-B53","doi-asserted-by":"crossref","first-page":"1591","DOI":"10.1212\/WNL.0b013e3181e04070","article-title":"Clinical staging and disease progression in frontotemporal dementia","volume":"74","author":"Mioshi","year":"2010","journal-title":"Neurology"},{"key":"key\n\t\t\t\t20170624055815_awr195-B54","doi-asserted-by":"crossref","first-page":"975","DOI":"10.1016\/S1388-2457(99)00030-9","article-title":"Motoneuron disease: usefulness of transcranial magnetic stimulation in improving the diagnosis","volume":"110","author":"Miscio","year":"1999","journal-title":"Clin Neurophysiol"},{"key":"key\n\t\t\t\t20170624055815_awr195-B55","doi-asserted-by":"crossref","first-page":"592","DOI":"10.1001\/archneur.1979.00500450086021","article-title":"Presenile dementia with motoneuron disease in Japan. A new entity?","volume":"36","author":"Mitsuyama","year":"1979","journal-title":"Arch Neurol"},{"key":"key\n\t\t\t\t20170624055815_awr195-B56","doi-asserted-by":"crossref","first-page":"1546","DOI":"10.1212\/WNL.51.6.1546","article-title":"Frontotemporal lobar degeneration: A consensus on clinical diagnostic criteria","volume":"51","author":"Neary","year":"1998","journal-title":"Neurology"},{"key":"key\n\t\t\t\t20170624055815_awr195-B57","doi-asserted-by":"crossref","first-page":"23","DOI":"10.1136\/jnnp.53.1.23","article-title":"Frontal lobe dementia and motoneuron disease","volume":"53","author":"Neary","year":"1990","journal-title":"J Neurol Neurosurg Psychiatry"},{"key":"key\n\t\t\t\t20170624055815_awr195-B58","doi-asserted-by":"crossref","first-page":"2406","DOI":"10.1093\/brain\/awg240","article-title":"Progressive non-fluent aphasia is associated with hypometabolism centred on the left anterior insula","volume":"126","author":"Nestor","year":"2003","journal-title":"Brain"},{"key":"key\n\t\t\t\t20170624055815_awr195-B59","doi-asserted-by":"crossref","first-page":"2922","DOI":"10.1093\/brain\/awp214","article-title":"A new subtype of frontotemporal lobar degeneration with FUS pathology","volume":"132","author":"Neumann","year":"2009","journal-title":"Brain"},{"key":"key\n\t\t\t\t20170624055815_awr195-B60","doi-asserted-by":"crossref","first-page":"130","DOI":"10.1126\/science.1134108","article-title":"Ubiquitinated TDP-43 in frontotemporal lobar degeneration and amyotrophic lateral sclerosis","volume":"314","author":"Neumann","year":"2006","journal-title":"Science"},{"key":"key\n\t\t\t\t20170624055815_awr195-B61","doi-asserted-by":"crossref","first-page":"2410","DOI":"10.1016\/j.clinph.2004.04.022","article-title":"Different TMS patterns of intracortical inhibition in early onset Alzheimer dementia and frontotemporal dementia","volume":"115","author":"Pierantozzi","year":"2004","journal-title":"Clin Neurophysiol"},{"key":"key\n\t\t\t\t20170624055815_awr195-B62","doi-asserted-by":"crossref","first-page":"174","DOI":"10.1002\/mus.880110214","article-title":"Central motor conduction times using transcranial stimulation and F Wave latencies","volume":"11","author":"Robinson","year":"1988","journal-title":"Muscle Nerve"},{"key":"key\n\t\t\t\t20170624055815_awr195-B63","doi-asserted-by":"crossref","first-page":"1562","DOI":"10.1212\/WNL.0b013e3181a4124e","article-title":"Patterns of cortical thinning in the language variants of frontotemporal lobar degeneration","volume":"72","author":"Rohrer","year":"2009","journal-title":"Neurology"},{"key":"key\n\t\t\t\t20170624055815_awr195-B64","doi-asserted-by":"crossref","first-page":"476","DOI":"10.1136\/jnnp.2010.212225","article-title":"Clinical, genetic and pathological heterogeneity of frontotemporal dementia: a review","volume":"82","author":"Seelaar","year":"2011","journal-title":"J Neurol Neurosurg Psychiatry"},{"key":"key\n\t\t\t\t20170624055815_awr195-B65","doi-asserted-by":"crossref","first-page":"31","DOI":"10.1007\/s00401-007-0236-3","article-title":"Frontotemporal lobar degeneration: clinical and pathological relationships","volume":"114","author":"Snowden","year":"2007","journal-title":"Acta neuropathol"},{"key":"key\n\t\t\t\t20170624055815_awr195-B66","doi-asserted-by":"crossref","first-page":"1668","DOI":"10.1126\/science.1154584","article-title":"TDP-43 Mutations in Familial and Sporadic Amyotrophic Lateral Sclerosis","volume":"319","author":"Sreedharan","year":"2008","journal-title":"Science"},{"key":"key\n\t\t\t\t20170624055815_awr195-B67","doi-asserted-by":"crossref","first-page":"366","DOI":"10.1212\/WNL.0b013e3181ccc732","article-title":"Genetic contribution of FUS to frontotemporal lobar degeneration","volume":"74","author":"Van Langenhove","year":"2010","journal-title":"Neurology"},{"key":"key\n\t\t\t\t20170624055815_awr195-B68","doi-asserted-by":"crossref","first-page":"2436","DOI":"10.1093\/brain\/awl172","article-title":"Novel threshold tracking techniques suggest that cortical hyperexcitability is an early feature of motoneuron disease","volume":"129","author":"Vucic","year":"2006","journal-title":"Brain"},{"key":"key\n\t\t\t\t20170624055815_awr195-B69","doi-asserted-by":"crossref","first-page":"1540","DOI":"10.1093\/brain\/awn071","article-title":"Cortical hyperexcitability may precede the onset of familial amyotrophic lateral sclerosis","volume":"131","author":"Vucic","year":"2008","journal-title":"Brain"},{"key":"key\n\t\t\t\t20170624055815_awr195-B70","doi-asserted-by":"crossref","first-page":"141","DOI":"10.1093\/brain\/120.1.141","article-title":"Localization of the motor hand area to a knob on the precentral gyrus. A new landmark","volume":"120","author":"Yousry","year":"1997","journal-title":"Brain"}],"container-title":["Brain"],"original-title":[],"language":"en","link":[{"URL":"http:\/\/academic.oup.com\/brain\/article-pdf\/134\/9\/2582\/17869835\/awr195.pdf","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2024,4,9]],"date-time":"2024-04-09T22:22:50Z","timestamp":1712701370000},"score":1,"resource":{"primary":{"URL":"https:\/\/academic.oup.com\/brain\/article-lookup\/doi\/10.1093\/brain\/awr195"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2011,8,11]]},"references-count":70,"journal-issue":{"issue":"9","published-online":{"date-parts":[[2011,8,11]]},"published-print":{"date-parts":[[2011,9]]}},"URL":"https:\/\/doi.org\/10.1093\/brain\/awr195","relation":{},"ISSN":["1460-2156","0006-8950"],"issn-type":[{"value":"1460-2156","type":"electronic"},{"value":"0006-8950","type":"print"}],"subject":[],"published":{"date-parts":[[2011,8,11]]}}}