{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,7,30]],"date-time":"2025-07-30T12:04:30Z","timestamp":1753877070104,"version":"3.41.2"},"reference-count":14,"publisher":"Oxford University Press (OUP)","issue":"12","license":[{"start":{"date-parts":[[2022,12,31]],"date-time":"2022-12-31T00:00:00Z","timestamp":1672444800000},"content-version":"vor","delay-in-days":30,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2022,12,1]]},"abstract":"<jats:title>Abstract<\/jats:title><jats:p>Persistent Mullerian Duct Syndrome (PMDS) is a rare disorder of defective sexual development in males. It is characterized by aberrant synthesis or inadequate action of Mullerian inhibiting factor resulting in derivatives of Mullerian duct, i.e. uterus, fallopian tube and upper vagina, to persist in a phenotypic male with 46XY karyotype. Here, we report a 19-year-old male with bilateral undescended testes. Further evaluation revealed that the patient had both his testes placed intra-abdominally along with a rudimentary uterus.<\/jats:p>","DOI":"10.1093\/jscr\/rjac596","type":"journal-article","created":{"date-parts":[[2022,12,31]],"date-time":"2022-12-31T08:56:02Z","timestamp":1672476962000},"source":"Crossref","is-referenced-by-count":0,"title":["A rare form of male pseudohermaphroditism\u2014Persistent Mullerian Duct Syndrome"],"prefix":"10.1093","volume":"2022","author":[{"given":"Raazia","family":"Ramzan","sequence":"first","affiliation":[{"name":"Dow University of Health Sciences , Karachi 74200 , Pakistan"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Naveed Ali","family":"Khan","sequence":"additional","affiliation":[{"name":"Dow University of Health Sciences , Karachi 74200 , Pakistan"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Abdul","family":"Khalique","sequence":"additional","affiliation":[{"name":"Dow University of Health Sciences , Karachi 74200 , Pakistan"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Munira Abdul","family":"Aziz","sequence":"additional","affiliation":[{"name":"Dow University of Health Sciences , Karachi 74200 , Pakistan"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"286","published-online":{"date-parts":[[2022,12,30]]},"reference":[{"key":"2022123108112713200_ref1","first-page":"231","article-title":"Hernia uteri inguinalis bein Manne","volume":"83","author":"Nilson","year":"1939","journal-title":"Acta Chir Scand"},{"key":"2022123108112713200_ref2","doi-asserted-by":"crossref","first-page":"1","DOI":"10.1155\/2022\/2643833","article-title":"Persistent M\u00fcllerian Duct Syndrome: understanding the challenges","volume":"2022","author":"Chua","year":"2022","journal-title":"Case Rep Urol"},{"key":"2022123108112713200_ref3","first-page":"162","article-title":"Persistent Mullerian Duct Syndrome with transverse testicular ectopia: rare 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Rep"},{"key":"2022123108112713200_ref10","doi-asserted-by":"crossref","first-page":"1","DOI":"10.1155\/2013\/674105","article-title":"Anti-m\u00fcllerian hormone: a valuable addition to the toolbox of the pediatric endocrinologist","volume":"2013","author":"Josso","year":"2013","journal-title":"Int J Endocrinol"},{"key":"2022123108112713200_ref11","first-page":"PD28","article-title":"A rare case report of inguinal hernia with Persistent Mullerian Duct and Klinefelter Syndrome","volume":"10","author":"Dadheech","year":"2016","journal-title":"J Clin Diagn Res"},{"key":"2022123108112713200_ref12","doi-asserted-by":"crossref","first-page":"468","DOI":"10.1210\/er.2006-0005","article-title":"Germ cell tumors in the intersex gonad: old paths, new directions, moving frontiers","volume":"27","author":"Cools","year":"2006","journal-title":"Endocr Rev"},{"key":"2022123108112713200_ref13","doi-asserted-by":"crossref","first-page":"298","DOI":"10.1016\/j.ijscr.2020.10.113","article-title":"Female 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