{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,4]],"date-time":"2026-10-04T12:54:03Z","timestamp":1791118443744,"version":"4.1.0"},"reference-count":10,"publisher":"Oxford University Press (OUP)","issue":"10","license":[{"start":{"date-parts":[[2026,10,4]],"date-time":"2026-10-04T00:00:00Z","timestamp":1791072000000},"content-version":"vor","delay-in-days":3,"URL":"https:\/\/creativecommons.org\/licenses\/by-nc\/4.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2026,10,4]]},"abstract":"<jats:title>Abstract<\/jats:title>\n                  <jats:p>Background: Pleuropulmonary blastoma (PPB) is a rare and aggressive pediatric thoracic malignancy within the DICER1 syndrome spectrum. Despite well-established multimodal treatment based on surgery and chemotherapy, evidence guiding the use of adjuvant radiotherapy remains scarce, given the rarity of this tumor. Case report: A 3-year-old girl with type II PPB, presenting with recurrent pyopneumothorax, achieved a 76% tumor reduction after seven cycles of IVADo chemotherapy, allowing incomplete surgical resection with residual viable tumor. Adjuvant VMAT (45\u00a0Gy\/25 fractions) achieved excellent target coverage with organ sparing and was well tolerated (grade 2 radiodermatitis only), and the patient remained disease-free at 9\u00a0months. Conclusion: This case highlights the feasibility of modern VMAT-based adjuvant radiotherapy for incompletely resected type II PPB and illustrates how advanced treatment planning can optimize local control while limiting radiation exposure to critical organs.<\/jats:p>","DOI":"10.1093\/omcr\/omag183","type":"journal-article","created":{"date-parts":[[2026,9,17]],"date-time":"2026-09-17T19:20:06Z","timestamp":1789672806000},"source":"Crossref","is-referenced-by-count":0,"title":["Adjuvant volumetric modulated arc therapy for incompletely resected type II pleuropulmonary blastoma: a case report"],"prefix":"10.1093","volume":"2026","author":[{"ORCID":"https:\/\/orcid.org\/0009-0006-2506-7043","authenticated-orcid":false,"given":"Salma","family":"Ichou","sequence":"first","affiliation":[{"name":"Department of Radiation Therapy, National Institute of Oncology Sidi Mohamed Ben Abdellah , Avenue Allal El Fassi, Hay Riad, Rabat 10000 ,","place":["Morocco"]},{"name":"Faculty of Medicine and Pharmacy of Rabat, Mohammed V University , Avenue Mohammed Belarbi El Alaoui, Souissi, Rabat Institut, BP 6203, Rabat 10000 ,","place":["Morocco"]},{"name":"University Mohammed V , Avenue des Nations Unies, Agdal, BP 8007 N.U., Rabat 10000 ,","place":["Morocco"]}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-9283-9908","authenticated-orcid":false,"given":"Ihsane","family":"Skitioui","sequence":"additional","affiliation":[{"name":"Department of Radiation Therapy, National Institute of Oncology Sidi Mohamed Ben Abdellah , Avenue Allal El Fassi, Hay Riad, Rabat 10000 , Morocco"},{"name":"Faculty of Medicine and Pharmacy of Rabat, Mohammed V University , Avenue Mohammed Belarbi El Alaoui, Souissi, Rabat Institut, BP 6203, Rabat 10000 ,","place":["Morocco"]},{"name":"University Mohammed V , Avenue des Nations Unies, Agdal, BP 8007 N.U., Rabat 10000 ,","place":["Morocco"]}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Amine","family":"Lachgar","sequence":"additional","affiliation":[{"name":"Department of Radiation Therapy, National Institute of Oncology Sidi Mohamed Ben Abdellah , Avenue Allal El Fassi, Hay Riad, Rabat 10000 , Morocco"},{"name":"Faculty of Medicine and Pharmacy of Rabat, Mohammed V University , Avenue Mohammed Belarbi El Alaoui, Souissi, Rabat Institut, BP 6203, Rabat 10000 ,","place":["Morocco"]},{"name":"University Mohammed V , Avenue des Nations Unies, Agdal, BP 8007 N.U., Rabat 10000 ,","place":["Morocco"]}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Karima","family":"Nouni","sequence":"additional","affiliation":[{"name":"Department of Radiation Therapy, National Institute of Oncology Sidi Mohamed Ben Abdellah , Avenue Allal El Fassi, Hay Riad, Rabat 10000 , Morocco"},{"name":"Faculty of Medicine and Pharmacy of Rabat, Mohammed V University , Avenue Mohammed Belarbi El Alaoui, Souissi, Rabat Institut, BP 6203, Rabat 10000 ,","place":["Morocco"]},{"name":"University Mohammed V , Avenue des Nations Unies, Agdal, BP 8007 N.U., Rabat 10000 ,","place":["Morocco"]}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Hanan","family":"El Kacemi","sequence":"additional","affiliation":[{"name":"Department of Radiation Therapy, National Institute of Oncology Sidi Mohamed Ben Abdellah , Avenue Allal El Fassi, Hay Riad, Rabat 10000 , Morocco"},{"name":"Faculty of Medicine and Pharmacy of Rabat, Mohammed V University , Avenue Mohammed Belarbi El Alaoui, Souissi, Rabat Institut, BP 6203, Rabat 10000 ,","place":["Morocco"]},{"name":"University Mohammed V , Avenue des Nations Unies, Agdal, BP 8007 N.U., Rabat 10000 ,","place":["Morocco"]}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Tayeb","family":"Kebdani","sequence":"additional","affiliation":[{"name":"Department of Radiation Therapy, National Institute of Oncology Sidi Mohamed Ben 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