{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,7,30]],"date-time":"2025-07-30T11:51:15Z","timestamp":1753876275000,"version":"3.41.2"},"reference-count":8,"publisher":"Oxford University Press (OUP)","issue":"7","license":[{"start":{"date-parts":[[2024,7,10]],"date-time":"2024-07-10T00:00:00Z","timestamp":1720569600000},"content-version":"vor","delay-in-days":9,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2024,7,2]]},"abstract":"<jats:title>Abstract<\/jats:title>\n               <jats:sec>\n                  <jats:title>Background<\/jats:title>\n                  <jats:p>Lutembacher\u2019s syndrome refers to the rare combination of atrial septal defect and mitral stenosis. This condition is still underdiagnosed despite its distinct clinical, paraclinical, and therapeutic implications.<\/jats:p>\n               <\/jats:sec>\n               <jats:sec>\n                  <jats:title>Case summary<\/jats:title>\n                  <jats:p>We report the case of a 60-year-old woman presenting with acute congestive heart failure. Investigations revealed the combination of low-gradient severe rheumatic mitral stenosis and ostium secundum atrial septal defect. Despite the medical team\u2019s conservative management of her condition and recommendation for surgical intervention, the patient chose to discharge herself against medical advice. She died 6 months later.<\/jats:p>\n               <\/jats:sec>\n               <jats:sec>\n                  <jats:title>Conclusion<\/jats:title>\n                  <jats:p>Lutembacher\u2019s syndrome continues to be a rare condition in our practice. Once low-gradient severe mitral stenosis is diagnosed, it is essential to search for an associated atrial septal defect, especially when there is an early onset of significant right ventricular enlargement or dysfunction or when an intriguing inconsistency exists between the mitral area and the transmitral gradient.<\/jats:p>\n               <\/jats:sec>","DOI":"10.1093\/ehjcr\/ytae327","type":"journal-article","created":{"date-parts":[[2024,7,10]],"date-time":"2024-07-10T11:41:58Z","timestamp":1720611718000},"source":"Crossref","is-referenced-by-count":1,"title":["A rare case of Lutembacher\u2019s syndrome presenting with low-gradient severe mitral stenosis: case report and literature overview"],"prefix":"10.1093","volume":"8","author":[{"ORCID":"https:\/\/orcid.org\/0009-0007-7895-062X","authenticated-orcid":false,"given":"Samah","family":"El-Mhadi","sequence":"first","affiliation":[{"name":"Department of Cardiology B, Ibn Sina University Hospital Center , Rabat , Morocco"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Belghait","family":"El Hajjaj","sequence":"additional","affiliation":[{"name":"Department of Cardiology B, Ibn Sina University Hospital Center , Rabat , Morocco"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Nabil","family":"Laktib","sequence":"additional","affiliation":[{"name":"Department of Cardiology B, Ibn Sina University Hospital Center , Rabat , Morocco"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Latifa","family":"Oukerraj","sequence":"additional","affiliation":[{"name":"Department of Cardiology B, Ibn Sina University Hospital Center , Rabat , Morocco"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Mohamed","family":"Cherti","sequence":"additional","affiliation":[{"name":"Department of Cardiology B, Ibn Sina University Hospital Center , Rabat , Morocco"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"286","published-online":{"date-parts":[[2024,7,10]]},"reference":[{"volume-title":"Statpearls","year":"2023","author":"Mahajan","key":"2024073119543439300_ytae327-B1"},{"key":"2024073119543439300_ytae327-B2","first-page":"122","article-title":"Current diagnostic and treatment strategies for Lutembacher syndrome: the pivotal role of echocardiography","volume":"5","author":"Aminde","year":"2015","journal-title":"Cardiovasc Diagn Ther"},{"key":"2024073119543439300_ytae327-B3","doi-asserted-by":"crossref","first-page":"179","DOI":"10.4103\/0975-3583.95381","article-title":"Lutembacher's syndrome","volume":"3","author":"Kulkarni","year":"2012","journal-title":"J Cardiovasc Dis Res"},{"key":"2024073119543439300_ytae327-B4","doi-asserted-by":"crossref","first-page":"20","DOI":"10.1016\/j.ihj.2016.07.003","article-title":"Lutembacher's syndrome: is the mitral pathology always rheumatic?","volume":"69","author":"Vaideeswar","year":"2017","journal-title":"Indian Heart J"},{"key":"2024073119543439300_ytae327-B5","doi-asserted-by":"crossref","first-page":"e6939","DOI":"10.1002\/ccr3.6939","article-title":"Lutembacher syndrome in a middle-aged woman in Ghana with an extremely large atrial septal defect","volume":"11","author":"Adu-Boakye","year":"2023","journal-title":"Clin Case Rep"},{"key":"2024073119543439300_ytae327-B6","first-page":"9402987","article-title":"An incidental diagnosis of rheumatic mitral stenosis and secundum atrial septal defect (Lutembacher's syndrome) in a young woman","volume":"2019","author":"Alam","year":"2019","journal-title":"Case Rep Cardiol"},{"key":"2024073119543439300_ytae327-B7","doi-asserted-by":"crossref","first-page":"e247984","DOI":"10.1136\/bcr-2021-247984","article-title":"Non-surgical treatment of Lutembacher syndrome: combined percutaneous transcatheter therapy","volume":"15","author":"Johny","year":"2022","journal-title":"BMJ Case Rep"},{"key":"2024073119543439300_ytae327-B8","first-page":"469","article-title":"Surgical indications and treatment of mitral valve disease associated with secundum atrial septal defect with special reference to left ventricular geometry and function","volume":"35","author":"Shigenobu","year":"1994","journal-title":"J Cardiovasc Surg (Torino)"}],"container-title":["European Heart Journal - Case Reports"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/academic.oup.com\/ehjcr\/advance-article-pdf\/doi\/10.1093\/ehjcr\/ytae327\/58496345\/ytae327.pdf","content-type":"application\/pdf","content-version":"am","intended-application":"syndication"},{"URL":"https:\/\/academic.oup.com\/ehjcr\/article-pdf\/8\/7\/ytae327\/58625954\/ytae327.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"syndication"},{"URL":"https:\/\/academic.oup.com\/ehjcr\/article-pdf\/8\/7\/ytae327\/58625954\/ytae327.pdf","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2024,8,1]],"date-time":"2024-08-01T02:55:44Z","timestamp":1722480944000},"score":1,"resource":{"primary":{"URL":"https:\/\/academic.oup.com\/ehjcr\/article\/doi\/10.1093\/ehjcr\/ytae327\/7710405"}},"subtitle":[],"editor":[{"given":"Filippo","family":"Puricelli","sequence":"additional","affiliation":[],"role":[{"role":"editor","vocabulary":"crossref"}]},{"given":"Domenico","family":"Filomena","sequence":"additional","affiliation":[],"role":[{"role":"editor","vocabulary":"crossref"}]},{"given":"Annagrazia","family":"Cecere","sequence":"additional","affiliation":[],"role":[{"role":"editor","vocabulary":"crossref"}]},{"given":"Arvind","family":"Singh","sequence":"additional","affiliation":[],"role":[{"role":"editor","vocabulary":"crossref"}]},{"given":"Ivan","family":"Wong","sequence":"additional","affiliation":[],"role":[{"role":"editor","vocabulary":"crossref"}]},{"given":"Ralph Mark Louis","family":"Neijenhuis","sequence":"additional","affiliation":[],"role":[{"role":"editor","vocabulary":"crossref"}]}],"short-title":[],"issued":{"date-parts":[[2024,7]]},"references-count":8,"journal-issue":{"issue":"7","published-print":{"date-parts":[[2024,7,2]]}},"URL":"https:\/\/doi.org\/10.1093\/ehjcr\/ytae327","relation":{},"ISSN":["2514-2119"],"issn-type":[{"type":"electronic","value":"2514-2119"}],"subject":[],"published-other":{"date-parts":[[2024,7]]},"published":{"date-parts":[[2024,7]]},"article-number":"ytae327"}}