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The understanding of GSD has increased in recent decades, and nutritional management of some GSDs has allowed better control of hypoglycemia and metabolic complications. However, growth failure and liver, renal, and other complications are frequent problems in the long\u2010term outcome. Hypoglycemia is the main biochemical consequence of GSD type I and some of the other GSDs. The basis of dietary therapy is nutritional manipulation to prevent hypoglycemia and improve metabolic dysfunction, with the use of continuous nocturnal intragastric feeding or cornstarch therapy at night and foods rich in starches with low concentrations of galactose and fructose during the day and to prevent hypoglycemia during the night.<\/jats:p><\/jats:sec>","DOI":"10.1097\/mpg.0b013e3181818ea5","type":"journal-article","created":{"date-parts":[[2009,3,5]],"date-time":"2009-03-05T21:34:19Z","timestamp":1236288859000},"source":"Crossref","is-referenced-by-count":55,"title":["Nutritional Therapy for Glycogen Storage Diseases"],"prefix":"10.1002","volume":"47","author":[{"given":"Solange","family":"Heller","sequence":"first","affiliation":[{"name":"Department of Gastroenterology and Nutrition Hospital Infantil de M\u00e9xico Federico G\u00f3mez M\u00e9xico DF 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