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The fused type (right-left cusp fusion, right-non-coronary cusp fusion and left-non-coronary cusp fusion phenotypes); 2. The 2-sinus type (latero-lateral and antero-posterior phenotypes); and 3. The partial-fusion (forme fruste) type. The presence of raphe and the symmetry of the fused type phenotypes are critical aspects to describe. The International Consensus also recognizes 3 types of bicuspid valve-associated aortopathy: 1. The ascending phenotype; 2. The root phenotype; and 3. Extended phenotypes.<\/jats:p>","DOI":"10.1093\/ejcts\/ezab038","type":"journal-article","created":{"date-parts":[[2021,1,25]],"date-time":"2021-01-25T15:23:05Z","timestamp":1611588185000},"page":"448-476","source":"Crossref","is-referenced-by-count":190,"title":["International consensus statement on nomenclature and classification of the congenital bicuspid aortic valve and its aortopathy, for clinical, surgical, interventional and research purposes"],"prefix":"10.1093","volume":"60","author":[{"ORCID":"https:\/\/orcid.org\/0000-0002-2341-5247","authenticated-orcid":false,"given":"Hector I","family":"Michelena","sequence":"first","affiliation":[{"name":"Department of Cardiovascular Medicine, Mayo Clinic, Rochester, MN, USA"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-4636-3339","authenticated-orcid":false,"given":"Alessandro","family":"Della Corte","sequence":"additional","affiliation":[{"name":"Department of Translational Medical Sciences, University of Campania \u201cL. 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