{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,2,21]],"date-time":"2025-02-21T08:27:35Z","timestamp":1740126455381,"version":"3.37.3"},"reference-count":6,"publisher":"Oxford University Press (OUP)","issue":"8","license":[{"start":{"date-parts":[[2024,3,12]],"date-time":"2024-03-12T00:00:00Z","timestamp":1710201600000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/academic.oup.com\/pages\/standard-publication-reuse-rights"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2024,7,19]]},"abstract":"<jats:p>A 28-year-old woman presented with generalized hardening of the skin, joint immobility, shortness of breath and lower back pain since the age of 7\u2005years.<\/jats:p>","DOI":"10.1093\/ced\/llae084","type":"journal-article","created":{"date-parts":[[2024,3,12]],"date-time":"2024-03-12T04:53:12Z","timestamp":1710219192000},"page":"944-946","source":"Crossref","is-referenced-by-count":0,"title":["Childhood-onset progressive skin fibrosis and joint immobility"],"prefix":"10.1093","volume":"49","author":[{"ORCID":"https:\/\/orcid.org\/0000-0003-1538-3406","authenticated-orcid":false,"given":"Ecem","family":"Baklan","sequence":"first","affiliation":[{"name":"Department of Dermatology and Venereal Diseases, Ege University, Faculty of Medicine, \u0130zmir, T\u00fcrkiye"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-6295-211X","authenticated-orcid":false,"given":"Nilay","family":"Duman","sequence":"additional","affiliation":[{"name":"Department of Dermatology and Venereal Diseases, Ege University, Faculty of Medicine, \u0130zmir, T\u00fcrkiye"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Banu","family":"Yaman","sequence":"additional","affiliation":[{"name":"Department of Pathology, Ege University, Faculty of Medicine , \u0130zmir , T\u00fcrkiye"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Can","family":"Ceylan","sequence":"additional","affiliation":[{"name":"Department of Dermatology and Venereal Diseases, Ege University, Faculty of Medicine, \u0130zmir, T\u00fcrkiye"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"286","published-online":{"date-parts":[[2024,3,12]]},"reference":[{"key":"2024071909321225100_llae084-B1","doi-asserted-by":"crossref","first-page":"163","DOI":"10.1016\/j.jaad.2016.01.038","article-title":"Segmental stiff skin syndrome (SSS): a distinct clinical entity","volume":"75","author":"Myers","year":"2016","journal-title":"J Am Acad Dermatol"},{"key":"2024071909321225100_llae084-B2","doi-asserted-by":"crossref","first-page":"23ra20","DOI":"10.1126\/scitranslmed.3000488","article-title":"Mutations in fibrillin-1 cause congenital scleroderma: stiff skin syndrome","volume":"2","author":"Loeys","year":"2010","journal-title":"Sci Transl Med"},{"key":"2024071909321225100_llae084-B3","doi-asserted-by":"crossref","first-page":"e237","DOI":"10.1016\/j.jaad.2016.05.047","article-title":"Segmental stiff skin syndrome (SSS): two additional cases with a positive response to mycophenolate mofetil and physical therapy","volume":"75","author":"Kurtzman","year":"2016","journal-title":"J Am Acad Dermatol"},{"key":"2024071909321225100_llae084-B4","doi-asserted-by":"crossref","first-page":"1351","DOI":"10.1001\/archderm.144.10.1351","article-title":"The stiff skin syndrome: case series, differential diagnosis of the stiff skin phenotype, and review of the literature","volume":"144","author":"Liu","year":"2008","journal-title":"Arch Dermatol"},{"key":"2024071909321225100_llae084-B5","doi-asserted-by":"crossref","first-page":"e15633","DOI":"10.1111\/dth.15633","article-title":"Classification and rising medication therapy in stiff skin syndrome: a case report and literature review","volume":"35","author":"Lin","year":"2022","journal-title":"Dermatol Ther"},{"key":"2024071909321225100_llae084-B6","doi-asserted-by":"crossref","first-page":"207","DOI":"10.1007\/s100670050158","article-title":"Skin score decrease in systemic sclerosis patients treated with intravenous immunoglobulin \u2013 a preliminary report","volume":"19","author":"Levy","year":"2000","journal-title":"Clin Rheumatol"}],"container-title":["Clinical and Experimental Dermatology"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/academic.oup.com\/ced\/advance-article-pdf\/doi\/10.1093\/ced\/llae084\/57764714\/llae084.pdf","content-type":"application\/pdf","content-version":"am","intended-application":"syndication"},{"URL":"https:\/\/academic.oup.com\/ced\/article-pdf\/49\/8\/944\/58594001\/llae084.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"syndication"},{"URL":"https:\/\/academic.oup.com\/ced\/article-pdf\/49\/8\/944\/58594001\/llae084.pdf","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2024,7,19]],"date-time":"2024-07-19T09:32:18Z","timestamp":1721381538000},"score":1,"resource":{"primary":{"URL":"https:\/\/academic.oup.com\/ced\/article\/49\/8\/944\/7625616"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2024,3,12]]},"references-count":6,"journal-issue":{"issue":"8","published-online":{"date-parts":[[2024,3,12]]},"published-print":{"date-parts":[[2024,7,19]]}},"URL":"https:\/\/doi.org\/10.1093\/ced\/llae084","relation":{},"ISSN":["0307-6938","1365-2230"],"issn-type":[{"type":"print","value":"0307-6938"},{"type":"electronic","value":"1365-2230"}],"subject":[],"published-other":{"date-parts":[[2024,8]]},"published":{"date-parts":[[2024,3,12]]}}}