{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,10,8]],"date-time":"2025-10-08T00:32:20Z","timestamp":1759883540413,"version":"build-2065373602"},"reference-count":11,"publisher":"Oxford University Press (OUP)","issue":"10","license":[{"start":{"date-parts":[[2025,10,7]],"date-time":"2025-10-07T00:00:00Z","timestamp":1759795200000},"content-version":"vor","delay-in-days":7,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2025,9,30]]},"abstract":"<jats:title>Abstract<\/jats:title>\n               <jats:p>Mayer-Rokitansky-K\u00fcster-Hauser (MRKH) syndrome is a reproductive tract malformation occurring in ~1 in 5000 female births. It is characterized by congenital agenesis or marked hypoplasia of the Mullerian ducts derivative structures. About 3% of MRKH patients have a functioning uterus. A 12-year-old otherwise healthy female presented with persistent cyclic severe right lower quadrant pain. She was found to have MRKH syndrome with a right-sided functioning uterus and hematometra and ipsilateral hematosalpinx. She subsequently underwent diagnostic cystoscopy, vaginoscopy, and pelvic laparoscopy. Laparoscopic drainage of the hematometra and hematosalpinx, and hysterostomy catheter placement and uterine fixation to anterior abdominal wall were performed. Symptoms fully resolved post-operatively. A computed tomography scan 2 weeks later demonstrated resolution of the hematometra and significant improvement in the hematosalpinx. MRKH syndrome with a functioning uterus may present as cyclic abdominal pain in adolescent female patients. Laparoscopic uterine drain placement is a management option.<\/jats:p>","DOI":"10.1093\/jscr\/rjaf797","type":"journal-article","created":{"date-parts":[[2025,10,7]],"date-time":"2025-10-07T18:16:38Z","timestamp":1759860998000},"source":"Crossref","is-referenced-by-count":0,"title":["Mayer-Rokitansky-K\u00fcster-Hauser syndrome complicated by hematometra and hematosalpinx treated with laparoscopic uterine drain placement: a case report"],"prefix":"10.1093","volume":"2025","author":[{"given":"Uma V","family":"Mahajan","sequence":"first","affiliation":[{"name":"Department of General Surgery, Division of Pediatric Surgery, State University of New York , 445 Lenox Road, Brooklyn, NY 11226 ,","place":["United States"]}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Marla","family":"Sacks","sequence":"additional","affiliation":[{"name":"Department of General Surgery, Division of Pediatric Surgery, State University of New York , 445 Lenox Road, Brooklyn, NY 11226 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T","family":"Velcek","sequence":"additional","affiliation":[{"name":"Department of General Surgery, Division of Pediatric Surgery, State University of New York , 445 Lenox Road, Brooklyn, NY 11226 ,","place":["United States"]}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"286","published-online":{"date-parts":[[2025,10,7]]},"reference":[{"key":"2025100714124191400_ref1","doi-asserted-by":"publisher","first-page":"362","DOI":"10.1016\/j.jpag.2014.07.019","article-title":"Typical and atypical associated findings in a group of 346 patients with Mayer-Rokitansky-Kuester-Hauser syndrome","volume":"28","author":"Rall","year":"2015","journal-title":"J Pediatr Adolesc Gynecol"},{"key":"2025100714124191400_ref2","doi-asserted-by":"publisher","first-page":"2384","DOI":"10.1093\/humrep\/dew220","article-title":"Prevalence and patient characteristics of Mayer\u2013Rokitansky\u2013K\u00fcster\u2013Hauser syndrome: a nationwide registry-based 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