{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,11,4]],"date-time":"2025-11-04T10:51:54Z","timestamp":1762253514823,"version":"3.41.2"},"reference-count":10,"publisher":"Oxford University Press (OUP)","issue":"9","license":[{"start":{"date-parts":[[2020,9,30]],"date-time":"2020-09-30T00:00:00Z","timestamp":1601424000000},"content-version":"vor","delay-in-days":29,"URL":"http:\/\/creativecommons.org\/licenses\/by\/4.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2020,9,1]]},"abstract":"<jats:title>Abstract<\/jats:title>\n               <jats:p>Mayer\u2013Rokitansky\u2013K\u00fcster\u2013Hauser syndrome is a congenital malformation that affects the uterus and upper two-thirds of the vagina. Its prevalence is estimated to be 1 in 4500 live births. We present the case of a 19-year-old patient that presented with primary amenorrhea and cyclic abdominal pain. Upon the exploratory laparoscopy, a right rudimentary uterine horn and left unicornuate uterus were found. These two entities were completely separated from each other and from the vaginal vault. In addition, a left ovarian endometrioma was also found. The unicornuate uterus was resected with an intent to resolve the pain. Endometriosis is known to raise the risk of ovarian cancer by 50%. Therefore, a left salpingo-oophorectomy was performed to minimize the risk of ovarian cancer and endometriosis recurrence. In conclusion, ovarian endometriomas should be suspected when obstructive malformations are present with active endometrial remnants. These lesions should be managed appropriately to optimize the postoperative outcomes.<\/jats:p>","DOI":"10.1093\/jscr\/rjaa393","type":"journal-article","created":{"date-parts":[[2020,9,1]],"date-time":"2020-09-01T11:09:37Z","timestamp":1598958577000},"source":"Crossref","is-referenced-by-count":2,"title":["A rare form of Mayer\u2013Rokitansky\u2013K\u00fcster\u2013Hauser syndrome associated with ovarian endometrioma: a case report"],"prefix":"10.1093","volume":"2020","author":[{"ORCID":"https:\/\/orcid.org\/0000-0001-9837-8420","authenticated-orcid":false,"given":"Antoine","family":"Naem","sequence":"first","affiliation":[{"name":"Faculty of Medicine of Damascus University, Damascus, Syria"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Anwar","family":"Shamandi","sequence":"additional","affiliation":[{"name":"Faculty of Medicine of Damascus University, Damascus, Syria"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Bashar","family":"AL-Kurdy","sequence":"additional","affiliation":[{"name":"University Hospital of Obstetrics and Gynecology, Damascus, Syria"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"286","published-online":{"date-parts":[[2020,9,30]]},"reference":[{"key":"2020092920344705800_ref1","doi-asserted-by":"crossref","first-page":"101655","DOI":"10.1016\/j.jogoh.2019.101655","article-title":"Postoperative evaluation of chronic pain in patients with Mayer-Rokitansky-K\u00fcster-Hauser (MRKH) syndrome and uterine horn remnant: experience of a tertiary referring gynaecological department","volume":"49","author":"Dabi","year":"2020","journal-title":"J Gynecol Obstet Hum Reprod"},{"key":"2020092920344705800_ref2","doi-asserted-by":"crossref","first-page":"792","DOI":"10.1093\/humrep\/dei381","article-title":"Clinical aspects of Mayer-Rokitansky-Kuester-Hauser syndrome: recommendations for clinical 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