{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,8,24]],"date-time":"2025-08-24T01:40:18Z","timestamp":1755999618171,"version":"3.41.2"},"reference-count":10,"publisher":"Oxford University Press (OUP)","issue":"1","license":[{"start":{"date-parts":[[2020,1,14]],"date-time":"2020-01-14T00:00:00Z","timestamp":1578960000000},"content-version":"vor","delay-in-days":13,"URL":"http:\/\/creativecommons.org\/licenses\/by-nc\/4.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2020,1,1]]},"abstract":"<jats:title>Abstract<\/jats:title>\n               <jats:p>Mucopolysaccharidoses are a group of rare lysosomal storage diseases caused by a deficiency of enzymes, which breakdown glycosaminoglycans, with consequent dysfunction of affected tissues. Mandibular coronoid hyperplasia, with associated trismus, has been recently described as a feature of the craniofacial abnormalities seen in these patients. However, the details of the surgical and post-operative management of these patients have not been previously documented. This case describes the successful management of severe trismus from coronoid process hyperplasia in a 14-year-old male, utilising an extra-oral approach for bilateral coronoidectomies and removal of exophytic zygomatic bone, followed by immediate and long-term physiotherapy. An improvement of mandibular opening from 8 to 45\u00a0mm has been maintained at 18\u00a0months post operation.<\/jats:p>","DOI":"10.1093\/jscr\/rjz388","type":"journal-article","created":{"date-parts":[[2019,12,6]],"date-time":"2019-12-06T12:34:37Z","timestamp":1575635677000},"source":"Crossref","is-referenced-by-count":7,"title":["Successful management of severe coronoid process hyperplasia in a patient with mucopolysaccharidosis VI: a case report"],"prefix":"10.1093","volume":"2020","author":[{"given":"Darius","family":"Khadembaschi","sequence":"first","affiliation":[{"name":"Faculty of Medicine, University of Queensland, St Lucia, Brisbane, Queensland, Australia"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"John","family":"Arvier","sequence":"additional","affiliation":[{"name":"Department of Oral and Maxillofacial Surgery, Queensland Children\u2019s Hospital, South Brisbane, Brisbane, Queensland, Australia"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Nicholas","family":"Beech","sequence":"additional","affiliation":[{"name":"Department of Oral and Maxillofacial Surgery, Queensland Children\u2019s Hospital, South Brisbane, Brisbane, Queensland, Australia"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"David","family":"Dolan","sequence":"additional","affiliation":[{"name":"Department of Anaesthetics, Queensland Children\u2019s Hospital, South Brisbane, Queensland, Australia"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Jim","family":"McGill","sequence":"additional","affiliation":[{"name":"Department of Metabolic Medicine, Queensland Children\u2019s Hospital, South Brisbane, Queensland, 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