{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,7]],"date-time":"2026-08-07T16:32:47Z","timestamp":1786120367436,"version":"build-2736575974"},"reference-count":12,"publisher":"Ovid Technologies (Wolters Kluwer Health)","issue":"3","content-domain":{"domain":["lww.com","ovid.com"],"crossmark-restriction":true},"short-container-title":[],"published-print":{"date-parts":[[2012,3]]},"abstract":"<jats:sec>\n                    <jats:title>Abstract<\/jats:title>\n                    <jats:p>We describe a patient presenting with progressive upper limb numbness and sensory ataxia of the 4 limbs. Motor nerve conduction studies were completely normal. Sensory electrophysiology showed reduced\/absent upper limb sensory action potentials (SAPs). In the lower limbs, SAPs were mostly normal. Sensory conduction velocities were normal. Forearm sensory conduction blocks were present for both median nerves on antidromic testing. The maximal recordable sural SAP was preserved in comparison to maximal recordable radial SAP, consistent with an \u201cabnormal radial normal sural\u201d pattern. Somatosensory evoked potentials were unrecordable for tibial and median nerves. Cerebrospinal fluid protein was raised (0.99 g\/L). The patient worsened on oral corticosteroids but subsequently made substantial functional recovery on intravenous immunoglobulins. This case is different to those previously reported of sensory chronic inflammatory demyelinating polyradiculoneuropathy, given its exclusive sensory electrophysiologic presentation, presence of predominant upper limb reduced sensory amplitudes, and detection of sensory conduction blocks. These electrophysiologic features were of paramount importance in establishing diagnosis and effective therapy.<\/jats:p>\n                  <\/jats:sec>","DOI":"10.1097\/cnd.0b013e31822484fb","type":"journal-article","created":{"date-parts":[[2012,2,22]],"date-time":"2012-02-22T05:50:41Z","timestamp":1329889841000},"page":"149-152","update-policy":"https:\/\/doi.org\/10.1097\/lww.0000000000001000","source":"Crossref","is-referenced-by-count":27,"title":["Chronic Inflammatory Pure Sensory Polyradiculoneuropathy"],"prefix":"10.1097","volume":"13","author":[{"given":"Yusuf A.","family":"Rajabally","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Siew L.","family":"Wong","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"276","reference":[{"key":"R1-7-20240808","doi-asserted-by":"crossref","first-page":"1662","DOI":"10.1212\/01.WNL.0000142507.12763.58","article-title":"Chronic immune sensory polyradiculopathy. A possibly treatable sensory ataxia.","volume":"63","author":"Sinnreich","year":"2004","journal-title":"Neurology"},{"key":"R2-7-20240808","doi-asserted-by":"crossref","first-page":"973","DOI":"10.1136\/jnnp.2005.081547","article-title":"A modified peripheral neuropathy scale: the Overall Neuropathy Limitations Scale.","volume":"77","author":"Graham","year":"2006","journal-title":"J Neurol Neurosurg Psychiatry"},{"key":"R3-7-20240808","doi-asserted-by":"crossref","first-page":"939","DOI":"10.1111\/j.1468-1331.2010.02953.x","article-title":"Electrophysiological sensory demyelination in typical chronic inflammatory demyelinating polyneuropathy.","volume":"17","author":"Rajabally","year":"2010","journal-title":"Eur J Neurol"},{"key":"R4-7-20240808","doi-asserted-by":"crossref","first-page":"677","DOI":"10.1136\/jnnp.55.8.677","article-title":"Chronic sensory demyelinating neuropathy: chronic inflammatory demyelinating polyneuropathy presenting as a pure sensory neuropathy.","volume":"55","author":"Oh","year":"1992","journal-title":"J Neurol Neurosurg Psychiatry"},{"key":"R5-7-20240808","doi-asserted-by":"crossref","first-page":"227","DOI":"10.1046\/j.1468-1331.2000.00048.x","article-title":"Ataxic form of chronic inflammatory demyelinating polyradiculoneuropathy (CIDP).","volume":"7","author":"Yato","year":"2000","journal-title":"Eur J Neurol"},{"key":"R6-7-20240808","doi-asserted-by":"crossref","first-page":"132","DOI":"10.1111\/j.1085-9489.2004.09302.x","article-title":"Sensory CIDP presenting as cryptogenic sensory polyneuropathy.","volume":"9","author":"Chin","year":"2004","journal-title":"J Peripher Nerv Syst"},{"key":"R7-7-20240808","first-page":"145","article-title":"Clinically and electrodiagnostically pure sensory demyelinating polyneuropathy.","volume":"36","author":"Rubin","year":"1996","journal-title":"Electromyogr Clin Neurophysiol"},{"key":"R8-7-20240808","doi-asserted-by":"crossref","first-page":"1999","DOI":"10.1016\/j.clinph.2007.06.014","article-title":"The value of sensory electrophysiology in chronic inflammatory demyelinating polyneuropathy.","volume":"118","author":"Rajabally","year":"2007","journal-title":"Clin Neurophysiol"},{"key":"R9-7-20240808","doi-asserted-by":"crossref","first-page":"1599","DOI":"10.1002\/mus.21186","article-title":"Sensory nerve conduction slowing is a specific marker for CIDP.","volume":"38","author":"Bragg","year":"2008","journal-title":"Muscle Nerve"},{"key":"R10-7-20240808","doi-asserted-by":"crossref","first-page":"356","DOI":"10.1111\/j.1468-1331.2009.02930.x","article-title":"European Federation of Neurological SocietiesPeripheral Nerve Society guideline on management of chronic inflammatory demyelinating polyneuropathy: report of a joint task force of the European Federation of Neurological Societies and the Peripheral Nerve SocietyFirst Revision.","volume":"17","author":"Van den Bergh","year":"2010","journal-title":"Eur J Neurol"},{"key":"R11-7-20240808","doi-asserted-by":"crossref","first-page":"440","DOI":"10.1002\/mus.880180411","article-title":"Late motor involvement in cases presenting as chronic sensory demyelinating polyneuropathy.","volume":"18","author":"Berger","year":"1995","journal-title":"Muscle Nerve"},{"key":"R12-7-20240808","doi-asserted-by":"crossref","first-page":"1134","DOI":"10.1007\/s004150050531","article-title":"Development of weakness in patients with chronic inflammatory demyelinating polyneuropathy and only sensory symptoms at presentation: a long-term follow-up study.","volume":"246","author":"van Dijk","year":"1999","journal-title":"J Neurol"}],"container-title":["Journal of Clinical Neuromuscular Disease"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/www.ovid.com\/00131402-201203000-00007","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2026,8,6]],"date-time":"2026-08-06T20:38:08Z","timestamp":1786048688000},"score":1,"resource":{"primary":{"URL":"https:\/\/www.ovid.com\/00131402-201203000-00007"}},"subtitle":["A Rare CIDP Variant With Unusual Electrophysiology"],"short-title":[],"issued":{"date-parts":[[2012,3]]},"references-count":12,"journal-issue":{"issue":"3","published-print":{"date-parts":[[2012]]}},"URL":"https:\/\/doi.org\/10.1097\/cnd.0b013e31822484fb","relation":{},"ISSN":["1522-0443"],"issn-type":[{"value":"1522-0443","type":"print"}],"subject":[],"published":{"date-parts":[[2012,3]]}}}