{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,8,15]],"date-time":"2025-08-15T00:12:40Z","timestamp":1755216760014,"version":"3.43.0"},"reference-count":12,"publisher":"Ovid Technologies (Wolters Kluwer Health)","issue":"5","content-domain":{"domain":["lww.com","ovid.com"],"crossmark-restriction":true},"short-container-title":[],"published-print":{"date-parts":[[2024,7]]},"abstract":"<jats:p>Multiple myeloma is a rare disease in pediatrics, where about 30 cases are described under 15 years old. It is even rarer when atypical multiple myeloma occurs in the context of autoimmunity. This case describes a 9-year-old female with autoimmune lymphoproliferative-like disease and combined immune deficiency that developed acute kidney failure with monoclonal peak associated with <jats:italic toggle=\"yes\">RAC2<\/jats:italic> and <jats:italic toggle=\"yes\">TNFRSF9<\/jats:italic> variants. An adapted protocol from the backbone adult multiple myeloma standard of care with the addition of an allogeneic hematopoietic stem cell transplant was used. The patient, now nearly a year posttransplant, shows 100% chimerism with no sign of relapse.<\/jats:p>","DOI":"10.1097\/mph.0000000000002859","type":"journal-article","created":{"date-parts":[[2024,4,23]],"date-time":"2024-04-23T11:01:03Z","timestamp":1713870063000},"page":"e331-e333","update-policy":"https:\/\/doi.org\/10.1097\/lww.0000000000001000","source":"Crossref","is-referenced-by-count":0,"title":["Unveiling the Uncommon: A Unique Case of ALPS-like Syndrome Complicated by Plasma Cell Disorder"],"prefix":"10.1097","volume":"46","author":[{"given":"Meziane","family":"Brizini","sequence":"first","affiliation":[{"name":"Department of Pediatrics, CHU de Qu\u00e9bec, Universit\u00e9 Laval"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Bruno","family":"Michon","sequence":"additional","affiliation":[{"name":"Department of Pediatrics Hematology-Oncology, CHU de Qu\u00e9bec, Universit\u00e9 Laval"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Marc-Antoine","family":"B\u00e9dard","sequence":"additional","affiliation":[{"name":"Department of Immunology and Allergy, CHU de Qu\u00e9bec, Universit\u00e9 Laval, Qu\u00e9bec, Canada"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"276","published-online":{"date-parts":[[2024,4,23]]},"reference":[{"key":"R1-20250804","doi-asserted-by":"crossref","first-page":"1980","DOI":"10.1002\/ijc.33762","article-title":"Epidemiology, genetics and treatment of multiple myeloma and precursor diseases","volume":"149","author":"Hemminki","year":"2021","journal-title":"Int J Cancer"},{"key":"R2-20250804","doi-asserted-by":"crossref","first-page":"1463","DOI":"10.1001\/archinte.1996.00440120125014","article-title":"Multiple myeloma in patients younger than 30 years. 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