{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,7,11]],"date-time":"2026-07-11T23:01:55Z","timestamp":1783810915861,"version":"3.55.0"},"reference-count":100,"publisher":"Oxford University Press (OUP)","issue":"1","license":[{"start":{"date-parts":[[2023,11,8]],"date-time":"2023-11-08T00:00:00Z","timestamp":1699401600000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by-nc\/4.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2023,12,29]]},"abstract":"<jats:title>ABSTRACT<\/jats:title>\n               <jats:p>Coronary periarteritis is a dangerous manifestation of IgG4-related disease, because it forms coronary artery aneurysms, which may cause sudden cardiac death. We report the case of a 78-year-old woman with IgG4-related coronary periarteritis and a coronary aneurysm, which showed progressive enlargement despite maintenance therapy for Type 1 autoimmune pancreatitis. This case was unique, in that coronary periarteritis was the only active lesion that recurred. Low-dose glucocorticoids suppressed the progression of periarterial lesions but led to rapid thinning of the aneurysmal wall and an increase in the size of mural thrombi, which pose a risk of myocardial infarction. Our systematic literature review including 98 cases of 86 articles was performed to examine its treatment strategies and complications. Among the cases in which the effect of immunosuppressive therapy could be followed radiologically, 33 of 37 (89.1%) cases showed improvement in wall thickening\/periarterial soft tissue, while 6 of 13 (46.2%) showed worsening increase in the outer diameter of the coronary aneurysms. We propose a draft treatment algorithm and suggest that immunosuppressive therapy for IgG4-related coronary periarteritis with coronary aneurysms should be conducted only after the therapeutic benefit has been determined to outweigh the risks. Because coronary periarteritis can occur without other organ involvement, as in our case, all cases of IgG4-related disease require careful monitoring of coronary artery lesions.<\/jats:p>","DOI":"10.1093\/mrcr\/rxad065","type":"journal-article","created":{"date-parts":[[2023,11,10]],"date-time":"2023-11-10T08:58:01Z","timestamp":1699606681000},"page":"182-194","source":"Crossref","is-referenced-by-count":8,"title":["Solitary recurrence of\u00a0IgG4-related giant coronary aneurysm: Case report and\u00a0review of\u00a0the literature focusing on\u00a0treatment strategies and\u00a0complications"],"prefix":"10.1093","volume":"8","author":[{"given":"Hiroyuki","family":"Kawahara","sequence":"first","affiliation":[{"name":"Department of Rheumatology, Kanazawa University Graduate School of Medical Sciences , Kanazawa, Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Ichiro","family":"Mizushima","sequence":"additional","affiliation":[{"name":"Department of Rheumatology, Kanazawa University Graduate School of Medical Sciences , Kanazawa, Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Yasushi","family":"Matsumoto","sequence":"additional","affiliation":[{"name":"Department of Cardiovascular Surgery, National Hospital Organization Kanazawa Medical Center , Kanazawa, Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Kenji","family":"Sakata","sequence":"additional","affiliation":[{"name":"Department of Cardiovascular Medicine, Kanazawa University Graduate School of Medical Sciences , Kanazawa, Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Masayuki","family":"Takamura","sequence":"additional","affiliation":[{"name":"Department of Cardiovascular Medicine, Kanazawa University Graduate School of Medical Sciences , Kanazawa, Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Dai","family":"Inoue","sequence":"additional","affiliation":[{"name":"Department of Radiology, Kanazawa University Graduate School of Medical Sciences , Kanazawa, Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Satomi","family":"Kasashima","sequence":"additional","affiliation":[{"name":"Department of Clinical Laboratory Science, Kanazawa University , Kanazawa, Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-4613-2116","authenticated-orcid":false,"given":"Mitsuhiro","family":"Kawano","sequence":"additional","affiliation":[{"name":"Department of Rheumatology, Kanazawa University Graduate School of Medical Sciences , Kanazawa, Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"286","published-online":{"date-parts":[[2023,11,8]]},"reference":[{"key":"2023122911394474900_R1","article-title":"Advances in\u00a0the diagnosis and\u00a0management of\u00a0IgG4 related 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