{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,8,28]],"date-time":"2025-08-28T12:46:48Z","timestamp":1756385208877,"version":"3.41.2"},"reference-count":10,"publisher":"Oxford University Press (OUP)","issue":"6","license":[{"start":{"date-parts":[[2019,7,1]],"date-time":"2019-07-01T00:00:00Z","timestamp":1561939200000},"content-version":"vor","delay-in-days":30,"URL":"http:\/\/creativecommons.org\/licenses\/by-nc\/4.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2019,6,1]]},"abstract":"<jats:title>Abstract<\/jats:title>\n               <jats:p>Supravalvar mitral ring is a rare congenital abnormality characterized by a ridge of connective tissue located above the mitral valve. It is a cause of congenital mitral stenosis typically presenting in childhood and usually associated with other cardiac abnormalities. We report the rare case of a 24-year-old male presenting with an isolated aneurysmal supravalvar mitral ring. He presented at the emergency room with a 2-week history of worsening heart failure symptoms and antecedent effort intolerance of 4\u00a0years duration. He was referred from a primary care facility with an echo diagnosis of cor-triatriatum. Echocardiography done at our centre revealed an isolated aneurysmal supravalvar mitral ring of the intramitral variant. This report highlights the unusual isolated presentation of a supravalvar mitral ring in a young adult and the need to carefully differentiate it from cor-triatriatum, a possible close mimic.<\/jats:p>","DOI":"10.1093\/omcr\/omz050","type":"journal-article","created":{"date-parts":[[2019,7,1]],"date-time":"2019-07-01T05:02:41Z","timestamp":1561957361000},"source":"Crossref","is-referenced-by-count":2,"title":["A rare case of an isolated aneurysmal supravalvar mitral ring in a young Nigerian adult: a cor-triatriatum mimic"],"prefix":"10.1093","volume":"2019","author":[{"ORCID":"https:\/\/orcid.org\/0000-0002-0760-8014","authenticated-orcid":false,"given":"Oyewole A","family":"Kushimo","sequence":"first","affiliation":[{"name":"Cardiology Unit, Department of Medicine, Lagos University Teaching Hospital, PMB, Lagos, Nigeria"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Ogochukwu","family":"Sokunbi","sequence":"additional","affiliation":[{"name":"Department of Paediatrics, Lagos University Teaching Hospital, PMB, Lagos, Nigeria"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Michael","family":"Akinkunmi","sequence":"additional","affiliation":[{"name":"Cardiology Unit, Department of Medicine, Lagos University Teaching Hospital, PMB, Lagos, Nigeria"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Yeside O","family":"Akinbolagbe","sequence":"additional","affiliation":[{"name":"Department of Paediatrics, Lagos University Teaching Hospital, PMB, Lagos, Nigeria"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"286","published-online":{"date-parts":[[2019,6,24]]},"reference":[{"key":"2019070105023921000_ref1","doi-asserted-by":"crossref","first-page":"70","DOI":"10.1017\/S1047951108003399","article-title":"An analysis of 24 autopsied cases with supramitral rings","volume":"19","author":"Vaideeswar","year":"2009","journal-title":"Cardiol Young"},{"key":"2019070105023921000_ref2","doi-asserted-by":"crossref","first-page":"538","DOI":"10.1016\/j.jtcvs.2008.08.023","article-title":"Congenital supravalvar mitral ring: an underestimated anomaly","volume":"137","author":"Toscano","year":"2009","journal-title":"J Thorac Cardiovasc Surg"},{"key":"2019070105023921000_ref3","doi-asserted-by":"crossref","first-page":"592","DOI":"10.1016\/0002-9149(78)90629-X","article-title":"Anatomic types of congenital mitral stenosis: report of 49 autopsy cases with consideration of diagnosis and surgical implications","volume":"42","author":"Ruckman","year":"1978","journal-title":"Am J Cardiol"},{"key":"2019070105023921000_ref4","doi-asserted-by":"crossref","first-page":"714","DOI":"10.1016\/0002-9149(63)90098-5","article-title":"The developmental complex of \u201cparachute mitral valve,\u201d supravalvular ring of left atrium, subaortic stenosis, and coarctation of aorta","volume":"11","author":"Shone","year":"1963","journal-title":"Am J Cardiol"},{"key":"2019070105023921000_ref5","first-page":"E20","article-title":"An isolated supramitral ring detected in an adult patient","volume":"9","author":"Baysan","year":"2009","journal-title":"Anadolu Kardiyol Derg AKD Anatol J Cardiol"},{"key":"2019070105023921000_ref6","doi-asserted-by":"crossref","first-page":"25","DOI":"10.1378\/chest.65.1.25","article-title":"Isolated supravalvular stenosing ring of left atrium: diagnosis before operation and successful surgical treatment","volume":"65","author":"Chung","year":"1974","journal-title":"Chest"},{"key":"2019070105023921000_ref7","first-page":"901","volume-title":"The Practice of Clinical Echocardiography","author":"Otto","year":"2012"},{"key":"2019070105023921000_ref8","doi-asserted-by":"crossref","first-page":"997","DOI":"10.1016\/j.athoracsur.2005.06.079","article-title":"Supramitral ring: good prognosis in a subset of patients with congenital mitral stenosis","volume":"81","author":"Collison","year":"2006","journal-title":"Ann Thorac Surg"},{"key":"2019070105023921000_ref9","doi-asserted-by":"crossref","first-page":"1048","DOI":"10.1111\/echo.12867","article-title":"Three-dimensional echocardiography enhances diagnostic accuracy of supramitral ring","volume":"32","author":"Jone","year":"2015","journal-title":"Echocardiography"},{"key":"2019070105023921000_ref10","doi-asserted-by":"crossref","first-page":"61","DOI":"10.15420\/ecr.2010.6.2.61","article-title":"3D Echocardiography in mitral valve heart disease \u2013 is it the new gold standard","volume":"6","author":"Rana","year":"2010","journal-title":"Eur Cardiol"}],"container-title":["Oxford Medical Case Reports"],"original-title":[],"language":"en","link":[{"URL":"http:\/\/academic.oup.com\/omcr\/article-pdf\/2019\/6\/omz050\/28854323\/omz050.pdf","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2019,7,1]],"date-time":"2019-07-01T05:02:45Z","timestamp":1561957365000},"score":1,"resource":{"primary":{"URL":"https:\/\/academic.oup.com\/omcr\/article\/doi\/10.1093\/omcr\/omz050\/5521854"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2019,6,1]]},"references-count":10,"journal-issue":{"issue":"6","published-online":{"date-parts":[[2019,6,24]]},"published-print":{"date-parts":[[2019,6,1]]}},"URL":"https:\/\/doi.org\/10.1093\/omcr\/omz050","relation":{},"ISSN":["2053-8855"],"issn-type":[{"type":"electronic","value":"2053-8855"}],"subject":[],"published-other":{"date-parts":[[2019,6]]},"published":{"date-parts":[[2019,6,1]]},"article-number":"omz050"}}