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However, resistant inflammatory EBA with widespread mucosal involvement remains a rare entity given its low prevalence. It commonly represents a great burden for the patient\u2019s quality of life with most cases being resistant to different therapeutic modalities. We present a case of resistant inflammatory EBA with esophageal strictures that improved after therapy with intravenous immunoglobulin and rituximab.<\/jats:p>","DOI":"10.1093\/omcr\/omab010","type":"journal-article","created":{"date-parts":[[2021,4,28]],"date-time":"2021-04-28T22:52:02Z","timestamp":1619650322000},"source":"Crossref","is-referenced-by-count":1,"title":["Epidermolysis bullosa acquisita: an uncommon cause of esophageal stricture"],"prefix":"10.1093","volume":"2021","author":[{"ORCID":"https:\/\/orcid.org\/0000-0002-0386-5742","authenticated-orcid":false,"given":"Carlos","family":"Figueredo","sequence":"first","affiliation":[{"name":"Department of Internal Medicine, Montefiore Medical Center, Bronx, NY, USA"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Konstantin","family":"Boroda","sequence":"additional","affiliation":[{"name":"Division of Gastroenterology and Hepatology, Montefiore Medical Center, Bronx, NY, 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