{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2023,9,3]],"date-time":"2023-09-03T09:42:01Z","timestamp":1693734121257},"reference-count":23,"publisher":"Ovid Technologies (Wolters Kluwer Health)","issue":"2","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2020,12]]},"abstract":"<jats:title>Abstract<\/jats:title>\n          <jats:p>Typical distal symptoms in anti\u2013myelin-associated glycoprotein (anti-MAG) neuropathy are believed to be due to the binding of immunoglobulin M to distal nerve terminals. We describe the case of a 56-year-old man diagnosed with immunoglobulin M anti-MAG neuropathy in the setting of Waldenstr\u00f6m macroglobulinemia, which developed acute neurological worsening presenting as cauda equina syndrome. Lumbosacral magnetic resonance imaging revealed enlarged nerve roots with diffuse heterogeneous gadolinium enhancement. Treatment with steroids resulted in substantial clinical improvement. Increased recognition of atypical presentations may lead to improved characterization of anti-MAG neuropathy as a more widespread disease.<\/jats:p>","DOI":"10.1097\/cnd.0000000000000307","type":"journal-article","created":{"date-parts":[[2020,11,17]],"date-time":"2020-11-17T22:35:39Z","timestamp":1605652539000},"page":"109-113","source":"Crossref","is-referenced-by-count":0,"title":["Proximal Nerve Root Involvement in immunoglobulin M Anti\u2013Myelin-Associated Glycoprotein Neuropathy Presenting as Cauda Equina Syndrome"],"prefix":"10.1097","volume":"22","author":[{"given":"Marco","family":"Fernandes","sequence":"first","affiliation":[{"name":"Department of Neurology, Hospital de Egas Moniz, Centro Hospitalar de Lisboa Ocidental, Lisbon, Portugal;"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Pedro","family":"Calv\u00e3o-Pires","sequence":"additional","affiliation":[{"name":"Department of Neuroradiology, Hospital de Egas Moniz, Centro Hospitalar de Lisboa Ocidental, Lisbon, Portugal; and"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Andr\u00e9","family":"Caetano","sequence":"additional","affiliation":[{"name":"Department of Neurology, Hospital de Egas Moniz, Centro Hospitalar de Lisboa Ocidental, Lisbon, Portugal;"},{"name":"CEDOC Chronic Diseases Research Centre, Nova Medical School\/Faculdade de Ci\u00eancias M\u00e9dicas, Universidade Nova de Lisboa, Lisbon, Portugal."}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Lu\u00eds","family":"Santos","sequence":"additional","affiliation":[{"name":"Department of Neurology, Hospital de Egas Moniz, Centro Hospitalar de Lisboa Ocidental, Lisbon, Portugal;"},{"name":"CEDOC Chronic Diseases Research Centre, Nova Medical School\/Faculdade de Ci\u00eancias M\u00e9dicas, Universidade Nova de Lisboa, Lisbon, 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