{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,13]],"date-time":"2026-09-13T03:24:36Z","timestamp":1789269876140,"version":"build-2803163510"},"reference-count":10,"publisher":"Oxford University Press (OUP)","issue":"11","license":[{"start":{"date-parts":[[2021,9,15]],"date-time":"2021-09-15T00:00:00Z","timestamp":1631664000000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/academic.oup.com\/pages\/standard-publication-reuse-rights"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2021,10,20]]},"abstract":"<jats:title>Abstract<\/jats:title>\n               <jats:p>Mevalonate kinase deficiency should be considered in patients with severe very-early-onset inflammatory bowel disease (IBD), especially in patients with a history of recurrent or chronic fever, peritoneal adhesions, and atypical IBD pathology. Anti-interleukin-1 therapy may be efficacious in these patients with monogenic very-early-onset IBD.<\/jats:p>","DOI":"10.1093\/ibd\/izab139","type":"journal-article","created":{"date-parts":[[2021,9,15]],"date-time":"2021-09-15T17:30:32Z","timestamp":1631727032000},"page":"1853-1857","source":"Crossref","is-referenced-by-count":19,"title":["Mevalonate Kinase Deficiency: A Cause of Severe Very-Early-Onset Inflammatory Bowel Disease"],"prefix":"10.1093","volume":"27","author":[{"given":"Brigitte","family":"Bader-Meunier","sequence":"first","affiliation":[{"name":"Department of Paediatric Immunology, Hematology, and Rheumatology, Groupe Hospitalier Necker-Enfants Malades, Assistance Publique-H\u00f4pitaux de Paris, Reference Centre for Rheumatic, Autoimmune and Systemic Diseases in Children, Assistance Publique-H\u00f4pitaux de Paris, and Imagine Foundation , Paris , France"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Andreia 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