{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,11,19]],"date-time":"2025-11-19T14:09:48Z","timestamp":1763561388279,"version":"3.45.0"},"reference-count":5,"publisher":"Oxford University Press (OUP)","issue":"11","license":[{"start":{"date-parts":[[2025,10,15]],"date-time":"2025-10-15T00:00:00Z","timestamp":1760486400000},"content-version":"vor","delay-in-days":1,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2025,10,31]]},"abstract":"<jats:title>Abstract<\/jats:title>\n                  <jats:sec>\n                    <jats:title>Background<\/jats:title>\n                    <jats:p>Pulmonary hypertension is often a difficult to diagnose condition, in particular in younger population of patients. Early diagnosis and treatment of this condition is crucial to prevent further morbidity and mortality.<\/jats:p>\n                  <\/jats:sec>\n                  <jats:sec>\n                    <jats:title>Case summary<\/jats:title>\n                    <jats:p>A 32-year-old woman with a history of Ebstein anomaly (EA) and secundum atrial septal defect (ASD), who underwent transcatheter ASD closure at age 19, presented with progressive fatigue and exertional dyspnoea. Further evaluation revealed presence of compression of right pulmonary veins (rPVs) by the ASD device resulting in post-capillary pulmonary hypertension (PHTN) and worsening of right ventricular (RV) failure. Following surgical explantation of the ASD device, PHTN resolved with improvement of patient\u2019s functional status.<\/jats:p>\n                  <\/jats:sec>\n                  <jats:sec>\n                    <jats:title>Discussion<\/jats:title>\n                    <jats:p>This case depicts a rare haemodynamic entity of worsening PHTN in a 32-year-old patient with EA post-ASD closure. It illustrates a rare complication of compression of rPVs by the ASD device. Therefore, suspicion should be high for evaluating rPVs in EA with worsening PTHN and RV failure post-ASD closure.<\/jats:p>\n                  <\/jats:sec>","DOI":"10.1093\/ehjcr\/ytaf527","type":"journal-article","created":{"date-parts":[[2025,10,13]],"date-time":"2025-10-13T13:25:07Z","timestamp":1760361907000},"source":"Crossref","is-referenced-by-count":0,"title":["Secondary pulmonary hypertension in an adult patient with Ebstein anomaly post-atrial septal defect closure; can it be reversible? A case report"],"prefix":"10.1093","volume":"9","author":[{"given":"Ahmed","family":"Kheiwa","sequence":"first","affiliation":[{"name":"Department of Internal Medicine, Division of Cardiology, Loma Linda University Medical Center , 11234 Anderson St., Loma Linda, CA 92354 ,","place":["USA"]}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-7701-6268","authenticated-orcid":false,"given":"Vandad","family":"Saadat","sequence":"additional","affiliation":[{"name":"Department of Internal Medicine, Loma Linda University Medical Center , 11234 Anderson St., Loma Linda, CA 92354 ,","place":["USA"]}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Joseph","family":"Chung","sequence":"additional","affiliation":[{"name":"Department of Internal Medicine, Division of Cardiology, Loma Linda University Medical Center , 11234 Anderson St., Loma Linda, CA 92354 ,","place":["USA"]}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Stephen","family":"Nageotte","sequence":"additional","affiliation":[{"name":"Departments of Pediatrics, Pediatric Cardiology, Loma Linda University Medical Center , 11234 Anderson St., Loma Linda, CA 92354 ,","place":["USA"]}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Anees","family":"Razzouk","sequence":"additional","affiliation":[{"name":"Department of Cardiothoracic Surgery, Loma Linda University Medical Center , 11234 Anderson St., Loma Linda, CA 92354 ,","place":["USA"]}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"286","published-online":{"date-parts":[[2025,10,14]]},"reference":[{"key":"2025111909071295500_ytaf527-B1","doi-asserted-by":"crossref","first-page":"594","DOI":"10.1007\/s11936-012-0209-2","article-title":"Diagnosis and management of Ebstein anomaly of the tricuspid valve","volume":"14","author":"Krieger","year":"2012","journal-title":"Curr Treat Options Cardiovasc Med"},{"key":"2025111909071295500_ytaf527-B2","doi-asserted-by":"crossref","first-page":"487","DOI":"10.1016\/S1010-7940(00)00466-8","article-title":"Surgical treatment of Wolf-Parkinson-White syndrome during plastic operations in patients with Ebstein\u2019s anomaly","volume":"18","author":"Lazorishinets","year":"2000","journal-title":"Eur J Cardiothorac Surg"},{"key":"2025111909071295500_ytaf527-B3","first-page":"e698","article-title":"2018 AHA\/ACC guideline for the management of adults with congenital heart disease: a report of the American College of Cardiology\/American Heart Association task force on clinical practice guidelines","volume":"139","author":"Stout","year":"2019","journal-title":"Circulation"},{"key":"2025111909071295500_ytaf527-B4","doi-asserted-by":"crossref","first-page":"1970","DOI":"10.1093\/eurheartj\/ehx794","article-title":"Sudden death in patients with Ebstein\u2019s anomaly","volume":"39","author":"Attenhoffer","year":"2018","journal-title":"Eur Heart J"},{"key":"2025111909071295500_ytaf527-B5","first-page":"1300","article-title":"Catheter ablation of ventricular arrhythmia for Ebstein\u2019s anomaly in unoperated and post-surgical patients","volume":"4","author":"Moore","year":"2018","journal-title":"J Am Coll Cardiol"}],"container-title":["European Heart Journal - 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