{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,15]],"date-time":"2026-10-15T10:18:34Z","timestamp":1792059514632,"version":"4.4.0"},"reference-count":16,"publisher":"Wiley","issue":"6","license":[{"start":{"date-parts":[[2009,1,2]],"date-time":"2009-01-02T00:00:00Z","timestamp":1230854400000},"content-version":"vor","delay-in-days":581,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["The Laryngoscope"],"published-print":{"date-parts":[[2007,6]]},"abstract":"<jats:title>Abstract<\/jats:title><jats:p><jats:bold>Objective<\/jats:bold>: To evaluate the long\u2010term hearing outcomes of neurofibromatosis type 2 (NF2) patients with cochlear implants.<\/jats:p><jats:p><jats:bold>Methods<\/jats:bold>: Retrospective analysis of cochlear implant performance in NF2 patients using open\u2010 and closed\u2010set speech perception testing.<\/jats:p><jats:p><jats:bold>Results<\/jats:bold>: Patients with NF2\u2010associated bilateral vestibular schwannomas frequently become profoundly deaf. The aim of surgical resection should be to preserve serviceable hearing in at least one ear; however, this goal can be difficult to achieve. Frequently, tumor size or poor preoperative hearing status can require a surgical approach that leaves the patient with a profound, bilateral sensorineural hearing loss. If the cochlear nerve is preserved anatomically after vestibular schwannoma surgery, and if promontory stimulation confirms the functionality of the cochlear nerve, then cochlear implantation is an excellent option to restore hearing. We present six cochlear implant patients with NF2 who attained a significant improvement in open\u2010 and closed\u2010set speech understanding with a mean follow\u2010up of 7.9 (range: 5\u201313) years after surgery. In all but one case, the hearing results did not deteriorate over the follow\u2010up period.<\/jats:p><jats:p><jats:bold>Conclusion<\/jats:bold>: Early surgical intervention for vestibular schwannomas in NF2 patients when the cochlear nerve can be spared is an important consideration to allow for possible cochlear implantation. A 6\u2010 to 8\u2010week recovery period for the anatomically intact cochlear nerve may be necessary to obtain a positive promontory stimulation response following tumor resection and should be performed prior to cochlear implantation.<\/jats:p>","DOI":"10.1097\/mlg.0b013e31804b1ae7","type":"journal-article","created":{"date-parts":[[2007,5,23]],"date-time":"2007-05-23T22:16:51Z","timestamp":1179958611000},"page":"1069-1072","source":"Crossref","is-referenced-by-count":113,"title":["Cochlear Implantation in the Neurofibromatosis Type 2 Patient: Long\u2010Term Follow\u2010up"],"prefix":"10.1002","volume":"117","author":[{"given":"Brian A.","family":"Neff","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"R Mark","family":"Wiet","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"John M.","family":"Lasak","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Noel L.","family":"Cohen","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Harold C.","family":"Pillsbury","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Richard T.","family":"Ramsden","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"D Bradley","family":"Welling","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"311","published-online":{"date-parts":[[2009,1,2]]},"reference":[{"key":"e_1_2_6_2_2","doi-asserted-by":"publisher","DOI":"10.1097\/00129492-200403000-00012"},{"key":"e_1_2_6_3_2","doi-asserted-by":"publisher","DOI":"10.3171\/jns.2002.96.6.1063"},{"key":"e_1_2_6_4_2","doi-asserted-by":"publisher","DOI":"10.1097\/00005537-200303000-00015"},{"key":"e_1_2_6_5_2","doi-asserted-by":"publisher","DOI":"10.1001\/archotol.1995.01890040083014"},{"key":"e_1_2_6_6_2","doi-asserted-by":"publisher","DOI":"10.1017\/S0022215100143452"},{"key":"e_1_2_6_7_2","first-page":"525","article-title":"Cochlear implants in the management of bilateral acoustic neuromas.","volume":"13","author":"Hoffman RA","year":"1992","journal-title":"Am J Otol"},{"key":"e_1_2_6_8_2","first-page":"367","volume-title":"Cochlear Implants","author":"Grant IL","year":"2000"},{"key":"e_1_2_6_9_2","doi-asserted-by":"publisher","DOI":"10.1097\/00129492-200503000-00013"},{"key":"e_1_2_6_10_2","doi-asserted-by":"publisher","DOI":"10.1288\/00005537-198811000-00004"},{"key":"e_1_2_6_11_2","doi-asserted-by":"publisher","DOI":"10.1097\/00129492-200107000-00015"},{"key":"e_1_2_6_12_2","doi-asserted-by":"publisher","DOI":"10.1288\/00005537-198906000-00008"},{"key":"e_1_2_6_13_2","doi-asserted-by":"publisher","DOI":"10.1016\/S0196-0709(00)80041-1"},{"key":"e_1_2_6_14_2","first-page":"50","article-title":"Multichannel auditory brainstem implant: US clinical trial results.","volume":"27","author":"Ebinger K","year":"2000","journal-title":"J Laryngol Otol Suppl"},{"key":"e_1_2_6_15_2","doi-asserted-by":"publisher","DOI":"10.1097\/00003446-200206000-00002"},{"key":"e_1_2_6_16_2","unstructured":"Shannonet al.Psychophysical and speech results from the first patients with the penetrating auditory brainstem implant (PABI). Presented at: VIII International Cochlear Implant Conference; May 10\u201013 2004 Indianapolis IN."},{"key":"e_1_2_6_17_2","doi-asserted-by":"publisher","DOI":"10.1097\/00129492-200606000-00013"}],"container-title":["The Laryngoscope"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.wiley.com\/onlinelibrary\/tdm\/v1\/articles\/10.1097%2FMLG.0b013e31804b1ae7","content-type":"unspecified","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/pdf\/10.1097\/MLG.0b013e31804b1ae7","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2023,10,10]],"date-time":"2023-10-10T02:41:19Z","timestamp":1696905679000},"score":1,"resource":{"primary":{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/10.1097\/MLG.0b013e31804b1ae7"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2007,6]]},"references-count":16,"journal-issue":{"issue":"6","published-print":{"date-parts":[[2007,6]]}},"alternative-id":["10.1097\/MLG.0b013e31804b1ae7"],"URL":"https:\/\/doi.org\/10.1097\/mlg.0b013e31804b1ae7","archive":["Portico"],"relation":{},"ISSN":["0023-852X","1531-4995"],"issn-type":[{"value":"0023-852X","type":"print"},{"value":"1531-4995","type":"electronic"}],"subject":[],"published":{"date-parts":[[2007,6]]}}}