{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,9,11]],"date-time":"2025-09-11T21:17:33Z","timestamp":1757625453609,"version":"3.44.0"},"reference-count":11,"publisher":"Ovid Technologies (Wolters Kluwer Health)","issue":"1","license":[{"start":{"date-parts":[[2025,1,3]],"date-time":"2025-01-03T00:00:00Z","timestamp":1735862400000},"content-version":"unspecified","delay-in-days":0,"URL":"http:\/\/creativecommons.org\/licenses\/by\/4.0\/"}],"content-domain":{"domain":["lww.com","ovid.com"],"crossmark-restriction":true},"short-container-title":[],"published-print":{"date-parts":[[2025,1,3]]},"abstract":"<jats:sec>\n            <jats:title>Rationale:<\/jats:title>\n            <jats:p>Berry syndrome is a complex congenital heart anomaly characterized by a combination of aortopulmonary window, interrupted aortic arch or hypoplastic aortic arch or coarctation of the aorta, anomalous origin of the right pulmonary artery, patent ductus arteriosus, and intact ventricular septum. It is an extremely rare condition, with approximately 100 reported cases to date.<\/jats:p>\n          <\/jats:sec>\n          <jats:sec>\n            <jats:title>Patient concerns:<\/jats:title>\n            <jats:p>In this article, we report a case of a 6-year-old girl with Berry syndrome who presented with significant ischemic and hypoxic symptoms.<\/jats:p>\n          <\/jats:sec>\n          <jats:sec>\n            <jats:title>Diagnoses:<\/jats:title>\n            <jats:p>Based on the patient\u2019s medical history and examinations, a definitive diagnosis of Berry syndrome was established.<\/jats:p>\n          <\/jats:sec>\n          <jats:sec>\n            <jats:title>Interventions:<\/jats:title>\n            <jats:p>She underwent a 1-stage surgical treatment and had a successful discharge. The surgical process was aimed to preserve the growth potential of the aorta and pulmonary arteries while achieving unobstructed left ventricular outflow and continuity of the aortic arch, ensuring no shunting between the main pulmonary arteries.<\/jats:p>\n          <\/jats:sec>\n          <jats:sec>\n            <jats:title>Outcomes:<\/jats:title>\n            <jats:p>Intraoperative transesophageal echocardiography confirmed continuous flow through the aortic arch and no shunting between the MPA and the aorta.<\/jats:p>\n          <\/jats:sec>","DOI":"10.1097\/md.0000000000041009","type":"journal-article","created":{"date-parts":[[2025,1,7]],"date-time":"2025-01-07T14:02:55Z","timestamp":1736258575000},"page":"e41009","update-policy":"https:\/\/doi.org\/10.1097\/lww.0000000000001000","source":"Crossref","is-referenced-by-count":0,"title":["Berry syndrome, a rare congenital cardiac structural abnormality with 1-stage surgical repair: A case report"],"prefix":"10.1097","volume":"104","author":[{"given":"Yueqiu","family":"Su","sequence":"first","affiliation":[{"name":"Department of Anesthesiology, West China Hospital, Sichuan University\/West China School of Nursing, Chengdu, Sichuan, China"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0009-0008-5688-4569","authenticated-orcid":false,"given":"Zhou","family":"Leng","sequence":"additional","affiliation":[{"name":"Department of Anesthesiology, West China Hospital, Sichuan University, Chengdu, Sichuan, China."}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"276","reference":[{"key":"R1-20250909","doi-asserted-by":"crossref","first-page":"108","DOI":"10.1016\/0002-9149(82)90284-3","article-title":"Distal aortopulmonary septal defect, aortic origin of the right pulmonary artery, intact ventricular septum, patent ductus arteriosus and hypoplasia of the aortic isthmus: a newly recognized syndrome.","volume":"49","author":"Berry","year":"1982","journal-title":"Am J Cardiol"},{"key":"R2-20250909","doi-asserted-by":"crossref","first-page":"15","DOI":"10.1186\/s12872-020-01837-y","article-title":"Berry syndrome: a case report and literature review.","volume":"21","author":"Bi","year":"2021","journal-title":"BMC Cardiovasc Disord"},{"key":"R3-20250909","doi-asserted-by":"crossref","first-page":"790303","DOI":"10.3389\/fcvm.2021.790303","article-title":"Outcomes of one-stage surgical repair for berry syndrome in neonates.","volume":"8","author":"Shi","year":"2022","journal-title":"Front Cardiovasc Med"},{"key":"R4-20250909","doi-asserted-by":"crossref","first-page":"772","DOI":"10.1007\/s11427-017-9086-7","article-title":"Berry syndrome: a rare cardiac malformation with extra-cardiac findings.","volume":"60","author":"Li","year":"2017","journal-title":"Sci China Life Sci"},{"key":"R5-20250909","doi-asserted-by":"crossref","first-page":"1139","DOI":"10.1016\/j.jtcvs.2016.11.058","article-title":"Current outcomes of one-stage surgical correction for berry syndrome.","volume":"153","author":"Hu","year":"2017","journal-title":"J Thorac Cardiovasc Surg"},{"key":"R6-20250909","doi-asserted-by":"crossref","first-page":"563","DOI":"10.1111\/echo.13832","article-title":"Prenatal diagnosis of berry syndrome by fetal echocardiography: a report of four cases.","volume":"35","author":"Zhang","year":"2018","journal-title":"Echocardiogr"},{"key":"R7-20250909","doi-asserted-by":"crossref","first-page":"443","DOI":"10.1016\/0002-9149(87)90953-2","article-title":"Anatomy and pathogenesis of aorticopulmonary septal defect.","volume":"59","author":"Kutsche","year":"1987","journal-title":"Am J Cardiol"},{"key":"R8-20250909","doi-asserted-by":"crossref","first-page":"526","DOI":"10.1007\/s12055-021-01206-0","article-title":"Berry syndrome-a rare congenital cardiac anomaly.","volume":"37","author":"Haranal","year":"2021","journal-title":"Indian J Thorac Cardiovasc Surg"},{"key":"R9-20250909","doi-asserted-by":"crossref","first-page":"1511","DOI":"10.1007\/s00246-012-0412-7","article-title":"Berry syndrome: a possible genetic link.","volume":"34","author":"Jayaram","year":"2013","journal-title":"Pediatr Cardiol"},{"key":"R10-20250909","doi-asserted-by":"crossref","first-page":"389","DOI":"10.1111\/j.1747-0803.2010.00476.x","article-title":"A case of berry syndrome type 2B.","volume":"6","author":"Mannelli","year":"2011","journal-title":"Congenit Heart Dis"},{"key":"R11-20250909","doi-asserted-by":"crossref","first-page":"1475","DOI":"10.1007\/s11748-020-01301-w","article-title":"Surgical repair in a patient with berry syndrome.","volume":"68","author":"Ando","year":"2020","journal-title":"Gen Thorac Cardiovasc Surg"}],"container-title":["Medicine"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/journals.lww.com\/10.1097\/MD.0000000000041009","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2025,9,9]],"date-time":"2025-09-09T18:01:27Z","timestamp":1757440887000},"score":1,"resource":{"primary":{"URL":"https:\/\/journals.lww.com\/10.1097\/MD.0000000000041009"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2025,1,3]]},"references-count":11,"journal-issue":{"issue":"1","published-print":{"date-parts":[[2025]]}},"URL":"https:\/\/doi.org\/10.1097\/md.0000000000041009","relation":{},"ISSN":["1536-5964"],"issn-type":[{"type":"electronic","value":"1536-5964"}],"subject":[],"published":{"date-parts":[[2025,1,3]]}}}