{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,9,8]],"date-time":"2025-09-08T05:36:59Z","timestamp":1757309819545},"reference-count":7,"publisher":"Oxford University Press (OUP)","issue":"4","license":[{"start":{"date-parts":[[2020,6,29]],"date-time":"2020-06-29T00:00:00Z","timestamp":1593388800000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/creativecommons.org\/licenses\/by-nc\/4.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2020,8,1]]},"abstract":"<jats:title>Abstract<\/jats:title>\n               <jats:sec>\n                  <jats:title>Background<\/jats:title>\n                  <jats:p>Ebstein\u2019s anomaly (EA) is mainly thought of as a right heart condition, however, congenital left-sided lesions can co-exist. Therefore, it is paramount to include the left side of the heart as part of a routine investigation in these patients. We present a 57-year-old symptomatic patient with EA and progressive tricuspid regurgitation (TR) associated with acquired left ventricular outflow obstruction (LVOTO).<\/jats:p>\n               <\/jats:sec>\n               <jats:sec>\n                  <jats:title>Case summary<\/jats:title>\n                  <jats:p>A 57-year-old women, known to have severe EA presented with shortness of breath and chest pain on exertion secondary to progression of the tricuspid valve regurgitation and right ventricle dilatation leading to a dynamic compression of the left outflow tract requiring surgical intervention.<\/jats:p>\n               <\/jats:sec>\n               <jats:sec>\n                  <jats:title>Discussion<\/jats:title>\n                  <jats:p>Left ventricular obstruction secondary to severe TR and dilation of the right ventricle can present and remain silent at rest but becoming significant on exertion. Therefore, we recommend that all patients with EA and significant TR undergo exercise echocardiography at regular intervals to specifically look for acquired dynamic LVOTO.<\/jats:p>\n               <\/jats:sec>","DOI":"10.1093\/ehjcr\/ytaa077","type":"journal-article","created":{"date-parts":[[2020,6,29]],"date-time":"2020-06-29T01:15:00Z","timestamp":1593393300000},"page":"1-5","source":"Crossref","is-referenced-by-count":2,"title":["Left heart matters in Ebstein\u2019s anomaly: the importance of a closer follow up\u2014a case report"],"prefix":"10.1093","volume":"4","author":[{"given":"Maria Victoria","family":"Ordo\u00f1ez","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Radwa","family":"Bedair","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Stephanie L","family":"Curtis","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"286","published-online":{"date-parts":[[2020,6,29]]},"reference":[{"key":"2020101507150967900_ytaa077-B1","doi-asserted-by":"crossref","first-page":"1067","DOI":"10.4103\/0366-6999.230731","article-title":"Outcomes of Ebstein\u2019s anomaly patients treated with tricuspid valvuloplasty or tricuspid valve replacement: experience of a single center","volume":"131","author":"Li","year":"2018","journal-title":"Chin Med J (Engl)"},{"key":"2020101507150967900_ytaa077-B2","volume-title":"Diagnosis and Management of Adult Congenital Heart Disease","author":"Gatzoulis","edition":"3rd ed"},{"key":"2020101507150967900_ytaa077-B3","doi-asserted-by":"crossref","first-page":"1120","DOI":"10.1016\/j.jtcvs.2008.02.034","article-title":"The outcomes of operations for 539 patients with Ebstein anomaly","volume":"135","author":"Brown","year":"2008","journal-title":"J Thorac Cardiovasc Surg"},{"key":"2020101507150967900_ytaa077-B4"},{"key":"2020101507150967900_ytaa077-B5","doi-asserted-by":"crossref","first-page":"286","DOI":"10.1016\/S0167-5273(96)02825-2","article-title":"Subaortic stenosis due to accessory tissue of the mitral valve associated with Ebstein\u2019s anomaly in an adult","volume":"57","author":"Isobe","year":"1996","journal-title":"Int J Cardiol"},{"key":"2020101507150967900_ytaa077-B6","doi-asserted-by":"crossref","first-page":"282","DOI":"10.1016\/j.ijcard.2015.06.084","article-title":"An unusual cause of dynamic left ventricular outflow obstruction: An unusual case of dynamic LVOTO","volume":"197","author":"Waterhouse","year":"2015","journal-title":"Int J Cardiol"},{"key":"2020101507150967900_ytaa077-B7","doi-asserted-by":"crossref","first-page":"e33","DOI":"10.1161\/CIRCULATIONAHA.115.016208","article-title":"Case of Ebstein anomaly complicated by left ventricular outflow tract obstruction secondary to deformed basal septum attributable to atrialized right ventricle","volume":"133","author":"Hirata","year":"2016","journal-title":"Circulation"}],"container-title":["European Heart Journal - Case Reports"],"original-title":[],"language":"en","link":[{"URL":"http:\/\/academic.oup.com\/ehjcr\/article-pdf\/4\/4\/1\/33889392\/ytaa077.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"syndication"},{"URL":"http:\/\/academic.oup.com\/ehjcr\/article-pdf\/4\/4\/1\/33889392\/ytaa077.pdf","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2020,10,15]],"date-time":"2020-10-15T11:24:52Z","timestamp":1602761092000},"score":1,"resource":{"primary":{"URL":"https:\/\/academic.oup.com\/ehjcr\/article\/4\/4\/1\/5864531"}},"subtitle":[],"editor":[{"given":"Pankaj","family":"Garg","sequence":"additional","affiliation":[],"role":[{"role":"editor","vocabulary":"crossref"}]},{"given":"Rami Riziq Yousef","family":"Abumuaileq","sequence":"additional","affiliation":[],"role":[{"role":"editor","vocabulary":"crossref"}]},{"given":"Marwan","family":"Refaat","sequence":"additional","affiliation":[],"role":[{"role":"editor","vocabulary":"crossref"}]},{"given":"Kate","family":"von Klemperer","sequence":"additional","affiliation":[],"role":[{"role":"editor","vocabulary":"crossref"}]},{"given":"Rahul","family":"Mukherjee","sequence":"additional","affiliation":[],"role":[{"role":"editor","vocabulary":"crossref"}]},{"given":"Peregrine","family":"Green","sequence":"additional","affiliation":[],"role":[{"role":"editor","vocabulary":"crossref"}]}],"short-title":[],"issued":{"date-parts":[[2020,6,29]]},"references-count":7,"journal-issue":{"issue":"4","published-online":{"date-parts":[[2020,6,29]]},"published-print":{"date-parts":[[2020,8,1]]}},"URL":"https:\/\/doi.org\/10.1093\/ehjcr\/ytaa077","relation":{},"ISSN":["2514-2119"],"issn-type":[{"value":"2514-2119","type":"electronic"}],"subject":[],"published-other":{"date-parts":[[2020,8]]},"published":{"date-parts":[[2020,6,29]]}}}