{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,30]],"date-time":"2026-10-30T14:33:57Z","timestamp":1793370837076,"version":"4.5.0"},"reference-count":12,"publisher":"Oxford University Press (OUP)","issue":"5","license":[{"start":{"date-parts":[[2021,5,26]],"date-time":"2021-05-26T00:00:00Z","timestamp":1621987200000},"content-version":"vor","delay-in-days":25,"URL":"http:\/\/creativecommons.org\/licenses\/by-nc\/4.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2021,5,1]]},"abstract":"<jats:title>Abstract<\/jats:title>\n               <jats:p>The Mayer-Rokitansky-K\u00fcster-Hauser (MRKH) syndrome is a congenital disorder caused by the abnormal absence of paramesonephric ducts. The main characteristics of this syndrome include hypoplasia or aplasia of the uterus, absence of the cervix and upper part of vagina. Otherwise, ovaries and fallopian tubes have normal functions. A 9-year-old girl presented to the emergency department by acute abdominal pain. Based on a high probable diagnosis of ovarian torsion, surgical exploration was accomplished demonstrating rudimentary or aplastic uterus, hypoplasia of the left adnexa and torsion of the right ovary. In consideration of MRKH syndrome, further assessments were done and the diagnosis was confirmed.<\/jats:p>\n               <jats:p>As this syndrome is rare and there is a probability of ovarian torsion caused by malformation of the ovarian ligament, physicians should be aware of this syndrome to diagnose it earlier and preserve the ovarian tissue.<\/jats:p>","DOI":"10.1093\/jscr\/rjab130","type":"journal-article","created":{"date-parts":[[2021,5,11]],"date-time":"2021-05-11T19:11:40Z","timestamp":1620760300000},"source":"Crossref","is-referenced-by-count":5,"title":["A rare case of Mayer-Rokitansky-K\u00fcster-Hauser syndrome with right ovarian torsion and hypoplasia of the left adnexa"],"prefix":"10.1093","volume":"2021","author":[{"given":"Maryam","family":"Masoumi Shahrbabak","sequence":"first","affiliation":[{"name":"Gynecology ward, Imam Ali Hospital, Kerman University of Medical Sciences, Kerman, Iran"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Faridadin","family":"Ebrahimi Meimand","sequence":"additional","affiliation":[{"name":"Department of Minimally Invasive Surgery, Iran University of Medical Sciences, Tehran, Iran"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"286","published-online":{"date-parts":[[2021,5,26]]},"reference":[{"key":"2021070811435978300_ref1","doi-asserted-by":"crossref","first-page":"539","DOI":"10.1016\/j.jgyn.2008.07.002","article-title":"The Mayer-Rokitansky-K\u00fcster-Hauser (MRKH) syndrome: clinical description and genetics","volume":"37","author":"Morcel","year":"2008","journal-title":"Journal de Gynecologie Obstetrique et Biologie de la Reproduction"},{"key":"2021070811435978300_ref2","doi-asserted-by":"crossref","DOI":"10.1155\/2018\/2369430","article-title":"Diagnosis and management of ovarian tumor in Mayer-Rokitansky-K\u00fcster-Hauser (MRKH) 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Mayer-Rokitansky-K\u00fcster-Hauser syndrome","volume":"2015","author":"Narayanan","year":"2015","journal-title":"Case Rep"},{"key":"2021070811435978300_ref10","article-title":"Rare case of leiomyoma and adenomyosis in Mayer-Rokitansky-Kuster-Hauser syndrome","volume":"2016","author":"Hoo","year":"2016","journal-title":"Case Rep Obstetr Gynecol"},{"key":"2021070811435978300_ref11","doi-asserted-by":"crossref","first-page":"6","DOI":"10.1016\/j.jmig.2016.04.007","article-title":"Acute torsion of paraovarian cyst and ipsilateral uterine remnant leiomyoma in a patient with Mayer\u2013Rokitansky\u2013K\u00fcster\u2013Hauser syndrome","volume":"24","author":"Yi","year":"2017","journal-title":"J Minimally Invasive Gynecol"},{"key":"2021070811435978300_ref12","doi-asserted-by":"crossref","first-page":"607","DOI":"10.1016\/j.fertnstert.2014.04.034","article-title":"Acute torsion of uterine remnant leiomyoma with Mayer-Rokitansky-K\u00fcster-Hauser 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