{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,24]],"date-time":"2026-09-24T11:56:13Z","timestamp":1790250973146,"version":"4.1.0"},"reference-count":48,"publisher":"Ovid Technologies (Wolters Kluwer Health)","issue":"1","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2009,1]]},"DOI":"10.1097\/md.0b013e3181943f5e","type":"journal-article","created":{"date-parts":[[2009,1,19]],"date-time":"2009-01-19T03:13:29Z","timestamp":1232334809000},"page":"23-31","source":"Crossref","is-referenced-by-count":204,"title":["Neutrophilic Urticarial Dermatosis"],"prefix":"10.1097","volume":"88","author":[{"given":"Carine","family":"Kieffer","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Bernard","family":"Cribier","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Dan","family":"Lipsker","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"276","reference":[{"key":"R1-2-20210226","first-page":"481","article-title":"Exacerbation of skin lesions during fever in a patient with chronic infantile neurologic cutaneous articular syndrome.","volume":"99","author":"Aboin-Gonzalez","year":"2008","journal-title":"Actas Dermosifiliogr"},{"key":"R2-2-20210226","doi-asserted-by":"crossref","first-page":"360","DOI":"10.1111\/j.1468-3083.2004.01142.x","article-title":"Adult-onset Still's disease with atypical cutaneous features.","volume":"19","author":"Affleck","year":"2005","journal-title":"J Eur Acad Dermatol Venereol"},{"key":"R3-2-20210226","doi-asserted-by":"crossref","first-page":"735","DOI":"10.1111\/j.1346-8138.2002.tb00212.x","article-title":"Schnitzler's syndrome with IgG k gammopathy.","volume":"29","author":"Akimoto","year":"2002","journal-title":"J Dermatol"},{"key":"R4-2-20210226","doi-asserted-by":"crossref","first-page":"145","DOI":"10.1097\/md.0b013e18064f9f3","article-title":"Aseptic abscesses: a study of 30 patients with or without inflammatory bowel disease and review of the literature.","volume":"86","author":"Andre","year":"2007","journal-title":"Medicine (Baltimore)"},{"key":"R5-2-20210226","first-page":"540","article-title":"A study of the cutaneous manifestations of Behcet's disease in patients from the United States.","volume":"41","author":"Balabanova","year":"1999","journal-title":"J Am Acad Dermatol"},{"key":"R6-2-20210226","doi-asserted-by":"crossref","first-page":"1088","DOI":"10.1001\/archderm.1988.01670070076024","article-title":"Urticarial vasculitis progressing to systemic lupus erythematosus.","volume":"124","author":"Bisaccia","year":"1988","journal-title":"Arch Dermatol"},{"key":"R7-2-20210226","doi-asserted-by":"crossref","first-page":"1278","DOI":"10.1001\/archderm.1994.01690100062010","article-title":"The histopathologic spectrum of palisaded neutrophilic and granulomatous dermatitis in patients with collagen vascular disease.","volume":"130","author":"Chu","year":"1994","journal-title":"Arch Dermatol"},{"key":"R8-2-20210226","doi-asserted-by":"crossref","first-page":"99","DOI":"10.2310\/7750.2006.00017","article-title":"Urticaria as a cutaneous sign of adult-onset Still's disease.","volume":"10","author":"Criado","year":"2006","journal-title":"J Cutan Med Surg"},{"key":"R9-2-20210226","doi-asserted-by":"crossref","first-page":"573","DOI":"10.1016\/S0046-8177(03)00193-X","article-title":"The dermatopathologic manifestations of hepatitis C infection: a clinical, histological and molecular assesment of 35 cases.","volume":"34","author":"Crowson","year":"2003","journal-title":"Hum Pathol"},{"key":"R10-2-20210226","doi-asserted-by":"crossref","first-page":"94","DOI":"10.1159\/000246220","article-title":"Urticarial pathology in Schnitzler's (hyper-IgM) syndrome.","volume":"193","author":"De Castro","year":"1996","journal-title":"Dermatology"},{"key":"R11-2-20210226","doi-asserted-by":"crossref","first-page":"137","DOI":"10.1016\/j.semarthrit.2007.04.001","article-title":"Schnitzler syndrome. Beyond the case reports: review and follow-up of 94 patients with an emphasis on prognosis and treatment.","volume":"37","author":"De Koning","year":"2007","journal-title":"Semin Arthritis Rheum"},{"key":"R12-2-20210226","doi-asserted-by":"crossref","first-page":"59","DOI":"10.1001\/archderm.1994.01690010063008","article-title":"Cutaneous manifestations and histologic findings in the hyperimmunoglobulinemia D syndrome.","volume":"130","author":"Drenth","year":"1994","journal-title":"Arch Dermatol"},{"key":"R13-2-20210226","doi-asserted-by":"crossref","first-page":"551","DOI":"10.1136\/jmg.2005.030759","article-title":"Homozygous mutations in LPIN2 are responsible for the syndrome of chronic recurrent multifocal osteomyelitis and congenital dyserythropoietic anaemia (Majeed syndrome).","volume":"42","author":"Ferguson","year":"2005","journal-title":"J Med Genet"},{"key":"R14-2-20210226","doi-asserted-by":"crossref","first-page":"1794","DOI":"10.1002\/art.21061","article-title":"Rapid responses to anakinra in patients with refractory adult-onset Still's disease.","volume":"52","author":"Fitzgerald","year":"2005","journal-title":"Arthritis Rheum"},{"key":"R15-2-20210226","first-page":"527","article-title":"Hepatitis B-associated adult-onset Still's disease presenting with neutrophilic urticaria.","volume":"8","author":"Gambichler","year":"2003","journal-title":"Eur J Med Res"},{"key":"R16-2-20210226","doi-asserted-by":"crossref","first-page":"28S","DOI":"10.1111\/1523-1747.ep12355210","article-title":"Bullous SLE: a phenotypically distinctive but immunologically heterogeneous bullous disorder.","volume":"100","author":"Gammon","year":"1993","journal-title":"J Invest Dermatol"},{"key":"R18-2-20210226","doi-asserted-by":"crossref","first-page":"721","DOI":"10.1111\/j.1600-0560.2006.00559.x","article-title":"Non-bullous neutrophilic dermatosis: an uncommon dermatologic manifestation in patients with lupus erythematosus.","volume":"33","author":"Gleason","year":"2006","journal-title":"J Cutan Pathol"},{"key":"R19-2-20210226","doi-asserted-by":"crossref","first-page":"789","DOI":"10.1001\/archderm.1985.01660060103031","article-title":"Sweet's syndrome in subacute cutaneous lupus erythematosus.","volume":"121","author":"Goette","year":"1985","journal-title":"Arch Dermatol"},{"key":"R20-2-20210226","doi-asserted-by":"crossref","first-page":"99","DOI":"10.1111\/j.1365-2133.2004.06001.x","article-title":"Muckle-Wells syndrome: clinical and histological skin findings compatible with cold air urticaria in a large kindred.","volume":"151","author":"Haas","year":"2004","journal-title":"Br J Dermatol"},{"key":"R21-2-20210226","doi-asserted-by":"crossref","first-page":"399","DOI":"10.1191\/0961203305lu2083cr","article-title":"Sweet's syndrome as an initial presentation in systemic lupus erythematosus: a case report and review of the literature.","volume":"14","author":"Hou","year":"2005","journal-title":"Lupus"},{"key":"R22-2-20210226","doi-asserted-by":"crossref","first-page":"99","DOI":"10.1097\/00000372-198911020-00001","article-title":"Acute febrile neutrophilic dermatosis: a histopathological study of 37 patients and a review of the literature.","volume":"11","author":"Jordaan","year":"1989","journal-title":"Am J Dermatopathol"},{"key":"R23-2-20210226","doi-asserted-by":"crossref","first-page":"248","DOI":"10.1001\/archderm.141.2.248","article-title":"Neonatal-onset multisystem inflammatory disorder: the emerging role of pyrin genes in autoinflammatory diseases.","volume":"141","author":"Kilcline","year":"2005","journal-title":"Arch Dermatol"},{"key":"R24-2-20210226","doi-asserted-by":"crossref","first-page":"1591","DOI":"10.1001\/archderm.142.12.1591","article-title":"Phenotype, genotype, and sustained response to anakinra in 22 patients with autoinflammatory disease associated with CIAS-1\/NALP3 mutations.","volume":"142","author":"Leslie","year":"2006","journal-title":"Arch Dermatol"},{"key":"R25-2-20210226","doi-asserted-by":"crossref","first-page":"72","DOI":"10.1046\/j.0303-6987.2004.0141.x","article-title":"Mid-dermal elastolysis preceded by acute neutrophilic dermatosis.","volume":"31","author":"Lewis","year":"2004","journal-title":"J Cutan Pathol"},{"key":"R26-2-20210226","doi-asserted-by":"crossref","first-page":"290","DOI":"10.1016\/S0190-9622(98)70094-5","article-title":"Muckle-Wells syndrome: case report and review of cutaneous pathology.","volume":"39","author":"Lieberman","year":"1998","journal-title":"J Am Acad Dermatol"},{"key":"R27-2-20210226","doi-asserted-by":"crossref","first-page":"611","DOI":"10.1016\/S0025-6196(11)63565-9","article-title":"A new autosomal dominant disorder of pyogenic sterile arthritis, pyoderma gangrenosum and acne: PAPA syndrome.","volume":"72","author":"Lindor","year":"1997","journal-title":"Mayo Clin Proc"},{"key":"R28-2-20210226","doi-asserted-by":"crossref","first-page":"283","DOI":"10.1159\/000113940","article-title":"Neutrophilic cutaneous lupus erythematosus: at the edge between innate and acquired immunity?","volume":"216","author":"Lipsker","year":"2008","journal-title":"Dermatology"},{"key":"R29-2-20210226","doi-asserted-by":"crossref","first-page":"37","DOI":"10.1097\/00005792-200101000-00004","article-title":"The Schnitzler syndrome: four new cases and review of the literature.","volume":"80","author":"Lipsker","year":"2001","journal-title":"Medicine (Baltimore)"},{"key":"R30-2-20210226","first-page":"173","article-title":"Familial polymorphous cold eruption.","volume":"27","author":"Martin","year":"1981","journal-title":"Cutis"},{"key":"R31-2-20210226","doi-asserted-by":"crossref","first-page":"446","DOI":"10.1111\/j.1365-4362.1986.tb03450.x","article-title":"Systemic lupus erythematosus appearing as an urticarial vasculitis.","volume":"25","author":"Matarredona","year":"1986","journal-title":"Int J Dermatol"},{"key":"R32-2-20210226","doi-asserted-by":"crossref","first-page":"1242","DOI":"10.1371\/journal.pmed.0030297","article-title":"A proposed classification of the immunological diseases.","volume":"3","author":"McGonagle","year":"2006","journal-title":"PloS Medicine"},{"key":"R33-2-20210226","doi-asserted-by":"crossref","first-page":"441","DOI":"10.1016\/0190-9622(92)70069-R","article-title":"Urticarial vasculitis: a histologic and clinical review of 72 cases.","volume":"26","author":"Mehregan","year":"1992","journal-title":"J Am Acad Dermatol"},{"key":"R34-2-20210226","doi-asserted-by":"crossref","first-page":"32","DOI":"10.1111\/j.1346-8138.1995.tb03337.x","article-title":"A case of urticarial vasculitis associated with macroglobulinemia (Schnitzler's syndrome).","volume":"22","author":"Morita","year":"1995","journal-title":"J Dermatol"},{"key":"R35-2-20210226","first-page":"107","article-title":"Manifestations cutanees de la maladie de Still de l'adulte. A propos de 4 observations.","volume":"110","author":"Noyon","year":"1983","journal-title":"Ann Dermatol Venereol"},{"key":"R36-2-20210226","doi-asserted-by":"crossref","first-page":"371","DOI":"10.1046\/j.1365-2133.2002.04790.x","article-title":"Extravascular necrotizing palisaded granulomas as the presenting skin sign of systemic lupus erythematosus.","volume":"147","author":"Obermoser","year":"2002","journal-title":"Br J Dermatol"},{"key":"R37-2-20210226","doi-asserted-by":"crossref","first-page":"25","DOI":"10.1111\/j.1365-2133.1985.tb02040.x","article-title":"Neutrophilic urticaria.","volume":"113","author":"Peters","year":"1985","journal-title":"Br J Dermatol"},{"key":"R38-2-20210226","first-page":"297","article-title":"Manifestations dermatologiques des maladies inflammatoires du tube digestif.","volume":"119","author":"Piette","year":"1992","journal-title":"Ann Dermatol Venereol"},{"key":"R39-2-20210226","doi-asserted-by":"crossref","first-page":"125","DOI":"10.1097\/01.dad.0000249887.59810.76","article-title":"Acute febrile neutrophilic dermatosis: a histopathologic study of 31 cases with review of literature.","volume":"29","author":"Ratzinger","year":"2007","journal-title":"Am J Dermatopathol"},{"key":"R40-2-20210226","first-page":"485","article-title":"Pyoderma gangrenosum in a patient with bullous systemic lupus erythematosus.","volume":"12","author":"Sakamoto","year":"2002","journal-title":"Eur J Dermatol"},{"key":"R41-2-20210226","doi-asserted-by":"crossref","first-page":"389","DOI":"10.1007\/s100670070034","article-title":"Urticaria as a presenting manifestation of adult-onset Still's disease.","volume":"19","author":"Salaffi","year":"2000","journal-title":"Clin Rheumatol"},{"key":"R42-2-20210226","doi-asserted-by":"crossref","first-page":"599","DOI":"10.1016\/S0190-9622(82)70139-2","article-title":"The clinical and histopathologic spectrums of urticarial vasculitis: study of forty cases.","volume":"7","author":"Sanchez","year":"1982","journal-title":"J Am Acad Dermatol"},{"key":"R43-2-20210226","doi-asserted-by":"crossref","first-page":"S120","DOI":"10.1016\/j.jaad.2006.05.057","article-title":"Prompt response of refractory Schnitzler syndrome to treatment with anakinra.","volume":"56","author":"Schneider","year":"2007","journal-title":"J Am Acad Dermatol"},{"key":"R44-2-20210226","doi-asserted-by":"crossref","first-page":"906","DOI":"10.1046\/j.1365-2133.1998.02237.x","article-title":"Urticaria as a presentation of adult Still's disease.","volume":"138","author":"Setterfield","year":"1998","journal-title":"Br J Dermatol"},{"key":"R45-2-20210226","doi-asserted-by":"crossref","first-page":"394","DOI":"10.1159\/000018041","article-title":"Amicrobial pustulosis of the folds.","volume":"197","author":"Stefanidou","year":"1998","journal-title":"Dermatology"},{"key":"R46-2-20210226","doi-asserted-by":"crossref","first-page":"41","DOI":"10.1001\/archderm.134.1.41","article-title":"Microscopic morphology of different types of urticaria.","volume":"134","author":"Toppe","year":"1998","journal-title":"Arch Dermatol"},{"key":"R47-2-20210226","doi-asserted-by":"crossref","first-page":"64","DOI":"10.1159\/000081488","article-title":"Pyoderma gangrenosum preceding the diagnosis of systemic lupus erythematosus.","volume":"210","author":"Waldman","year":"2005","journal-title":"Dermatology"},{"key":"R48-2-20210226","doi-asserted-by":"crossref","first-page":"201","DOI":"10.1046\/j.1440-0960.1999.00361.x","article-title":"Schnitzler's syndrome: report of a case with progression to Waldenstrom's macroglobulinaemia.","volume":"40","author":"Welsh","year":"1999","journal-title":"Australas J Dermatol"},{"key":"R49-2-20210226","first-page":"129","article-title":"Neutrophilic urticaria.","volume":"68","author":"Winkelmann","year":"1988","journal-title":"Acta Derm Venereol"}],"container-title":["Medicine"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/www.ovid.com\/10.1097\/MD.0b013e3181943f5e","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2026,8,6]],"date-time":"2026-08-06T17:31:53Z","timestamp":1786037513000},"score":1,"resource":{"primary":{"URL":"https:\/\/www.ovid.com\/00005792-200901000-00002"}},"subtitle":["A Variant of Neutrophilic Urticaria Strongly Associated With Systemic Disease. Report of 9 New Cases and Review of the Literature"],"short-title":[],"issued":{"date-parts":[[2009,1]]},"references-count":48,"journal-issue":{"issue":"1","published-print":{"date-parts":[[2009]]}},"URL":"https:\/\/doi.org\/10.1097\/md.0b013e3181943f5e","relation":{"has-review":[{"id-type":"doi","id":"10.3410\/f.1160760.622168","asserted-by":"object"}]},"ISSN":["0025-7974"],"issn-type":[{"value":"0025-7974","type":"print"}],"subject":[],"published":{"date-parts":[[2009,1]]}}}