{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,7,5]],"date-time":"2026-07-05T01:54:00Z","timestamp":1783216440344,"version":"3.54.6"},"reference-count":25,"publisher":"Ovid Technologies (Wolters Kluwer Health)","issue":"8","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2018,8]]},"abstract":"<jats:sec>\n            <jats:title>Background:<\/jats:title>\n            <jats:p>Cutaneous angiosarcoma presents clinically in numerous ways, and can be mistaken for a different clinical entity, particularly when arising at unusual anatomic locations such as the eyelid.<\/jats:p>\n          <\/jats:sec>\n          <jats:sec>\n            <jats:title>Case Presentation:<\/jats:title>\n            <jats:p>A 57-year-old woman presented with a 1-year history of eyelid swelling. Concurrent imaging was also suggestive of an edematous process. Multiple superficial biopsies showed nonspecific dermal inflammation and interstitial edema. A diagnosis of Morbihan disease (chronic and idiopathic lymphedema of the eyelid) was rendered, and the patient was treated with compression and local therapy without clinical improvement. Three years after initial presentation, a diagnostic blepharoplasty was performed revealing a deep dermal vascular proliferation composed of anastomosing vascular channels with an atypical endothelial lining. A diagnosis of cutaneous angiosarcoma was ultimately made.<\/jats:p>\n          <\/jats:sec>\n          <jats:sec>\n            <jats:title>Conclusions:<\/jats:title>\n            <jats:p>This case illustrates a unique presentation of cutaneous angiosarcoma and the implications of different biopsy techniques in acquiring the correct diagnosis.<\/jats:p>\n          <\/jats:sec>","DOI":"10.1097\/dad.0000000000001096","type":"journal-article","created":{"date-parts":[[2018,1,12]],"date-time":"2018-01-12T16:55:44Z","timestamp":1515776144000},"page":"617-620","source":"Crossref","is-referenced-by-count":7,"title":["Cutaneous Angiosarcoma of the Eyelid Mimicking Morbihan Disease"],"prefix":"10.1097","volume":"40","author":[{"given":"Donna C.","family":"Ferguson","sequence":"first","affiliation":[{"name":"Department of Pathology, Microbiology and Immunology, Vanderbilt University Medical Center, Nashville, TN; and"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Louise A.","family":"Mawn","sequence":"additional","affiliation":[{"name":"Department of Ophthalmology and Visual Sciences, Vanderbilt Eye Institute, Vanderbilt University Medical Center, Nashville, TN."}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Rami N.","family":"Al-Rohil","sequence":"additional","affiliation":[{"name":"Department of Pathology, Microbiology and Immunology, Vanderbilt University Medical Center, Nashville, TN; and"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"276","reference":[{"key":"R1-20230908","doi-asserted-by":"crossref","first-page":"1046","DOI":"10.1002\/1097-0142(19870301)59:5<1046::AID-CNCR2820590533>3.0.CO;2-6","article-title":"Angiosarcoma of the face and scalp, prognosis and treatment","volume":"59","author":"Holden","year":"1987","journal-title":"Cancer."},{"key":"R2-20230908","doi-asserted-by":"crossref","first-page":"1346","DOI":"10.1046\/j.1365-2133.2000.03933.x","article-title":"Cutaneous angiosarcoma presenting as recurrent angio-oedema of the face","volume":"143","author":"Tay","year":"2000","journal-title":"Br J Dermatol."},{"key":"R3-20230908","doi-asserted-by":"crossref","first-page":"93","DOI":"10.1016\/j.anndiagpath.2010.07.012","article-title":"Cutaneous angiosarcoma. 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