{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,6,24]],"date-time":"2026-06-24T20:04:40Z","timestamp":1782331480923,"version":"3.54.5"},"reference-count":10,"publisher":"Oxford University Press (OUP)","issue":"3","license":[{"start":{"date-parts":[[2022,4,1]],"date-time":"2022-04-01T00:00:00Z","timestamp":1648771200000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/academic.oup.com\/journals\/pages\/open_access\/funder_policies\/chorus\/standard_publication_model"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2022,8,3]]},"abstract":"<jats:title>Abstract<\/jats:title>\n               <jats:p\/>\n               <jats:sec>\n                  <jats:title>OBJECTIVES<\/jats:title>\n                  <jats:p>Congenital tricuspid valve dysplasia (TVD) is a rare cardiac disease, often discussed in the same way as Ebstein\u2019s anomaly. Though the morphology of TVD is different, the clinical appearance is similar. The indication for surgical treatment depends on the morphology of the tricuspid valve (TV) and the clinical presentation.<\/jats:p>\n               <\/jats:sec>\n               <jats:sec>\n                  <jats:title>METHODS<\/jats:title>\n                  <jats:p>We reviewed all patients below 18 years of age who underwent TV repair between 2005 and 2019 and identified 9 with a TVD. The diagnosis was verified with the operative notes and patients were excluded if the septal leaflet was displaced as in Ebstein\u2019s anomaly. The aim of the study was to describe the morphology of the TV and analyse the surgical possibilities and their results.<\/jats:p>\n               <\/jats:sec>\n               <jats:sec>\n                  <jats:title>RESULTS<\/jats:title>\n                  <jats:p>The median age at surgery was 2.3 years (5 days to 14 years), 3 patients were neonates with a duct-dependent pulmonary circulation. Morphology of the TV showed a tethering of at least 1 leaflet in all patients, a restrictive septal leaflet in 8, a large anterior leaflet in 7 and a small posterior leaflet in 4. Surgical techniques included an annuloplasty in 7 patients, a leaflet procedure in 6 patients, an edge-to-edge stitch in 5 patients and a primary Starnes procedure in 1 neonate. During a median follow-up time of 2.8 years (5 months to 15 years), 1 valve replacement and 1 conversion to univentricular palliation were necessary.<\/jats:p>\n               <\/jats:sec>\n               <jats:sec>\n                  <jats:title>CONCLUSIONS<\/jats:title>\n                  <jats:p>Unequal leaflet size and tethering are the most common features of TVD. A variety of surgical techniques is available to achieve good results beyond the neonatal period.<\/jats:p>\n               <\/jats:sec>","DOI":"10.1093\/ejcts\/ezac212","type":"journal-article","created":{"date-parts":[[2022,3,18]],"date-time":"2022-03-18T20:09:55Z","timestamp":1647634195000},"source":"Crossref","is-referenced-by-count":8,"title":["Surgical treatment of tricuspid valve dysplasia in children"],"prefix":"10.1093","volume":"62","author":[{"ORCID":"https:\/\/orcid.org\/0000-0002-1971-4375","authenticated-orcid":false,"given":"Julie","family":"Cleuziou","sequence":"first","affiliation":[{"name":"Department of Congenital and Paediatric Heart Surgery, German Heart Center Munich, Technical University of Munich, School of Medicine , Munich, Germany"},{"name":"Division of Congenital and Paediatric Heart Surgery, University Hospital of Munich, Ludwig-Maximilians-Universit\u00e4t , Munich, Germany"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Milka","family":"Pringsheim","sequence":"additional","affiliation":[{"name":"Department of Pediatric Cardiology and Congenital Heart Defects, German Heart Center Munich, Technical University of Munich, School of Medicine , Munich, Germany"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Anni","family":"Stroh","sequence":"additional","affiliation":[{"name":"Department of Cardiovascular Surgery, German Heart Center Munich, Technical University of Munich, School of Medicine , Munich, Germany"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-8540-7090","authenticated-orcid":false,"given":"Melchior","family":"Burri","sequence":"additional","affiliation":[{"name":"Department of Cardiovascular Surgery, German Heart Center Munich, Technical University of Munich, School of Medicine , Munich, Germany"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"R\u00fcdiger","family":"Lange","sequence":"additional","affiliation":[{"name":"Department of Cardiovascular Surgery, German Heart Center Munich, Technical University of Munich, School of Medicine , Munich, Germany"},{"name":"German Center for Cardiovascular Research (DZHK)\u2014Partner Site Munich Heart Alliance , Munich, Germany"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-2716-1424","authenticated-orcid":false,"given":"J\u00fcrgen","family":"H\u00f6rer","sequence":"additional","affiliation":[{"name":"Department of Congenital and Paediatric Heart Surgery, German Heart Center Munich, Technical University of Munich, School of Medicine , Munich, Germany"},{"name":"Division of Congenital and Paediatric Heart Surgery, University Hospital of Munich, Ludwig-Maximilians-Universit\u00e4t , Munich, Germany"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"286","published-online":{"date-parts":[[2022,4,1]]},"reference":[{"key":"2022082913085572900_ezac212-B1","doi-asserted-by":"crossref","first-page":"121","DOI":"10.1017\/S104795111000168X","article-title":"Congenital tricuspid regurgitation: review and a proposed new classification","volume":"21","author":"Gupta","year":"2011","journal-title":"Cardiol Young"},{"key":"2022082913085572900_ezac212-B2","doi-asserted-by":"crossref","first-page":"783","DOI":"10.1177\/2150135120949235","article-title":"The congenital tricuspid valve spectrum: from Ebstein to dysplasia","volume":"11","author":"Stephens","year":"2020","journal-title":"World J Pediatr Congenit Heart Surg"},{"key":"2022082913085572900_ezac212-B3","doi-asserted-by":"crossref","first-page":"1545","DOI":"10.1016\/j.jtcvs.2020.05.032","article-title":"Cone versus conventional repair for Ebstein's 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Caucasian children","volume":"27","author":"Cantinotti","year":"2014","journal-title":"J Am Soc Echocardiogr"},{"key":"2022082913085572900_ezac212-B7","doi-asserted-by":"crossref","first-page":"1220","DOI":"10.1016\/j.jtcvs.2015.09.036","article-title":"Caution: there is no \u201call or none\u201d with Ebstein anomaly","volume":"150","author":"Dearani","year":"2015","journal-title":"J Thorac Cardiovasc Surg"},{"key":"2022082913085572900_ezac212-B8","doi-asserted-by":"crossref","first-page":"1155","DOI":"10.1093\/ejcts\/ezx146","article-title":"Fifteen years' experience with the use of artificial chords for valve reconstruction in children","volume":"52","author":"Kluin","year":"2017","journal-title":"Eur J Cardiothorac Surg"},{"key":"2022082913085572900_ezac212-B9","doi-asserted-by":"crossref","first-page":"1811","DOI":"10.1016\/j.athoracsur.2015.11.029","article-title":"Application of cone reconstruction for neonatal Ebstein anomaly or tricuspid valve dysplasia","volume":"101","author":"Mizuno","year":"2016","journal-title":"Ann Thorac Surg"},{"key":"2022082913085572900_ezac212-B10","doi-asserted-by":"crossref","first-page":"1257","DOI":"10.1161\/CIRCULATIONAHA.115.021241","article-title":"Single-Ventricle outcomes after neonatal palliation of severe Ebstein anomaly with modified Starnes procedure","volume":"134","author":"Kumar","year":"2016","journal-title":"Circulation"}],"container-title":["European Journal of Cardio-Thoracic 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