{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,7,30]],"date-time":"2025-07-30T12:14:05Z","timestamp":1753877645970,"version":"3.41.2"},"reference-count":10,"publisher":"Oxford University Press (OUP)","issue":"12","license":[{"start":{"date-parts":[[2023,12,21]],"date-time":"2023-12-21T00:00:00Z","timestamp":1703116800000},"content-version":"vor","delay-in-days":20,"URL":"https:\/\/creativecommons.org\/licenses\/by-nc\/4.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2023,12,1]]},"abstract":"<jats:title>Abstract<\/jats:title>\n               <jats:p>Pantothenate kinase-associated neurodegeneration (or previously known as Hallervorden-Spatz syndrome) is a very rare disorder that typically manifests in a child with neurological signs such as gait difficulties, dysarthria, and hyperreflexia, associated potentially with psychiatric symptoms such as cognitive decline. It demonstrates on MRI the typical \u2018eye of the tiger\u2019 appearance, which is due to gliosis and accumulation of iron in the globi pallidi. Other differentials can mimic this appearance on MRI, it is therefore important to search for the involvement of other basal ganglia nuclei and the cerebral cortex, and also to consider the clinical and biological context.<\/jats:p>","DOI":"10.1093\/omcr\/omad134","type":"journal-article","created":{"date-parts":[[2023,12,21]],"date-time":"2023-12-21T22:42:40Z","timestamp":1703198560000},"source":"Crossref","is-referenced-by-count":0,"title":["Ataxic gait and dysarthria in a child: pantothenate kinase-associated neurodegeneration as a diagnosis"],"prefix":"10.1093","volume":"2023","author":[{"ORCID":"https:\/\/orcid.org\/0000-0003-4841-0423","authenticated-orcid":false,"given":"Amine","family":"Naggar","sequence":"first","affiliation":[{"name":"Mohammed V University Radiology Department, Children\u2019s Hospital of Rabat, , Rabat, Morocco"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-9766-4887","authenticated-orcid":false,"given":"Khadija","family":"Laasri","sequence":"additional","affiliation":[{"name":"Mohammed V University Radiology Department, Children\u2019s Hospital of Rabat, , Rabat, Morocco"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Mohamed","family":"Fadil","sequence":"additional","affiliation":[{"name":"Mohammed V University Radiology Department, Children\u2019s Hospital of Rabat, , Rabat, Morocco"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Nazik","family":"Allali","sequence":"additional","affiliation":[{"name":"Mohammed V University Radiology Department, Children\u2019s Hospital of Rabat, , Rabat, Morocco"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Siham","family":"El Haddad","sequence":"additional","affiliation":[{"name":"Mohammed V University Radiology Department, Children\u2019s 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