{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,7,30]],"date-time":"2025-07-30T11:51:06Z","timestamp":1753876266974,"version":"3.41.2"},"reference-count":12,"publisher":"Oxford University Press (OUP)","issue":"8","license":[{"start":{"date-parts":[[2024,8,16]],"date-time":"2024-08-16T00:00:00Z","timestamp":1723766400000},"content-version":"vor","delay-in-days":15,"URL":"https:\/\/creativecommons.org\/licenses\/by-nc\/4.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2024,8,2]]},"abstract":"<jats:title>Abstract<\/jats:title>\n               <jats:sec>\n                  <jats:title>Background<\/jats:title>\n                  <jats:p>Arrhythmic mitral valve prolapse syndrome (ARMV) is a recognized but underdiagnosed disease pattern. Risk factors for ARMV are established but not very well known, and the association of the structural abnormality with ventricular arrhythmias is incompletely understood.<\/jats:p>\n               <\/jats:sec>\n               <jats:sec>\n                  <jats:title>Case summary<\/jats:title>\n                  <jats:p>Here, we present the case of a young man who presented at our hospital for radiofrequency catheter ablation and mitral valve surgery after two episodes of survived sudden cardiac arrest. We discuss the diagnostic and therapeutic strategies that were used. We shine light on the risk factors for ARMV and why early identification is crucial. We address the topic of primary prevention and its limitations. Finally, we discuss different treatment modalities for patients with ARMV.<\/jats:p>\n               <\/jats:sec>\n               <jats:sec>\n                  <jats:title>Discussion<\/jats:title>\n                  <jats:p>More awareness for ARMV is crucial. A consensus statement on clinical management exists, but scientific gaps in prospective data for primary prevention need to be filled and there is a need for a better understanding of the pathogenesis of ARMV.<\/jats:p>\n               <\/jats:sec>","DOI":"10.1093\/ehjcr\/ytae372","type":"journal-article","created":{"date-parts":[[2024,8,16]],"date-time":"2024-08-16T14:36:04Z","timestamp":1723818964000},"source":"Crossref","is-referenced-by-count":0,"title":["Case report: arrhythmic mitral valve prolapse syndrome\u2014are risk factors underdiagnosed?"],"prefix":"10.1093","volume":"8","author":[{"ORCID":"https:\/\/orcid.org\/0000-0003-1503-9613","authenticated-orcid":false,"given":"Martina","family":"Steinmaurer","sequence":"first","affiliation":[{"name":"Klinikum der Universit\u00e4t M\u00fcnchen, Standort Gro\u00dfhadern , Marchioninistra\u00dfe 15, 81377 Munich , Germany"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Jakob","family":"Sandmeyer","sequence":"additional","affiliation":[{"name":"Klinikum der Universit\u00e4t M\u00fcnchen, Standort Gro\u00dfhadern , Marchioninistra\u00dfe 15, 81377 Munich , Germany"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Moritz F","family":"Sinner","sequence":"additional","affiliation":[{"name":"Klinikum der Universit\u00e4t M\u00fcnchen, Standort Gro\u00dfhadern , Marchioninistra\u00dfe 15, 81377 Munich , Germany"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Kun","family":"Lu","sequence":"additional","affiliation":[{"name":"Klinikum der Universit\u00e4t M\u00fcnchen, Standort Gro\u00dfhadern , Marchioninistra\u00dfe 15, 81377 Munich , Germany"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Christian","family":"Hagl","sequence":"additional","affiliation":[{"name":"Klinikum der Universit\u00e4t M\u00fcnchen, Standort Gro\u00dfhadern , Marchioninistra\u00dfe 15, 81377 Munich , Germany"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"286","published-online":{"date-parts":[[2024,8,16]]},"reference":[{"key":"2024081614460040000_ytae372-B1","doi-asserted-by":"crossref","first-page":"1014","DOI":"10.1016\/j.echo.2005.06.013","article-title":"Mitral annular disjunction in advanced myxomatous mitral valve disease: echocardiographic detection and surgical correction","volume":"18","author":"Eriksson","year":"2005","journal-title":"J Am Soc Echocardiogr"},{"key":"2024081614460040000_ytae372-B2","doi-asserted-by":"crossref","first-page":"176","DOI":"10.1007\/s12574-017-0349-1","article-title":"The analysis of mitral annular disjunction detected by echocardiography and comparison with previously reported pathological data","volume":"15","author":"Konda","year":"2017","journal-title":"J 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cardiac arrest","volume":"9","author":"Alqarawi","year":"2023","journal-title":"JACC Clin Electrophysiol"},{"key":"2024081614460040000_ytae372-B8","doi-asserted-by":"crossref","first-page":"48","DOI":"10.1016\/j.ahj.2023.08.004","article-title":"Effectiveness of the risk stratification proposed by the 2022 European Heart Rhythm Association expert consensus statement on arrhythmic mitral valve prolapse","volume":"266","author":"L'Hoyes","year":"2023","journal-title":"Am Heart J"},{"key":"2024081614460040000_ytae372-B9","doi-asserted-by":"crossref","first-page":"3121","DOI":"10.1093\/eurheartj\/ehad491","article-title":"Arrhythmic mitral valve prolapse and mitral annular disjunction: pathophysiology, risk stratification, and management","volume":"44","author":"Essayagh","year":"2023","journal-title":"Eur Heart J"},{"key":"2024081614460040000_ytae372-B10","doi-asserted-by":"crossref","first-page":"635","DOI":"10.1016\/j.hrthm.2022.12.024","article-title":"Flecainide in patients with arrhythmic mitral valve syndrome: a case series","volume":"20","author":"Aabel","year":"2023","journal-title":"Heart Rhythm"},{"key":"2024081614460040000_ytae372-B11","doi-asserted-by":"crossref","first-page":"2005","DOI":"10.1161\/CIRCULATIONAHA.107.703157","article-title":"Sustained ventricular tachycardia associated with corrective valve surgery","volume":"116","author":"Eckart","year":"2007","journal-title":"Circulation"},{"key":"2024081614460040000_ytae372-B12","doi-asserted-by":"crossref","first-page":"581","DOI":"10.1016\/j.hroo.2023.08.003","article-title":"Genetic mechanisms underlying arrhythmogenic mitral valve prolapse: current and future perspectives","volume":"4","author":"Levy","year":"2023","journal-title":"Heart Rhythm O2"}],"container-title":["European Heart Journal - Case 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