{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,6,8]],"date-time":"2026-06-08T19:21:57Z","timestamp":1780946517874,"version":"3.54.1"},"reference-count":85,"publisher":"Oxford University Press (OUP)","issue":"2","license":[{"start":{"date-parts":[[2022,7,5]],"date-time":"2022-07-05T00:00:00Z","timestamp":1656979200000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by-nc\/4.0\/"}],"funder":[{"name":"Health and Labour Sciences Research"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2023,3,2]]},"abstract":"<jats:title>ABSTRACT<\/jats:title><jats:p>Recent advances in the management and understanding of immunoglobulin (Ig)G4-related kidney disease (RKD) have emphasized the importance of urgent treatment in IgG4-related tubulointerstitial nephritis. On the other hand, to avoid long-term glucocorticoid toxicity, strategies for early withdrawal of steroids or combination of immunosuppressants, such as rituximab, and the minimum dose of steroids have been pursued. However, disease recurrence after reducing or stopping steroid therapy hampers early withdrawal of glucocorticoid maintenance therapy. In addition, knowledge has accumulated in diagnostic approaches including differential diagnosis of anti-neutrophil cytoplasmic antibodies-associated vasculitis, idiopathic multicentric Castleman\u2019s disease, and Rosai\u2013Dorfman disease with kidney lesion, which leads to earlier and precise diagnosis of IgG4-RKD. This review summarizes recent progress in the differential diagnosis of IgG4-RKD and related treatment strategies and recent topics of hypocomplementaemia, membranous glomerulonephritis, and IgG4-related pyelitis and periureteral lesion.<\/jats:p>","DOI":"10.1093\/mr\/roac065","type":"journal-article","created":{"date-parts":[[2022,7,5]],"date-time":"2022-07-05T07:26:53Z","timestamp":1657006013000},"page":"242-251","source":"Crossref","is-referenced-by-count":25,"title":["Recent advances in IgG4-related kidney disease"],"prefix":"10.1093","volume":"33","author":[{"given":"Mitsuhiro","family":"Kawano","sequence":"first","affiliation":[{"name":"Department of Rheumatology, Graduate School of Medical Science, Kanazawa University , Kanazawa, Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Takako","family":"Saeki","sequence":"additional","affiliation":[{"name":"Department of Internal Medicine, Nagaoka Red Cross Hospital , Nagaoka, Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Yoshifumi","family":"Ubara","sequence":"additional","affiliation":[{"name":"Department of Nephrology and Rheumatology, Toranomon Hospital , Kawasaki, Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Shoko","family":"Matsui","sequence":"additional","affiliation":[{"name":"Health Administration Center, University of Toyama , Toyama, Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"286","published-online":{"date-parts":[[2022,7,5]]},"reference":[{"key":"2023030304341291800_","doi-asserted-by":"crossref","first-page":"231","DOI":"10.1080\/14397595.2018.1554321","article-title":"IgG4-related kidney disease and retroperitoneal fibrosis: an update","volume":"29","author":"Kawano","year":"2019","journal-title":"Mod Rheumatol"},{"key":"2023030304341291800_","doi-asserted-by":"crossref","first-page":"615","DOI":"10.1007\/s10157-011-0521-2","article-title":"Proposal for diagnostic criteria for IgG4-related kidney disease","volume":"15","author":"Kawano","year":"2011","journal-title":"Clin Exp Nephrol"},{"key":"2023030304341291800_","doi-asserted-by":"crossref","first-page":"599","DOI":"10.1038\/nrneph.2015.95","article-title":"IgG4-related disease and the kidney","volume":"11","author":"Cortazar","year":"2015","journal-title":"Nat Rev Nephrol"},{"key":"2023030304341291800_","doi-asserted-by":"crossref","DOI":"10.1186\/s13075-017-1467-x","article-title":"M. 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