{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,6,20]],"date-time":"2026-06-20T08:38:21Z","timestamp":1781944701191,"version":"3.54.5"},"reference-count":6,"publisher":"Ovid Technologies (Wolters Kluwer Health)","issue":"12","license":[{"start":{"date-parts":[[2024,3,22]],"date-time":"2024-03-22T00:00:00Z","timestamp":1711065600000},"content-version":"unspecified","delay-in-days":0,"URL":"http:\/\/creativecommons.org\/licenses\/by\/4.0\/"}],"content-domain":{"domain":["lww.com","ovid.com"],"crossmark-restriction":true},"short-container-title":[],"published-print":{"date-parts":[[2024,3,22]]},"abstract":"<jats:sec>\n            <jats:title>Introduction:<\/jats:title>\n            <jats:p>Cholesteatoma is a rare disease characterized by the accumulation of keratinized squamous epithelial cells in the middle ear or mastoid cavity. Vertigo and facial palsy, which are rare complications, may indicate erosion into the semicircular canals or the fallopian canal.<\/jats:p>\n          <\/jats:sec>\n          <jats:sec>\n            <jats:title>Patient concerns:<\/jats:title>\n            <jats:p>A 40-year-old woman presented to our clinic with progressive right-sided hearing loss over 5 years (primary concern). Approximately 10 years ago, the patient had developed acute right-sided facial weakness with no additional symptoms. A neurologist at another hospital had diagnosed her condition as Bell\u2019s palsy and treated it accordingly.<\/jats:p>\n          <\/jats:sec>\n          <jats:sec>\n            <jats:title>Diagnosis:<\/jats:title>\n            <jats:p>Adult-onset congenital cholesteatoma in the hypotympanum.<\/jats:p>\n          <\/jats:sec>\n          <jats:sec>\n            <jats:title>Intervention:<\/jats:title>\n            <jats:p>Combined endoscopic and microscopic removal of the cholesteatoma.<\/jats:p>\n          <\/jats:sec>\n          <jats:sec>\n            <jats:title>Outcomes:<\/jats:title>\n            <jats:p>Physical examination revealed slight improvement in right-sided peripheral facial palsy.<\/jats:p>\n          <\/jats:sec>\n          <jats:sec>\n            <jats:title>Lesson:<\/jats:title>\n            <jats:p>Routine eardrum examination is recommended for patients presenting with isolated peripheral facial palsy. If necessary, a patient should be referred to an otologist for further evaluation and treatment.<\/jats:p>\n          <\/jats:sec>","DOI":"10.1097\/md.0000000000037511","type":"journal-article","created":{"date-parts":[[2024,4,1]],"date-time":"2024-04-01T18:02:51Z","timestamp":1711994571000},"page":"e37511","update-policy":"https:\/\/doi.org\/10.1097\/lww.0000000000001000","source":"Crossref","is-referenced-by-count":3,"title":["Adult-onset congenital cholesteatoma in the hypotympanum initially presenting as Bell\u2019s palsy: A case report"],"prefix":"10.1097","volume":"103","author":[{"ORCID":"https:\/\/orcid.org\/0000-0002-7182-6913","authenticated-orcid":false,"given":"Pei-Shao","family":"Liao","sequence":"first","affiliation":[{"name":"Department of Otolaryngology Head and Neck Surgery, China Medical University Hospital, Taichung, Taiwan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Wei-Che","family":"Lan","sequence":"additional","affiliation":[{"name":"Department of Otolaryngology Head and Neck Surgery, China Medical University Hospital, Taichung, Taiwan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Ching-Yuan","family":"Wang","sequence":"additional","affiliation":[{"name":"Department of Otolaryngology Head and Neck Surgery, China Medical University Hospital, Taichung, Taiwan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Chia-Der","family":"Lin","sequence":"additional","affiliation":[{"name":"Department of Otolaryngology Head and Neck Surgery, China Medical University Hospital, Taichung, Taiwan"},{"name":"School of Medicine, China Medical University, Taichung, Taiwan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Yu","family":"Aoh","sequence":"additional","affiliation":[{"name":"Department of Neurology, China Medical University Hospital, Taichung, Taiwan."}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"276","reference":[{"key":"R2-20250503","doi-asserted-by":"crossref","first-page":"409","DOI":"10.1067\/mhn.2002.123446","article-title":"Congenital cholesteatoma: 20 years\u2019 experience at the children\u2019s hospital of Philadelphia.","volume":"126","author":"Potsic","year":"2002","journal-title":"Otolaryngol Head Neck Surg"},{"key":"R3-20250503","doi-asserted-by":"crossref","first-page":"34","DOI":"10.1067\/mhn.2002.121514","article-title":"Congenital middle ear cholesteatomas in children: our experience in 34 cases.","volume":"126","author":"Darrouzet","year":"2002","journal-title":"Otolaryngol Head Neck Surg"},{"key":"R4-20250503","doi-asserted-by":"crossref","first-page":"856","DOI":"10.3950\/jibiinkoka.106.856","article-title":"Congenital middle ear cholesteatoma: experience in 48 cases.","volume":"106","author":"Kojima","year":"2003","journal-title":"Nippon Jibiinkoka Gakkai Kaiho"},{"key":"R5-20250503","doi-asserted-by":"crossref","first-page":"841","DOI":"10.1016\/S0030-6665(02)00052-X","article-title":"The management of pediatric cholesteatoma.","volume":"35","author":"Shohet","year":"2002","journal-title":"Otolaryngol Clin North Am"},{"key":"R6-20250503","doi-asserted-by":"crossref","first-page":"1","DOI":"10.1186\/s43163-021-00151-4","article-title":"A case report of congenital cholesteatoma in adult patient mimicking as Bell palsy and proposed follow-up schedule for Bell palsy.","volume":"37","author":"Othman","year":"2021","journal-title":"Egypt J Otolaryngol"},{"key":"R7-20250503","doi-asserted-by":"crossref","first-page":"485","DOI":"10.1007\/s12070-011-0360-1","article-title":"Role of magnetic resonance imaging in cholesteatoma: the Indian experience.","volume":"65","author":"Vaid","year":"2013","journal-title":"Indian J Otolaryngol Head Neck Surg"}],"container-title":["Medicine"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/journals.lww.com\/10.1097\/MD.0000000000037511","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2025,5,4]],"date-time":"2025-05-04T00:20:43Z","timestamp":1746318043000},"score":1,"resource":{"primary":{"URL":"https:\/\/journals.lww.com\/10.1097\/MD.0000000000037511"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2024,3,22]]},"references-count":6,"journal-issue":{"issue":"12","published-print":{"date-parts":[[2024]]}},"URL":"https:\/\/doi.org\/10.1097\/md.0000000000037511","relation":{},"ISSN":["0025-7974","1536-5964"],"issn-type":[{"value":"0025-7974","type":"print"},{"value":"1536-5964","type":"electronic"}],"subject":[],"published":{"date-parts":[[2024,3,22]]}}}