{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,7]],"date-time":"2026-08-07T16:12:59Z","timestamp":1786119179455,"version":"build-2736575974"},"reference-count":9,"publisher":"Ovid Technologies (Wolters Kluwer Health)","issue":"3","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2008,4]]},"DOI":"10.1097\/mbc.0b013e3282f6d256","type":"journal-article","created":{"date-parts":[[2009,3,3]],"date-time":"2009-03-03T17:17:06Z","timestamp":1236100626000},"page":"240-242","source":"Crossref","is-referenced-by-count":2,"title":["Four novel FXI gene mutations in three factor XI- deficient patients"],"prefix":"10.1097","volume":"19","author":[{"given":"Emmanuelle","family":"de Raucourt","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Philippe","family":"de Mazancourt","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Florence","family":"Qu\u00e9lin","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"276","reference":[{"key":"R1-11-20210203","doi-asserted-by":"crossref","first-page":"10363","DOI":"10.1021\/bi00107a001","article-title":"The coagulation cascade: initiation maintenance and regulation","volume":"30","author":"Davie","year":"1991","journal-title":"Biochemistry"},{"key":"R2-11-20210203","doi-asserted-by":"crossref","first-page":"909","DOI":"10.1126\/science.1652157","article-title":"Factor XI activation in a revised model of blood coagulation","volume":"253","author":"Gailani","year":"1991","journal-title":"Science"},{"key":"R3-11-20210203","doi-asserted-by":"crossref","first-page":"1435","DOI":"10.1182\/blood.V79.6.1435.1435","article-title":"Expression of human blood coagulation factor XI: characterization of the defect in factor XI type III deficiency","volume":"79","author":"Mejers","year":"1992","journal-title":"Blood"},{"key":"R4-11-20210203","doi-asserted-by":"crossref","first-page":"153","DOI":"10.1056\/NEJM199107183250303","article-title":"Factor XI deficiency in Ashkenazi Jews in Israel","volume":"325","author":"Asakai","year":"1991","journal-title":"N Engl J Med"},{"key":"R5-11-20210203","doi-asserted-by":"crossref","first-page":"490","DOI":"10.1111\/j.1365-2516.2006.01304.x","article-title":"Variable bleeding manifestations characterize different types of surgery in patients with severe factor XI deficiency enabling parsimonious use of replacement therapy","volume":"12","author":"Salomon","year":"2006","journal-title":"Haemophilia"},{"key":"R6-11-20210203","doi-asserted-by":"crossref","first-page":"593","DOI":"10.1111\/j.1365-2516.2004.00944.x","article-title":"The rare coagulation disorders: review with guidelines for management from the United Kingdom Haemophilia Centre Doctors' Organisation","volume":"1","author":"Bolton Magg","year":"2004","journal-title":"Haemophilia"},{"key":"R7-11-20210203","doi-asserted-by":"crossref","first-page":"763","DOI":"10.1046\/j.1365-2141.1999.01769.x","article-title":"Heterozygous factor XI deficiency associated with three novel mutations","volume":"107","author":"Mitchell","year":"1999","journal-title":"Br J Haematol"},{"key":"R8-11-20210203","doi-asserted-by":"crossref","first-page":"557","DOI":"10.1038\/nsmb1095","article-title":"Crystal structure of the factor XI zymogen reveals a pathway for transactivation","volume":"13","author":"Papagrigoriou","year":"2006","journal-title":"Nat Struct Mol Biol"},{"key":"R9-11-20210203","doi-asserted-by":"crossref","first-page":"4671","DOI":"10.1182\/blood-2004-05-1864","article-title":"A classification system for cross-reactive material-negative factor XI deficiency","volume":"105","author":"Kravtsov","year":"2005","journal-title":"Blood"}],"container-title":["Blood Coagulation &amp; Fibrinolysis"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/www.ovid.com\/00001721-200804000-00011","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2026,8,6]],"date-time":"2026-08-06T17:36:34Z","timestamp":1786037794000},"score":1,"resource":{"primary":{"URL":"https:\/\/www.ovid.com\/00001721-200804000-00011"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2008,4]]},"references-count":9,"journal-issue":{"issue":"3","published-print":{"date-parts":[[2008]]}},"URL":"https:\/\/doi.org\/10.1097\/mbc.0b013e3282f6d256","relation":{},"ISSN":["0957-5235"],"issn-type":[{"value":"0957-5235","type":"print"}],"subject":[],"published":{"date-parts":[[2008,4]]}}}