{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,23]],"date-time":"2026-09-23T21:25:58Z","timestamp":1790198758264,"version":"4.1.0"},"reference-count":26,"publisher":"Ovid Technologies (Wolters Kluwer Health)","issue":"8","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2008,8]]},"DOI":"10.1097\/mph.0b013e3181758947","type":"journal-article","created":{"date-parts":[[2009,3,5]],"date-time":"2009-03-05T16:43:39Z","timestamp":1236271419000},"page":"631-634","source":"Crossref","is-referenced-by-count":29,"title":["XLA-associated Neutropenia Treatment"],"prefix":"10.1097","volume":"30","author":[{"given":"Zachary David","family":"Jacobs","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Jesus Ramon","family":"Guajardo","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Katherine Marie","family":"Anderson","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"276","reference":[{"key":"R1-15-20210227","doi-asserted-by":"crossref","first-page":"722","DOI":"10.1542\/peds.9.6.722","article-title":"Agammaglobulinemia","volume":"9","author":"Bruton","year":"1952","journal-title":"Pediatrics"},{"key":"R2-15-20210227","first-page":"1043","article-title":"Middleton's Allergy: Principles and Practice","author":"Ballow","year":"2003"},{"key":"R3-15-20210227","doi-asserted-by":"crossref","first-page":"105","DOI":"10.1111\/j.1600-065X.1994.tb00849.x","article-title":"Bruton's tyrosine kinase is a key regulator in B-cell development","volume":"138","author":"Rawlings","year":"1994","journal-title":"Immun Rev"},{"key":"R4-15-20210227","doi-asserted-by":"crossref","first-page":"271","DOI":"10.1006\/clin.1996.0188","article-title":"Neutropenia in X-linked agammaglobulinemia","volume":"81","author":"Farrar","year":"1996","journal-title":"Clin Immunol Immunopathol"},{"key":"R5-15-20210227","doi-asserted-by":"crossref","first-page":"175","DOI":"10.1016\/S0171-2985(86)80097-3","article-title":"Recombinant human granulocyte colony-stimulating factor: molecular and biological characterization","volume":"172","author":"Zsebo","year":"1986","journal-title":"Immunobiology"},{"key":"R6-15-20210227","doi-asserted-by":"crossref","first-page":"2144","DOI":"10.1182\/blood.V74.6.2144.2144","article-title":"Recombinant human granulocyte colony-stimulating factor as an activator of human granulocytes: potentiation of responses triggered by receptor-mediated agonists and stimulation of C3bi receptor expression and adherence","volume":"74","author":"Yuo","year":"1989","journal-title":"Blood"},{"key":"R7-15-20210227","doi-asserted-by":"crossref","first-page":"809","DOI":"10.1038\/bjc.1987.295","article-title":"Phase I\/II study of recombinant human granulocyte colony-stimulating factor in patients receiving intensive chemotherapy for small cell lung cancer","volume":"56","author":"Bronchud","year":"1987","journal-title":"Brit J Cancer"},{"key":"R8-15-20210227","doi-asserted-by":"crossref","first-page":"1414","DOI":"10.1056\/NEJM198806023182202","article-title":"Effect of granulocyte colony-stimulating factor on neutropenia and associated morbidity due to chemotherapy for transitional cell carcinoma of the urothelium","volume":"318","author":"Gabrilove","year":"1988","journal-title":"New Engl J Med"},{"key":"R9-15-20210227","doi-asserted-by":"crossref","first-page":"2496","DOI":"10.1182\/blood.V81.10.2496.2496","article-title":"A randomized controlled phase III trial of recombinant human granulocyte colony-stimulating factor (filgrastim) for treatment of severe chronic neutropenia","volume":"81","author":"Dale","year":"1993","journal-title":"Blood"},{"key":"R10-15-20210227","doi-asserted-by":"crossref","first-page":"82","DOI":"10.1002\/ajh.10255","article-title":"Severe chronic neutropenia: treatment and follow-up of patients in the severe chronic neutropenia international registry","volume":"72","author":"Dale","year":"2003","journal-title":"Am J Hematol"},{"key":"R11-15-20210227","first-page":"1778","article-title":"Wintrobe's Clinical Hematology","author":"Watts","year":"2004"},{"key":"R12-15-20210227","first-page":"424","article-title":"Mutations of the Btk gene in 12 unrelated families with X-linked agammaglobulinemia in Japan","volume":"97","author":"Kobayashi","year":"1996","journal-title":"Hum Genet"},{"key":"R13-15-20210227","doi-asserted-by":"crossref","first-page":"145","DOI":"10.1097\/00005792-198505000-00001","article-title":"X-linked agammaglobulinemia: an analysis of 96 patients","volume":"64","author":"Lederman","year":"1985","journal-title":"Medicine"},{"key":"R14-15-20210227","doi-asserted-by":"crossref","first-page":"388","DOI":"10.1136\/jcp.44.5.388","article-title":"Neutropenia associated with X-linked agammaglobulinemia","volume":"44","author":"Kozlowski","year":"1991","journal-title":"J Clin Pathol"},{"key":"R15-15-20210227","doi-asserted-by":"crossref","first-page":"657","DOI":"10.1080\/08880010390243103","article-title":"Is neutropenia a clue for early diagnosis of X-linked agammaglobulinemia?","volume":"20","author":"Tavil","year":"2003","journal-title":"Pediatr Hematol Oncol"},{"key":"R16-15-20210227","doi-asserted-by":"crossref","first-page":"491","DOI":"10.1007\/s10875-005-5370-x","article-title":"Severe neutropenia in Japanese patients with X-linked agammaglobulinemia","volume":"25","author":"Kanegane","year":"2005","journal-title":"J Clin Immunol"},{"key":"R17-15-20210227","doi-asserted-by":"crossref","first-page":"193","DOI":"10.1097\/01.md.0000229482.27398.ad","article-title":"X-linked agammaglobulinemia: report on a United States registry of 201 patients","volume":"85","author":"Winkelstein","year":"2006","journal-title":"Medicine"},{"key":"R18-15-20210227","first-page":"181","article-title":"Defective Fc, CR1 and CR3-mediated monocyte phagocytosis and chemotaxis in common variable immunodeficiency and X-linked agammaglobulinemia patients","volume":"13","author":"Amoras","year":"2003","journal-title":"J Invest Allergol Clin Immunol"},{"key":"R19-15-20210227","doi-asserted-by":"crossref","first-page":"1603","DOI":"10.1084\/jem.20021845","article-title":"Bruton's tyrosine kinase is required for lipopolysaccharide-induced tumor necrosis factor \u03b1 production","volume":"197","author":"Horwood","year":"2003","journal-title":"J Exp Med"},{"key":"R20-15-20210227","first-page":"300","article-title":"Maturation-linked expression of the Fc (IgG) receptor on developing human bone marrow and peripheral blood granulocytes","volume":"38","author":"Scott","year":"1979","journal-title":"Clin Exp Immunol"},{"key":"R21-15-20210227","doi-asserted-by":"crossref","first-page":"2879","DOI":"10.4049\/jimmunol.167.5.2879","article-title":"A role for IL-18 in neutrophil activation","volume":"167","author":"Leung","year":"2001","journal-title":"J Immunol"},{"key":"R22-15-20210227","doi-asserted-by":"crossref","first-page":"697","DOI":"10.1067\/mai.2003.1380","article-title":"IgG Fc receptor polymorphisms in human disease: implications for intravenous immunoglobulin therapy","volume":"111","author":"Binstadt","year":"2003","journal-title":"J Allergy Clin Immunol"},{"key":"R23-15-20210227","doi-asserted-by":"crossref","first-page":"275","DOI":"10.1146\/annurev.immunol.19.1.275","article-title":"IgG Fc receptors","volume":"19","author":"Ravetch","year":"2001","journal-title":"Annu Rev Immunol"},{"key":"R24-15-20210227","doi-asserted-by":"crossref","first-page":"1209","DOI":"10.1002\/humu.20410","article-title":"BTKbase: the mutation database for X-Linked agammaglobulinemia","volume":"27","author":"Valiaho","year":"2006","journal-title":"Hum Mutat"},{"key":"R25-15-20210227","doi-asserted-by":"crossref","first-page":"200","DOI":"10.1111\/j.0105-2896.2005.00225.x","article-title":"Bruton's tyrosine kinase: cell biology, sequence conservation, mutation spectrum, siRNA modifications, and expression profiling","volume":"203","author":"Lindvall","year":"2005","journal-title":"Immun Rev"},{"key":"R26-15-20210227","doi-asserted-by":"crossref","first-page":"1776","DOI":"10.1056\/NEJM199706193362502","article-title":"Granulocyte colony-stimulating factor in severe chemotherapy-induced afebrile neutropenia","volume":"336","author":"Hartmann","year":"1997","journal-title":"N Engl J Med"}],"container-title":["Journal of Pediatric Hematology\/Oncology"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/www.ovid.com\/10.1097\/MPH.0b013e3181758947","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2026,8,6]],"date-time":"2026-08-06T17:51:35Z","timestamp":1786038695000},"score":1,"resource":{"primary":{"URL":"https:\/\/www.ovid.com\/00043426-200808000-00015"}},"subtitle":["A Case Report and Review of the Literature"],"short-title":[],"issued":{"date-parts":[[2008,8]]},"references-count":26,"journal-issue":{"issue":"8","published-print":{"date-parts":[[2008]]}},"URL":"https:\/\/doi.org\/10.1097\/mph.0b013e3181758947","relation":{},"ISSN":["1077-4114"],"issn-type":[{"value":"1077-4114","type":"print"}],"subject":[],"published":{"date-parts":[[2008,8]]}}}