{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,7,30]],"date-time":"2025-07-30T11:50:00Z","timestamp":1753876200818,"version":"3.41.2"},"reference-count":16,"publisher":"Oxford University Press (OUP)","issue":"1","license":[{"start":{"date-parts":[[2023,1,7]],"date-time":"2023-01-07T00:00:00Z","timestamp":1673049600000},"content-version":"vor","delay-in-days":11,"URL":"https:\/\/creativecommons.org\/licenses\/by-nc\/4.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2022,12,27]]},"abstract":"<jats:title>Abstract<\/jats:title>\n               <jats:sec>\n                  <jats:title>Background<\/jats:title>\n                  <jats:p>Risk stratification for sudden cardiac death (SCD) is a key factor in the management of patients with hypertrophic cardiomyopathy (HCM). Cardiac magnetic resonance (CMR) has a unique role in the evaluation of HCM and offers superior diagnostic and prognostic information to assess the indication for a prophylactic implantable cardioverter-defibrillator (ICD).<\/jats:p>\n               <\/jats:sec>\n               <jats:sec>\n                  <jats:title>Case summary<\/jats:title>\n                  <jats:p>A 39-year-old patient with non-obstructive HCM with a low ESC HCM Risk-SCD score underwent a CMR revealing a left ventricular apical aneurysm and extensive late gadolinium enhancement; a prophylactic ICD was thus implanted. A month later, the patient was admitted in refractory electrical storm with over 50 appropriate ICD shocks due to sustained ventricular tachycardia. Despite anti-arrhythmic therapy and mechanical ventilation, the evolution was unfavourable with haemodynamic instability; veno-arterial extracorporeal membrane oxygenation was implanted. The patient was submitted to CMR-guided epicardial VT catheter ablation with complications of LV thrombus and severe pericardial effusion.<\/jats:p>\n               <\/jats:sec>\n               <jats:sec>\n                  <jats:title>Discussion<\/jats:title>\n                  <jats:p>This case details the complex risk stratification for SCD in patients with HCM, highlighting the important role of CMR in the integrated approach to risk stratification.<\/jats:p>\n               <\/jats:sec>","DOI":"10.1093\/ehjcr\/ytad010","type":"journal-article","created":{"date-parts":[[2023,1,8]],"date-time":"2023-01-08T08:50:01Z","timestamp":1673167801000},"source":"Crossref","is-referenced-by-count":1,"title":["Electrical storm in hypertrophic cardiomyopathy: Cardiac magnetic resonance and sudden cardiac death risk stratification: a case report"],"prefix":"10.1093","volume":"7","author":[{"ORCID":"https:\/\/orcid.org\/0000-0002-9970-7828","authenticated-orcid":false,"given":"Pedro","family":"Garcia Br\u00e1s","sequence":"first","affiliation":[{"name":"Department of Cardiology, Hospital de Santa Marta, Centro Hospitalar Universit\u00e1rio de Lisboa Central , Lisbon , Portugal"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-8812-2330","authenticated-orcid":false,"given":"S\u00edlvia Aguiar","family":"Rosa","sequence":"additional","affiliation":[{"name":"Department of Cardiology, Hospital de Santa Marta, Centro Hospitalar Universit\u00e1rio de Lisboa Central , Lisbon , Portugal"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Guilherme","family":"Portugal","sequence":"additional","affiliation":[{"name":"Department of Cardiology, Hospital de Santa Marta, Centro Hospitalar Universit\u00e1rio de Lisboa Central , Lisbon , Portugal"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"M\u00e1rio Martins","family":"Oliveira","sequence":"additional","affiliation":[{"name":"Department of Cardiology, Hospital de Santa Marta, Centro Hospitalar Universit\u00e1rio de Lisboa Central , Lisbon , Portugal"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"286","published-online":{"date-parts":[[2023,1,7]]},"reference":[{"key":"2023012017112382600_ytad010-B1","first-page":"7","article-title":"2014 ESC guidelines on diagnosis and management of hypertrophic cardiomyopathy","volume":"121","author":"Elliott","year":"2015","journal-title":"Eur Heart J"},{"key":"2023012017112382600_ytad010-B2","doi-asserted-by":"crossref","first-page":"484","DOI":"10.1161\/CIRCULATIONAHA.113.007094","article-title":"Prognostic value of quantitative contrast-enhanced cardiovascular magnetic resonance for the evaluation of sudden death risk in patients with hypertrophic 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