{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,7]],"date-time":"2026-08-07T16:15:18Z","timestamp":1786119318084,"version":"build-2736575974"},"reference-count":43,"publisher":"Ovid Technologies (Wolters Kluwer Health)","issue":"6","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2009,11]]},"DOI":"10.1097\/bor.0b013e328331927e","type":"journal-article","created":{"date-parts":[[2009,10,1]],"date-time":"2009-10-01T03:24:28Z","timestamp":1254367468000},"page":"575-580","source":"Crossref","is-referenced-by-count":46,"title":["Juvenile dermatomyositis: extramuscular manifestations and their management"],"prefix":"10.1097","volume":"21","author":[{"given":"Clodagh A","family":"Lowry","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Clarissa A","family":"Pilkington","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"276","reference":[{"key":"R1-2-20210128","doi-asserted-by":"crossref","first-page":"732","DOI":"10.1093\/rheumatology\/34.8.732","article-title":"The incidence of juvenile dermatomyositis: results from a nation-wide study","volume":"34","author":"Symmons","year":"1995","journal-title":"Br J Rheumatol"},{"key":"R2-2-20210128","doi-asserted-by":"crossref","first-page":"166","DOI":"10.1002\/art.21068","article-title":"History of infection before the onset of juvenile dermatomyositis: results from the National Institute of Arthritis and Musculoskeletal and Skin Diseases Research Registry","volume":"53","author":"Pachman","year":"2005","journal-title":"Arthritis Rheum"},{"key":"R3-2-20210128","doi-asserted-by":"crossref","first-page":"2201","DOI":"10.1016\/S0140-6736(08)60955-1","article-title":"Juvenile dermatomyositis and other idiopathic inflammatory myopathies of childhood","volume":"371","author":"Feldman","year":"2008","journal-title":"Lancet"},{"key":"R4-2-20210128","first-page":"2","article-title":"EM, Huber AM, Miller FW, Rider LC, for the International Myositis Assessment and Clinical Studies (IMACS) Group. Review of the classification and assessment of the cutaneous manifestations of the idiopathic inflammatory myopathies.","volume":"15","year":"2009","journal-title":"Dermatol Online J"},{"key":"R5-2-20210128","doi-asserted-by":"crossref","first-page":"1255","DOI":"10.1093\/rheumatology\/kel099","article-title":"The Juvenile Dermatomyositis National Registry and Repository (UK and Ireland): clinical characteristics of children recruited within the first 5 years","volume":"45","author":"McCann","year":"2006","journal-title":"Rheumatology"},{"key":"R6-2-20210128","doi-asserted-by":"crossref","first-page":"126","DOI":"10.1002\/art.1780250203","article-title":"Clinical and pathogenetic implications of histopathology in childhood polydermatomyositis","volume":"25","author":"Crowe","year":"1982","journal-title":"Arthritis Rheum"},{"key":"R7-2-20210128","doi-asserted-by":"crossref","first-page":"1353","DOI":"10.1177\/0883073808318544","article-title":"Juvenile dermatomyositis presenting with anasarca","volume":"23","author":"Saygi","year":"2008","journal-title":"J Child Neurol"},{"key":"R8-2-20210128","doi-asserted-by":"crossref","first-page":"942","DOI":"10.1067\/mpd.2001.113363","article-title":"Juvenile dermatomyositis presenting with anasarca: a possible indicator of severe disease activity","volume":"138","author":"Mitchell","year":"2001","journal-title":"J Pediatr"},{"key":"R9-2-20210128","doi-asserted-by":"crossref","first-page":"70","DOI":"10.1097\/MD.0b013e31816bc604","article-title":"Predictors of acquired lipodystrophy in juvenile-onset dermatomyositis and a gradient of severity","volume":"87","author":"Bingham","year":"2008","journal-title":"Medicine (Baltimore)"},{"key":"R10-2-20210128","doi-asserted-by":"crossref","first-page":"571","DOI":"10.1002\/art.23299","article-title":"Persistent association of nailfold capillaroscopy changes and skin involvement over thirty-six months with duration of untreated disease in patients with juvenile dermatomyositis","volume":"58","author":"Christen-Zaech","year":"2008","journal-title":"Arthritis Rheum"},{"key":"R11-2-20210128","doi-asserted-by":"crossref","first-page":"e21","DOI":"10.1056\/NEJMicm062850","article-title":"Gingival and periungual vasculopathy of juvenile dermatomyositis","volume":"360","author":"Rider","year":"2009","journal-title":"N Engl J Med"},{"key":"R12-2-20210128","doi-asserted-by":"crossref","first-page":"637","DOI":"10.1111\/j.1365-2133.2007.08055.x","article-title":"A systematic review of juvenile-onset clinically amyopathic dermatomyositis","volume":"157","author":"Germani","year":"2007","journal-title":"Br J Dermatol"},{"key":"R13-2-20210128","doi-asserted-by":"crossref","first-page":"413","DOI":"10.3109\/s10165-007-0610-y","article-title":"Juvenile dermatomyositis: clinical characteristics and the relatively high risk of interstitial lung disease","volume":"17","author":"Morinishi","year":"2007","journal-title":"Mod Rheumatol"},{"key":"R14-2-20210128","doi-asserted-by":"crossref","first-page":"226","DOI":"10.1016\/S0022-3476(80)80807-9","article-title":"Juvenile dermatomyositis clinical and immunological study","volume":"96","author":"Pachman","year":"1980","journal-title":"J Pediatr"},{"key":"R15-2-20210128","doi-asserted-by":"crossref","first-page":"1040","DOI":"10.1007\/s00296-006-0141-4","article-title":"Severe juvenile dermatomyositis: two patients complicated with extra musculocutaneous involvement","volume":"26","author":"Tosan","year":"2006","journal-title":"Rheumatol Int"},{"key":"R16-2-20210128","first-page":"S258","article-title":"Myositis specific autoantibodies (MSA) in children: a broadened spectrum of juvenile myositis [abstract]","volume":"36","author":"Rider","year":"1993","journal-title":"Arthritis Rheum"},{"key":"R17-2-20210128","doi-asserted-by":"crossref","first-page":"371","DOI":"10.1093\/rheumatology\/keg040","article-title":"Interstitial lung disease associated with juvenile dermatomyositis: clinical features and efficacy of cyclosporine A","volume":"42","author":"Kobayashi","year":"2003","journal-title":"Rheumatology (Oxford)"},{"key":"R18-2-20210128","first-page":"1424","article-title":"Cyclosporin A therapy in refractory juvenile dermatomyositis: Experience and long term follow up of 6 cases","volume":"23","author":"Zeller","year":"1996","journal-title":"J Rheumatol"},{"key":"R19-2-20210128","doi-asserted-by":"crossref","first-page":"179","DOI":"10.1007\/s00296-006-0191-7","article-title":"Juvenile dermatomyositis with a rare and remarkable complication: sinus bradycardia","volume":"27","author":"Karaca","year":"2006","journal-title":"Rheumatol Int"},{"key":"R20-2-20210128","doi-asserted-by":"crossref","first-page":"561","DOI":"10.1177\/000992289803700907","article-title":"Abdominal pain in a girl with juvenile dermatomyositis.","volume":"37","author":"Stefanski","year":"1998","journal-title":"Clin Pediatr"},{"key":"R21-2-20210128","doi-asserted-by":"crossref","first-page":"1011","DOI":"10.1259\/0007-1285-53-634-1011","article-title":"Pneumatosis intestinalis in dermatomyositis.","volume":"53","author":"Braunstein","year":"1980","journal-title":"Br J Radiol"},{"key":"R22-2-20210128","doi-asserted-by":"crossref","first-page":"1363","DOI":"10.1093\/rheumatology\/kem131","article-title":"Oropharyngeal dysphagia in juvenile dermatomyositis: an evaluation of videofluroscopy swallow study changes in relation to clinical symptoms and objective muscle scores","volume":"46","author":"Mc Cann","year":"2007","journal-title":"Rheumatology"},{"key":"R23-2-20210128","doi-asserted-by":"crossref","first-page":"1071","DOI":"10.1016\/S0031-3955(16)40054-4","article-title":"Juvenile dermatomyositis. Pathophysiology and disease expression.","volume":"42","author":"Pachman","year":"1995","journal-title":"Pediatr Clin North Am"},{"key":"R24-2-20210128","doi-asserted-by":"crossref","first-page":"541","DOI":"10.1002\/1529-0131(200003)43:3<541::AID-ANR9>3.0.CO;2-T","article-title":"Medium- and long-term functional outcomes in a multicenter cohort of children with juvenile dermatomyositis.","volume":"43","author":"Huber","year":"2000","journal-title":"Arthritis Rheum"},{"key":"R25-2-20210128","first-page":"119","article-title":"Calcinosis in JDM: pathogenesis and current therapies","volume":"1","author":"Rider","year":"2003","journal-title":"Pediatr Rheumatol Online J"},{"key":"R26-2-20210128","doi-asserted-by":"crossref","first-page":"397","DOI":"10.2214\/ajr.142.2.397","article-title":"Patterns of calcification in childhood dermatomyositis","volume":"142","author":"Blane","year":"1984","journal-title":"Am J Roentgenol"},{"key":"R27-2-20210128","doi-asserted-by":"crossref","first-page":"882","DOI":"10.1016\/S0022-3476(83)80706-9","article-title":"Childhood dermatomyositis: factors predicting functional outcome and development of dystrophic calcification","volume":"103","author":"Bowyer","year":"1983","journal-title":"J Pediatr"},{"key":"R28-2-20210128","doi-asserted-by":"crossref","first-page":"2368","DOI":"10.1002\/1529-0131(200010)43:10<2368::AID-ANR26>3.0.CO;2-8","article-title":"TNFalpha-308A allele in juvenile dermatomyositis: association with increased production of tumor necrosis factor alpha, disease duration, and pathologic calcifications","volume":"43","author":"Pachman","year":"2000","journal-title":"Arthritis Rheum"},{"key":"R29-2-20210128","doi-asserted-by":"crossref","first-page":"3345","DOI":"10.1002\/art.22158","article-title":"Composition of calcifications in children with juvenile dermatomyositis: association with chronic cutaneous inflammation","volume":"54","author":"Pachman","year":"2006","journal-title":"Arthritis Rheum"},{"key":"R30-2-20210128","doi-asserted-by":"crossref","first-page":"324","DOI":"10.1093\/rheumatology\/kem359","article-title":"Clinical associations of autoantibodies to a p155\/140 kDa doublet protein in juvenile dermatomyositis","volume":"47","author":"Gunawardena","year":"2008","journal-title":"Rheumatology (Oxford)"},{"key":"R31-2-20210128","doi-asserted-by":"crossref","first-page":"1807","DOI":"10.1002\/art.24547","article-title":"Autoantibodies to a 140-kd protein in juvenile dermatomyositis are associated with calcinosis","volume":"60","author":"Gunawardena","year":"2009","journal-title":"Arthritis Rheum"},{"key":"R32-2-20210128","doi-asserted-by":"crossref","first-page":"558","DOI":"10.1002\/art.21332","article-title":"Quantitative assessments of the effects of a single exercise session on muscles in juvenile dermatomyositis","volume":"53","author":"Maillard","year":"2005","journal-title":"Arthritis Rheum"},{"key":"R33-2-20210128","doi-asserted-by":"crossref","first-page":"222","DOI":"10.1002\/art.23341","article-title":"Pharmacokinetic study of oral prednisolone compared with intravenous methyl-prednisolone in patients with juvenile dermatomyositis","volume":"58","author":"Rouster-Stevens","year":"2008","journal-title":"Arthritis Rheum"},{"key":"R34-2-20210128","doi-asserted-by":"crossref","first-page":"3570","DOI":"10.1002\/art.21378","article-title":"The effectiveness of treating juvenile dermatomyositis with methotrexate and aggressively tapered corticosteroids","volume":"52","author":"Ramanan","year":"2005","journal-title":"Arthritis Rheum"},{"key":"R35-2-20210128","doi-asserted-by":"crossref","first-page":"505","DOI":"10.1067\/mjd.2002.122196","article-title":"Aggressive management of juvenile dermatomyositis results in improved outcome and decreased incidence of calcinosis","volume":"47","author":"Fisler","year":"2002","journal-title":"J Am Acad Dermatol"},{"key":"R37-2-20210128","doi-asserted-by":"crossref","first-page":"1255","DOI":"10.1093\/rheumatology\/kel099","article-title":"The Juvenile Dermatomyositis National Registry and Repository (UK and Ireland): clinical characteristics of children recruited within the first 5 yr","volume":"45","author":"McCann","year":"2006","journal-title":"Rheumatology (Oxford)"},{"key":"R38-2-20210128","doi-asserted-by":"crossref","first-page":"138","DOI":"10.1007\/s100670050032","article-title":"Efficacy of early treatment of severe juvenile dermatomyositis with intravenous methylprednisolone and methotrexate","volume":"19","author":"Al-Mayouf","year":"2000","journal-title":"Clin Rheumatol"},{"key":"R39-2-20210128","doi-asserted-by":"crossref","first-page":"877","DOI":"10.1093\/rheumatology\/ken074","article-title":"Effectiveness of infliximab in the treatment of refractory juvenile dermatomyositis with calcinosis","volume":"47","author":"Riley","year":"2008","journal-title":"Rheumatology (Oxford)"},{"key":"R41-2-20210128","doi-asserted-by":"crossref","first-page":"49","DOI":"10.1093\/rheumatology\/keg427","article-title":"International consensus outcome measures for patients with idiopathic inflammatory myopathies: development and initial validation of myositis activity and damage indices in patients with adult onset disease","volume":"43","author":"Isenberg","year":"2004","journal-title":"Rheumatology"},{"key":"R42-2-20210128","doi-asserted-by":"crossref","first-page":"4","DOI":"10.1002\/art.23248","article-title":"The provisional Paediatric Rheumatology International Trials Organisation\/American College of Rheumatology\/European League Against Rheumatism Disease activity core set for the evaluation of response to therapy in juvenile dermatomyositis: a prospective validation study","volume":"59","author":"Ruperto","year":"2008","journal-title":"Arthritis Rheum"},{"key":"R43-2-20210128","doi-asserted-by":"crossref","first-page":"7","DOI":"10.1002\/art.10924","article-title":"Disease activity score for children with juvenile dermatomyositis: reliability and validity evidence","volume":"49","author":"Bode","year":"2003","journal-title":"Arthritis Rheum"},{"key":"R44-2-20210128","doi-asserted-by":"crossref","first-page":"345","DOI":"10.1111\/j.1365-2133.2007.08342.x","article-title":"Development and validation of the Dermatomyositis Skin Severity Index","volume":"158","author":"Carroll","year":"2008","journal-title":"Br J Dermatol"},{"key":"R45-2-20210128","doi-asserted-by":"crossref","first-page":"214","DOI":"10.1002\/art.23340","article-title":"Preliminary validation and clinical meaning of the Cutaneous Assessment Tool (CAT) in juvenile dermatomyositis","volume":"59","author":"Huber","year":"2008","journal-title":"Arthritis Rheum"}],"container-title":["Current Opinion in Rheumatology"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/www.ovid.com\/10.1097\/BOR.0b013e328331927e","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2026,8,6]],"date-time":"2026-08-06T18:00:58Z","timestamp":1786039258000},"score":1,"resource":{"primary":{"URL":"https:\/\/www.ovid.com\/00002281-200911000-00002"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2009,11]]},"references-count":43,"journal-issue":{"issue":"6","published-print":{"date-parts":[[2009]]}},"URL":"https:\/\/doi.org\/10.1097\/bor.0b013e328331927e","relation":{},"ISSN":["1040-8711"],"issn-type":[{"value":"1040-8711","type":"print"}],"subject":[],"published":{"date-parts":[[2009,11]]}}}