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Maple syrup urine disease pathophysiology and treatment recommendations are reviewed.<\/jats:p>","DOI":"10.1093\/milmed\/usaa402","type":"journal-article","created":{"date-parts":[[2020,12,7]],"date-time":"2020-12-07T04:06:27Z","timestamp":1607313987000},"page":"e1037-e1039","source":"Crossref","is-referenced-by-count":0,"title":["Unusual Case of Acute Decompensated Maple Syrup Urine Disease in the Emergency Department"],"prefix":"10.1093","volume":"186","author":[{"ORCID":"https:\/\/orcid.org\/0000-0003-4238-6856","authenticated-orcid":false,"suffix":"MD","given":"Michael R","family":"Tobin","sequence":"first","affiliation":[{"name":"Department of Emergency Medicine, Resident Physician, Madigan Army Medical Center, Joint Base Lewis-McChord, WA, 98431, USA"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Justin","family":"Grisham","sequence":"additional","affiliation":[{"name":"Dept. of Emergency Medicine, Staff Physician, Madigan Army Medical Center, Joint Base Lewis-McChord, WA, USA"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Andrew","family":"Brigg","sequence":"additional","affiliation":[{"name":"Dept. of Emergency Medicine, Staff Physician, Madigan Army Medical Center, Joint Base Lewis-McChord, WA, USA"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Bradley","family":"Kinder","sequence":"additional","affiliation":[{"name":"Dept. of Emergency Medicine, Staff Physician, Madigan Army Medical Center, Joint Base Lewis-McChord, WA, USA"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"286","published-online":{"date-parts":[[2021,8,28]]},"reference":[{"key":"2021082810405064700_R1","first-page":"723","article-title":"a clinical approach. 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