{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,30]],"date-time":"2026-09-30T04:24:14Z","timestamp":1790742254569,"version":"4.1.0"},"reference-count":49,"publisher":"Oxford University Press (OUP)","issue":"5","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["J Neuropathol Exp Neurol"],"published-print":{"date-parts":[[2009,5]]},"DOI":"10.1097\/nen.0b013e31819fa6ba","type":"journal-article","created":{"date-parts":[[2009,5,21]],"date-time":"2009-05-21T22:57:23Z","timestamp":1242946643000},"page":"441-455","source":"Crossref","is-referenced-by-count":16,"title":["Impaired Expression of Ciliary Neurotrophic Factor in Charcot-Marie-Tooth Type 1A Neuropathy"],"prefix":"10.1093","volume":"68","author":[{"given":"Lucilla","family":"Nobbio","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Fulvia","family":"Fiorese","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Tiziana","family":"Vigo","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Michele","family":"Cilli","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Gianfranco","family":"Gherardi","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Marina","family":"Grandis","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Roberto Cosimo","family":"Melcangi","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Gianluigi","family":"Mancardi","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Michele","family":"Abbruzzese","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Angelo","family":"Schenone","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"286","published-online":{"date-parts":[[2009,5,1]]},"reference":[{"key":"2016030500323728000_68.5.441.1","doi-asserted-by":"publisher","DOI":"10.1038\/nrn1196"},{"key":"2016030500323728000_68.5.441.2","unstructured":"Dyck PJ Chance P Lebo R . Hereditary motor and sensory neuropathies. In Dyck PJ, Thomas PK, Griffin JW, et al, eds. Peripheral Neuropathy. 3rd ed. Philadelphia: Saunders, 1993"},{"key":"2016030500323728000_68.5.441.3","doi-asserted-by":"publisher","DOI":"10.1093\/brain\/123.7.1516"},{"key":"2016030500323728000_68.5.441.4","doi-asserted-by":"publisher","DOI":"10.1093\/brain\/122.8.1563"},{"key":"2016030500323728000_68.5.441.5","doi-asserted-by":"publisher","DOI":"10.1111\/j.1460-9568.2006.04666.x"},{"key":"2016030500323728000_68.5.441.6","doi-asserted-by":"publisher","DOI":"10.1038\/ncpneuro0583"},{"key":"2016030500323728000_68.5.441.7","doi-asserted-by":"publisher","DOI":"10.1038\/nm957"},{"key":"2016030500323728000_68.5.441.8","doi-asserted-by":"publisher","DOI":"10.1038\/nm1023"},{"key":"2016030500323728000_68.5.441.9","doi-asserted-by":"publisher","DOI":"10.1002\/ana.21026"},{"key":"2016030500323728000_68.5.441.10","doi-asserted-by":"publisher","DOI":"10.1002\/mus.1027"},{"key":"2016030500323728000_68.5.441.11","doi-asserted-by":"publisher","DOI":"10.1016\/j.mcn.2004.11.016"},{"key":"2016030500323728000_68.5.441.12","first-page":"825","article-title":"Expression profiling of sciatic nerve in a Charcot-Marie-Tooth disease type 1A mouse model","volume":"17","author":"Ten","year":"2005","journal-title":"J Neurosci Res"},{"key":"2016030500323728000_68.5.441.13","doi-asserted-by":"crossref","first-page":"5344","DOI":"10.1523\/JNEUROSCI.16-17-05344.1996","article-title":"A distinct pattern of trophic factor expression in myelin-deficient nerves of Trembler mice: Implications for trophic support by Schwann cells","volume":"16","author":"Friedman","year":"1996","journal-title":"J Neurosci"},{"key":"2016030500323728000_68.5.441.14","doi-asserted-by":"publisher","DOI":"10.1038\/345440a0"},{"key":"2016030500323728000_68.5.441.15","doi-asserted-by":"publisher","DOI":"10.1002\/glia.10221"},{"key":"2016030500323728000_68.5.441.16","doi-asserted-by":"publisher","DOI":"10.1038\/nm0602-620"},{"key":"2016030500323728000_68.5.441.17","doi-asserted-by":"crossref","first-page":"9221","DOI":"10.1523\/JNEUROSCI.22-21-09221.2002","article-title":"Ciliary neurotrophic factor (CNTF) enhances myelin formation: A novel role for CNTF and CNTF-related molecules","volume":"22","author":"Stankoff","year":"2002","journal-title":"J Neurosci"},{"key":"2016030500323728000_68.5.441.18","doi-asserted-by":"publisher","DOI":"10.1016\/S0896-6273(00)80128-2"},{"key":"2016030500323728000_68.5.441.19","doi-asserted-by":"publisher","DOI":"10.1038\/ng1195-274"},{"key":"2016030500323728000_68.5.441.20","doi-asserted-by":"crossref","first-page":"5351","DOI":"10.1523\/JNEUROSCI.16-17-05351.1996","article-title":"Impaired differentiation of Schwann cells in transgenic mice with increased PMP22 gene dosage","volume":"16","author":"Magyar","year":"1996","journal-title":"J Neurosci"},{"key":"2016030500323728000_68.5.441.21","doi-asserted-by":"publisher","DOI":"10.1083\/jcb.148.5.1021"},{"key":"2016030500323728000_68.5.441.22","doi-asserted-by":"publisher","DOI":"10.1016\/j.nbd.2004.02.007"},{"key":"2016030500323728000_68.5.441.23","doi-asserted-by":"publisher","DOI":"10.1002\/ana.1034"},{"key":"2016030500323728000_68.5.441.24","doi-asserted-by":"publisher","DOI":"10.1016\/0169-328X(91)90090-K"},{"key":"2016030500323728000_68.5.441.25","doi-asserted-by":"publisher","DOI":"10.1016\/0022-510X(91)90066-G"},{"key":"2016030500323728000_68.5.441.26","doi-asserted-by":"publisher","DOI":"10.1038\/342920a0"},{"key":"2016030500323728000_68.5.441.27","doi-asserted-by":"publisher","DOI":"10.1146\/annurev.immunol.15.1.797"},{"key":"2016030500323728000_68.5.441.28","doi-asserted-by":"publisher","DOI":"10.1073\/pnas.96.20.11458"},{"key":"2016030500323728000_68.5.441.29","doi-asserted-by":"publisher","DOI":"10.1126\/science.8390097"},{"key":"2016030500323728000_68.5.441.30","doi-asserted-by":"publisher","DOI":"10.1042\/bj3340297"},{"key":"2016030500323728000_68.5.441.31","doi-asserted-by":"crossref","first-page":"3507","DOI":"10.1523\/JNEUROSCI.10-11-03507.1990","article-title":"Survival effect of ciliary neurotrophic factor (CNTF) on chick embryonic motoneurons in culture: Comparison with other neurotrophic factors and cytokines","volume":"10","author":"Arakawa","year":"1990","journal-title":"J Neurosci"},{"key":"2016030500323728000_68.5.441.32","doi-asserted-by":"publisher","DOI":"10.1083\/jcb.118.1.139"},{"key":"2016030500323728000_68.5.441.33","doi-asserted-by":"publisher","DOI":"10.1016\/0959-4388(93)90157-T"},{"key":"2016030500323728000_68.5.441.34","doi-asserted-by":"crossref","first-page":"564","DOI":"10.1046\/j.1471-4159.1995.65020564.x","article-title":"Ciliary neurotrophic factor expression in Schwann cells is induced by axonal contact","volume":"65","author":"Lee","year":"1995","journal-title":"J Neurochem"},{"key":"2016030500323728000_68.5.441.35","doi-asserted-by":"publisher","DOI":"10.1083\/jcb.123.2.455"},{"key":"2016030500323728000_68.5.441.36","doi-asserted-by":"publisher","DOI":"10.1038\/365253a0"},{"key":"2016030500323728000_68.5.441.37","doi-asserted-by":"publisher","DOI":"10.1016\/0092-8674(92)90183-D"},{"key":"2016030500323728000_68.5.441.38","doi-asserted-by":"publisher","DOI":"10.1016\/j.brainresrev.2004.07.010"},{"key":"2016030500323728000_68.5.441.39","doi-asserted-by":"crossref","first-page":"4120","DOI":"10.1523\/JNEUROSCI.20-11-04120.2000","article-title":"Uncoupling of myelin assembly and Schwann cell differentiation by transgenic overexpression of peripheral myelin protein 22","volume":"20","author":"Niemann","year":"2000","journal-title":"J Neurosci"},{"key":"2016030500323728000_68.5.441.40","doi-asserted-by":"crossref","first-page":"443","DOI":"10.1002\/jnr.10133","article-title":"Proliferation of Schwann cells and regulation of cyclin D1 expression in an animal model of Charcot-Marie-Tooth disease type 1A","volume":"15","author":"Atanasoski","year":"2002","journal-title":"J Neurosci Res"},{"key":"2016030500323728000_68.5.441.41","first-page":"3351","article-title":"Constitutive activation of signal transducers and activators of transcription 3 correlates with cyclin D1 overexpression and may provide a novel prognostic marker in head and neck squamous cell carcinoma","volume":"15","author":"Masuda","year":"2002","journal-title":"Cancer Res"},{"key":"2016030500323728000_68.5.441.42","doi-asserted-by":"publisher","DOI":"10.1074\/jbc.M309304200"},{"key":"2016030500323728000_68.5.441.43","doi-asserted-by":"publisher","DOI":"10.1023\/A:1007628631985"},{"key":"2016030500323728000_68.5.441.44","doi-asserted-by":"publisher","DOI":"10.1097\/00005072-199608000-00007"},{"key":"2016030500323728000_68.5.441.45","doi-asserted-by":"publisher","DOI":"10.1002\/mus.1077"},{"key":"2016030500323728000_68.5.441.46","doi-asserted-by":"publisher","DOI":"10.1002\/mus.10074"},{"key":"2016030500323728000_68.5.441.47","doi-asserted-by":"publisher","DOI":"10.1016\/j.nmd.2007.06.006"},{"key":"2016030500323728000_68.5.441.48","doi-asserted-by":"publisher","DOI":"10.1212\/01.WNL.0000171978.70849.c5"},{"key":"2016030500323728000_68.5.441.49","doi-asserted-by":"publisher","DOI":"10.1002\/jnr.21388"}],"container-title":["Journal of Neuropathology &amp; Experimental Neurology"],"original-title":[],"language":"en","deposited":{"date-parts":[[2019,5,20]],"date-time":"2019-05-20T08:36:41Z","timestamp":1558341401000},"score":1,"resource":{"primary":{"URL":"https:\/\/academic.oup.com\/jnen\/article-lookup\/doi\/10.1097\/NEN.0b013e31819fa6ba"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2009,5]]},"references-count":49,"journal-issue":{"issue":"5","published-online":{"date-parts":[[2009,5,1]]},"published-print":{"date-parts":[[2009,5]]}},"alternative-id":["10.1097\/NEN.0b013e31819fa6ba"],"URL":"https:\/\/doi.org\/10.1097\/nen.0b013e31819fa6ba","relation":{},"ISSN":["0022-3069","1554-6578"],"issn-type":[{"value":"0022-3069","type":"print"},{"value":"1554-6578","type":"electronic"}],"subject":[],"published":{"date-parts":[[2009,5]]}}}