{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,6]],"date-time":"2026-10-06T13:56:19Z","timestamp":1791294979262,"version":"4.1.0"},"reference-count":66,"publisher":"Oxford University Press (OUP)","issue":"15","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Human Molecular Genetics"],"DOI":"10.1093\/hmg\/ddn136","type":"journal-article","created":{"date-parts":[[2008,4,29]],"date-time":"2008-04-29T00:34:52Z","timestamp":1209429292000},"page":"2357-2369","source":"Crossref","is-referenced-by-count":46,"title":["Epidermal expression of the truncated prelamin A causing Hutchinson-Gilford progeria syndrome: effects on keratinocytes, hair and skin"],"prefix":"10.1093","volume":"17","author":[{"given":"Y.","family":"Wang","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"A. A.","family":"Panteleyev","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"D. M.","family":"Owens","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"K.","family":"Djabali","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"C. L.","family":"Stewart","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"H. J.","family":"Worman","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"286","published-online":{"date-parts":[[2008,4,17]]},"reference":[{"key":"2_25221968","first-page":"914","volume":"2","year":"1904","journal-title":"BMJ","ISSN":"https:\/\/id.crossref.org\/issn\/0959-8138","issn-type":"print"},{"issue":"4","key":"3_12251118","doi-asserted-by":"publisher","first-page":"697","DOI":"10.1016\/S0022-3476(72)80229-4","volume":"80","author":"DeBusk","year":"1972","journal-title":"The Journal of pediatrics","ISSN":"https:\/\/id.crossref.org\/issn\/0022-3476","issn-type":"print"},{"issue":"6","key":"4_30352819","doi-asserted-by":"publisher","first-page":"592","DOI":"10.1056\/NEJMoa0706898","volume":"358","author":"Merideth","year":"2008","journal-title":"New England Journal of Medicine","ISSN":"https:\/\/id.crossref.org\/issn\/0028-4793","issn-type":"print"},{"issue":"6937","key":"5_17629219","doi-asserted-by":"publisher","first-page":"293","DOI":"10.1038\/nature01629","volume":"423","author":"Eriksson","year":"2003","journal-title":"Nature; Physical Science (London)","ISSN":"https:\/\/id.crossref.org\/issn\/1476-4687","issn-type":"print"},{"issue":"5628","key":"6_17695308","doi-asserted-by":"publisher","first-page":"2055","DOI":"10.1126\/science.1084125","volume":"300","year":"2003","journal-title":"Science","ISSN":"https:\/\/id.crossref.org\/issn\/0036-8075","issn-type":"print"},{"issue":"5","key":"7_17644737","doi-asserted-by":"publisher","first-page":"271","DOI":"10.1007\/s10038-003-0025-3","volume":"48","author":"Cao","year":"2003","journal-title":"Journal of human genetics","ISSN":"https:\/\/id.crossref.org\/issn\/1434-5161","issn-type":"print"},{"key":"8_30629606","first-page":"277","volume":"19","year":"1980","ISSN":"https:\/\/id.crossref.org\/issn\/1097-4172","issn-type":"print"},{"issue":"17","key":"9_13921788","doi-asserted-by":"publisher","first-page":"6450","DOI":"10.1073\/pnas.83.17.6450","volume":"83","author":"Fisher","year":"1986","journal-title":"PNAS","ISSN":"https:\/\/id.crossref.org\/issn\/0027-8424","issn-type":"print"},{"issue":"22","key":"10_14408680","doi-asserted-by":"crossref","first-page":"16321","DOI":"10.1016\/S0021-9258(19)85424-8","volume":"268","author":"Lin","year":"1993","journal-title":"Journal of Biological Chemistry","ISSN":"https:\/\/id.crossref.org\/issn\/0021-9258","issn-type":"print"},{"issue":"6088","key":"11_13946183","doi-asserted-by":"publisher","first-page":"560","DOI":"10.1038\/323560a0","volume":"323","author":"Aebi","year":"1986","journal-title":"Nature; Physical Science (London)","ISSN":"https:\/\/id.crossref.org\/issn\/1476-4687","issn-type":"print"},{"issue":"6053","key":"12_13728499","doi-asserted-by":"publisher","first-page":"463","DOI":"10.1038\/319463a0","volume":"319","author":"McKeon","year":"1986","journal-title":"Nature; Physical Science (London)","ISSN":"https:\/\/id.crossref.org\/issn\/1476-4687","issn-type":"print"},{"issue":"11","key":"13_13842103","doi-asserted-by":"publisher","first-page":"3839","DOI":"10.1073\/pnas.83.11.3839","volume":"83","author":"Goldman","year":"1986","journal-title":"PNAS","ISSN":"https:\/\/id.crossref.org\/issn\/0027-8424","issn-type":"print"},{"issue":"10","key":"14_28825241","doi-asserted-by":"publisher","first-page":"2121","DOI":"10.1016\/j.yexcr.2007.03.028","volume":"313","author":"Worman","year":"2007","journal-title":"Experimental cell research","ISSN":"https:\/\/id.crossref.org\/issn\/0014-4827","issn-type":"print"},{"issue":"5","key":"15_5629798","doi-asserted-by":"publisher","first-page":"1489","DOI":"10.1083\/jcb.110.5.1489","volume":"110","author":"Beck","year":"1990","journal-title":"The Journal of Cell Biology","ISSN":"https:\/\/id.crossref.org\/issn\/0021-9525","issn-type":"print"},{"issue":"20","key":"16_19673928","doi-asserted-by":"publisher","first-page":"13049","DOI":"10.1073\/pnas.192460799","volume":"99","year":"2002","journal-title":"PNAS","ISSN":"https:\/\/id.crossref.org\/issn\/0027-8424","issn-type":"print"},{"issue":"1","key":"17_17029879","doi-asserted-by":"publisher","first-page":"94","DOI":"10.1038\/nm0202-94","volume":"31","author":"Pend\u00a0\u00a0s","year":"2002","journal-title":"Nature genetics","ISSN":"https:\/\/id.crossref.org\/issn\/1061-4036","issn-type":"print"},{"issue":"Pt 1","key":"18_18746046","doi-asserted-by":"publisher","first-page":"129","DOI":"10.1042\/BJ20041359","volume":"387","author":"Corrigan","year":"2005","journal-title":"The Biochemical journal","ISSN":"https:\/\/id.crossref.org\/issn\/0264-6021","issn-type":"print"},{"issue":"Pt 16","key":"19_22463634","doi-asserted-by":"publisher","first-page":"3265","DOI":"10.1242\/jcs.03156","volume":"119","author":"Rusinol","year":"2006","journal-title":"Journal of Cell Science","ISSN":"https:\/\/id.crossref.org\/issn\/0021-9533","issn-type":"print"},{"issue":"12","key":"20_19676418","doi-asserted-by":"publisher","first-page":"2531","DOI":"10.1194\/jlr.R500011-JLR200","volume":"46","year":"2005","journal-title":"The Journal of Lipid Research","ISSN":"https:\/\/id.crossref.org\/issn\/0022-2275","issn-type":"print"},{"issue":"52","key":"21_22946338","doi-asserted-by":"publisher","first-page":"39741","DOI":"10.1074\/jbc.R600033200","volume":"281","year":"2006","journal-title":"Journal of Biological Chemistry","ISSN":"https:\/\/id.crossref.org\/issn\/0021-9258","issn-type":"print"},{"issue":"5","key":"22_18172260","doi-asserted-by":"publisher","first-page":"717","DOI":"10.1016\/j.exger.2004.02.002","volume":"39","author":"Bridger","year":"2004","journal-title":"Experimental gerontology","ISSN":"https:\/\/id.crossref.org\/issn\/0531-5565","issn-type":"print"},{"issue":"24","key":"23_19686510","doi-asserted-by":"publisher","first-page":"8963","DOI":"10.1073\/pnas.0402943101","volume":"101","year":"2004","journal-title":"PNAS","ISSN":"https:\/\/id.crossref.org\/issn\/0027-8424","issn-type":"print"},{"key":"24_19201192","doi-asserted-by":"publisher","first-page":"27","DOI":"10.1186\/1471-2121-6-27","volume":"6","author":"Paradisi","year":"2005","journal-title":"BMC cell biology [electronic resource]","ISSN":"https:\/\/id.crossref.org\/issn\/1471-2121","issn-type":"print"},{"issue":"29","key":"25_19690057","doi-asserted-by":"publisher","first-page":"10291","DOI":"10.1073\/pnas.0504641102","volume":"102","year":"2005","journal-title":"PNAS","ISSN":"https:\/\/id.crossref.org\/issn\/0027-8424","issn-type":"print"},{"issue":"7","key":"26_21587058","doi-asserted-by":"publisher","first-page":"2154","DOI":"10.1073\/pnas.0511133103","volume":"103","year":"2006","journal-title":"PNAS","ISSN":"https:\/\/id.crossref.org\/issn\/0027-8424","issn-type":"print"},{"issue":"36","key":"27_19690627","doi-asserted-by":"publisher","first-page":"12879","DOI":"10.1073\/pnas.0506001102","volume":"102","year":"2005","journal-title":"PNAS","ISSN":"https:\/\/id.crossref.org\/issn\/0027-8424","issn-type":"print"},{"issue":"20","key":"28_19449944","doi-asserted-by":"publisher","first-page":"2959","DOI":"10.1093\/hmg\/ddi326","volume":"14","year":"2005","journal-title":"Human Molecular Genetics","ISSN":"https:\/\/id.crossref.org\/issn\/0964-6906","issn-type":"print"},{"issue":"3-4","key":"29_21367500","doi-asserted-by":"publisher","first-page":"444","DOI":"10.1007\/s00439-005-0051-7","volume":"118","author":"Huang","year":"2005","journal-title":"Human genetics","ISSN":"https:\/\/id.crossref.org\/issn\/0340-6717","issn-type":"print"},{"issue":"40","key":"30_19690975","doi-asserted-by":"publisher","first-page":"14416","DOI":"10.1073\/pnas.0503712102","volume":"102","year":"2005","journal-title":"PNAS","ISSN":"https:\/\/id.crossref.org\/issn\/0027-8424","issn-type":"print"},{"issue":"4","key":"31_18782339","doi-asserted-by":"publisher","first-page":"440","DOI":"10.1038\/nm1204","volume":"11","author":"Scaffidi","year":"2005","journal-title":"Nature medicine","ISSN":"https:\/\/id.crossref.org\/issn\/1078-8956","issn-type":"print"},{"issue":"36","key":"32_19690626","doi-asserted-by":"publisher","first-page":"12873","DOI":"10.1073\/pnas.0505767102","volume":"102","year":"2005","journal-title":"PNAS","ISSN":"https:\/\/id.crossref.org\/issn\/0027-8424","issn-type":"print"},{"issue":"2","key":"33_12406247","doi-asserted-by":"publisher","first-page":"253","DOI":"10.1001\/archderm.107.2.253","volume":"107","author":"Fleischmajer","year":"1973","journal-title":"Archives of Dermatology","ISSN":"https:\/\/id.crossref.org\/issn\/0003-987X","issn-type":"print"},{"issue":"4","key":"34_5200012","doi-asserted-by":"publisher","first-page":"540","DOI":"10.1001\/archderm.125.4.540","volume":"125","author":"Badame","year":"1989","journal-title":"Archives of Dermatology","ISSN":"https:\/\/id.crossref.org\/issn\/0003-987X","issn-type":"print"},{"issue":"3","key":"35_9657602","doi-asserted-by":"crossref","first-page":"199","DOI":"10.1111\/j.1525-1470.1991.tb00859.x","volume":"8","author":"Gillar","year":"1991","journal-title":"Pediatric dermatology","ISSN":"https:\/\/id.crossref.org\/issn\/0736-8046","issn-type":"print"},{"issue":"4","key":"36_10476200","doi-asserted-by":"publisher","first-page":"282","DOI":"10.1046\/j.1525-1470.2000.01775.x","volume":"17","author":"Jansen","year":"2000","journal-title":"Pediatric dermatology","ISSN":"https:\/\/id.crossref.org\/issn\/0736-8046","issn-type":"print"},{"issue":"5","key":"37_5169966","doi-asserted-by":"publisher","first-page":"1563","DOI":"10.1073\/pnas.86.5.1563","volume":"86","author":"Vassar","year":"1989","journal-title":"PNAS","ISSN":"https:\/\/id.crossref.org\/issn\/0027-8424","issn-type":"print"},{"issue":"1","key":"38_16669827","doi-asserted-by":"publisher","first-page":"219","DOI":"10.1073\/pnas.94.1.219","volume":"94","author":"Wang","year":"1997","journal-title":"PNAS","ISSN":"https:\/\/id.crossref.org\/issn\/0027-8424","issn-type":"print"},{"key":"39_31523941","doi-asserted-by":"crossref","first-page":"177","DOI":"10.1046\/j.1524-475X.2002.11101.x","volume":"10","year":"2002","journal-title":"WOUND REP REG"},{"issue":"19","key":"40_11377094","doi-asserted-by":"crossref","first-page":"3419","DOI":"10.1242\/jcs.114.19.3419","volume":"114","author":"Panteleyev","year":"2001","journal-title":"Journal of Cell Science","ISSN":"https:\/\/id.crossref.org\/issn\/0021-9533","issn-type":"print"},{"issue":"4","key":"41_10982814","doi-asserted-by":"publisher","first-page":"523","DOI":"10.1046\/j.1523-1747.1999.00740.x","volume":"113","author":"Paus","year":"1999","journal-title":"Journal of Investigative Dermatology","ISSN":"https:\/\/id.crossref.org\/issn\/0022-202X","issn-type":"print"},{"issue":"1","key":"42_11226707","doi-asserted-by":"publisher","first-page":"3","DOI":"10.1046\/j.0022-202x.2001.01377.x","volume":"117","author":"Muller-Rover","year":"2001","journal-title":"Journal of Investigative Dermatology","ISSN":"https:\/\/id.crossref.org\/issn\/0022-202X","issn-type":"print"},{"issue":"2","key":"43_16860421","doi-asserted-by":"publisher","first-page":"231","DOI":"10.1006\/bbrc.1997.6945","volume":"236","author":"Coulombe","year":"1997","journal-title":"Biochemical and biophysical research communications","ISSN":"https:\/\/id.crossref.org\/issn\/0006-291X","issn-type":"print"},{"issue":"1","key":"44_18678550","doi-asserted-by":"publisher","first-page":"274","DOI":"10.1016\/j.yexcr.2004.10.033","volume":"304","author":"Santoro","year":"2005","journal-title":"Experimental cell research","ISSN":"https:\/\/id.crossref.org\/issn\/0014-4827","issn-type":"print"},{"key":"45_28544011","doi-asserted-by":"publisher","first-page":"2849","DOI":"10.2741\/2277","volume":"12","author":"Raja","year":"2007","journal-title":"Frontiers in bioscience : a journal and virtual library","ISSN":"https:\/\/id.crossref.org\/issn\/1093-9946","issn-type":"print"},{"issue":"9","key":"46_18423745","doi-asserted-by":"publisher","first-page":"715","DOI":"10.1136\/jmg.2004.019323","volume":"41","author":"Reddel","year":"2004","journal-title":"Journal of Medical Genetics","ISSN":"https:\/\/id.crossref.org\/issn\/0022-2593","issn-type":"print"},{"issue":"5","key":"47_6384110","doi-asserted-by":"publisher","first-page":"913","DOI":"10.1083\/jcb.147.5.913","volume":"147","author":"Sullivan","year":"1999","journal-title":"The Journal of Cell Biology","ISSN":"https:\/\/id.crossref.org\/issn\/0021-9525","issn-type":"print"},{"issue":"52","key":"48_19688344","doi-asserted-by":"publisher","first-page":"18111","DOI":"10.1073\/pnas.0408558102","volume":"101","year":"2004","journal-title":"PNAS","ISSN":"https:\/\/id.crossref.org\/issn\/0027-8424","issn-type":"print"},{"issue":"20","key":"49_18446348","doi-asserted-by":"publisher","first-page":"2493","DOI":"10.1093\/hmg\/ddh265","volume":"13","year":"2004","journal-title":"Human Molecular Genetics","ISSN":"https:\/\/id.crossref.org\/issn\/0964-6906","issn-type":"print"},{"issue":"11","key":"50_18870706","doi-asserted-by":"publisher","first-page":"1503","DOI":"10.1093\/hmg\/ddi159","volume":"14","year":"2005","journal-title":"Human Molecular Genetics","ISSN":"https:\/\/id.crossref.org\/issn\/0964-6906","issn-type":"print"},{"issue":"4","key":"51_9748601","doi-asserted-by":"crossref","first-page":"1112","DOI":"10.1042\/bst0191112","volume":"19","author":"Fuchs","year":"1991","journal-title":"Biochemical Society Transactions","ISSN":"https:\/\/id.crossref.org\/issn\/0300-5127","issn-type":"print"},{"key":"52_31523942","first-page":"899","volume":"69","year":"1992","ISSN":"https:\/\/id.crossref.org\/issn\/1097-4172","issn-type":"print"},{"issue":"8","key":"53_22391227","doi-asserted-by":"publisher","first-page":"2115","DOI":"10.1172\/JCI28968","volume":"116","year":"2006","journal-title":"Journal of Clinical Investigation","ISSN":"https:\/\/id.crossref.org\/issn\/0021-9738","issn-type":"print"},{"issue":"9","key":"54_21644902","doi-asserted-by":"publisher","first-page":"3250","DOI":"10.1073\/pnas.0600012103","volume":"103","year":"2006","journal-title":"PNAS","ISSN":"https:\/\/id.crossref.org\/issn\/0027-8424","issn-type":"print"},{"issue":"7","key":"55_30600466","doi-asserted-by":"publisher","first-page":"969","DOI":"10.1242\/jcs.022913","volume":"121","year":"2008","journal-title":"Journal of Cell Science","ISSN":"https:\/\/id.crossref.org\/issn\/0021-9533","issn-type":"print"},{"issue":"3","key":"56_18021984","doi-asserted-by":"publisher","first-page":"357","DOI":"10.1172\/JCI200419448","volume":"113","author":"Nikolova","year":"2004","journal-title":"Journal of Clinical Investigation","ISSN":"https:\/\/id.crossref.org\/issn\/0021-9738","issn-type":"print"},{"issue":"1","key":"57_18576023","doi-asserted-by":"publisher","first-page":"155","DOI":"10.1093\/hmg\/ddi017","volume":"14","year":"2005","journal-title":"Human Molecular Genetics","ISSN":"https:\/\/id.crossref.org\/issn\/0964-6906","issn-type":"print"},{"issue":"15","key":"58_19265809","doi-asserted-by":"publisher","first-page":"2167","DOI":"10.1093\/hmg\/ddi221","volume":"14","year":"2005","journal-title":"Human Molecular Genetics","ISSN":"https:\/\/id.crossref.org\/issn\/0964-6906","issn-type":"print"},{"issue":"16","key":"59_22356430","doi-asserted-by":"publisher","first-page":"2479","DOI":"10.1093\/hmg\/ddl170","volume":"15","year":"2006","journal-title":"Human Molecular Genetics","ISSN":"https:\/\/id.crossref.org\/issn\/0964-6906","issn-type":"print"},{"issue":"5767","key":"60_21622301","doi-asserted-by":"publisher","first-page":"1621","DOI":"10.1126\/science.1124875","volume":"311","year":"2006","journal-title":"Science","ISSN":"https:\/\/id.crossref.org\/issn\/0036-8075","issn-type":"print"},{"issue":"1-2","key":"61_30431108","doi-asserted-by":"crossref","first-page":"36","DOI":"10.1016\/j.bbalip.2007.11.003","volume":"1781","author":"Yang","year":"2008","journal-title":"Biochimica et Biophysica Acta. Protein Structure and Molecular Enzymology","ISSN":"https:\/\/id.crossref.org\/issn\/0006-3002","issn-type":"print"},{"key":"62_28598038","doi-asserted-by":"crossref","first-page":"4435","DOI":"10.1242\/jcs.114.24.4435","volume":"114","year":"2001","journal-title":"Journal of Cell Science","ISSN":"https:\/\/id.crossref.org\/issn\/0021-9533","issn-type":"print"},{"issue":"6","key":"63_10565808","doi-asserted-by":"publisher","first-page":"431","DOI":"10.1034\/j.1600-0625.2000.009006431.x","volume":"9","author":"Li","year":"2000","journal-title":"Experimental dermatology","ISSN":"https:\/\/id.crossref.org\/issn\/0906-6705","issn-type":"print"},{"issue":"11","key":"64_10815357","doi-asserted-by":"crossref","first-page":"1709","DOI":"10.1242\/jcs.112.11.1709","volume":"112","author":"Ostlund","year":"1999","journal-title":"Journal of Cell Science","ISSN":"https:\/\/id.crossref.org\/issn\/0021-9533","issn-type":"print"},{"issue":"1-3","key":"65_18091320","doi-asserted-by":"crossref","first-page":"87","DOI":"10.1016\/j.bbagen.2004.01.008","volume":"1671","author":"Manilal","year":"2004","journal-title":"Biochimica et Biophysica Acta. Protein Structure and Molecular Enzymology","ISSN":"https:\/\/id.crossref.org\/issn\/0006-3002","issn-type":"print"},{"key":"66_23822909","first-page":"233","volume":"11","year":"1992","journal-title":"Journal of experimental &amp; clinical cancer research : CR","ISSN":"https:\/\/id.crossref.org\/issn\/0392-9078","issn-type":"print"},{"issue":"1","key":"67_10724816","doi-asserted-by":"crossref","first-page":"53","DOI":"10.1111\/j.1600-0625.1999.tb00348.x","volume":"8","author":"Romero","year":"1999","journal-title":"Experimental dermatology","ISSN":"https:\/\/id.crossref.org\/issn\/0906-6705","issn-type":"print"}],"container-title":["Human Molecular Genetics"],"original-title":[],"language":"en","deposited":{"date-parts":[[2021,9,9]],"date-time":"2021-09-09T03:00:22Z","timestamp":1631156422000},"score":1,"resource":{"primary":{"URL":"https:\/\/academic.oup.com\/hmg\/article-lookup\/doi\/10.1093\/hmg\/ddn136"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2008,4,17]]},"references-count":66,"journal-issue":{"issue":"15","published-online":{"date-parts":[[2008,4,17]]}},"URL":"https:\/\/doi.org\/10.1093\/hmg\/ddn136","relation":{},"ISSN":["0964-6906","1460-2083"],"issn-type":[{"value":"0964-6906","type":"print"},{"value":"1460-2083","type":"electronic"}],"subject":[],"published":{"date-parts":[[2008,4,17]]}}}