{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,21]],"date-time":"2026-10-21T07:45:12Z","timestamp":1792568712520,"version":"4.5.0"},"reference-count":35,"publisher":"Ovid Technologies (Wolters Kluwer Health)","issue":"12","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2017,12]]},"abstract":"<jats:p>Skin biopsies of 41 angioimmunoblastic T-cell lymphoma patients were retrospectively analyzed for the expression of follicular helper T-cell (TFH) markers, Epstein-Barr virus (EBV), and the presence of <jats:italic toggle=\"yes\">RHOA<\/jats:italic> (p.G17V) and <jats:italic toggle=\"yes\">IDH2<\/jats:italic> (p.R172K\/S) mutations using allele-specific polymerase chain reaction. We categorized cases into 4 distinctive patterns: (1) low-density lymphocytic perivascular infiltrates (n=11), (2) dense perivascular infiltrates with atypical cells and occasional inflammatory cells (n=13), (3) diffuse infiltrates reminiscent of angioimmunoblastic T-cell lymphoma (n=4), or (4) other aspects (n=13). Two EBV<jats:sup>+<\/jats:sup> and 2 plasmacytoid lymphoproliferative disorders were seen. We observed variable expression of TFH markers (CD10 [50%], BCLB6 [84%], PD1 [94%], CXCL13 [84%], and ICOS [97.5%]), and EBV<jats:sup>+<\/jats:sup> B-blasts (26%). A TFH phenotype was identified in 82% and 73%, respectively, of cases with the most challenging patterns 1 and 2. TFH markers and EBV can thus help for diagnosis and are detected in samples with low-density infiltrates. We found <jats:italic toggle=\"yes\">RHOA G17V<\/jats:italic> and <jats:italic toggle=\"yes\">IDH2 R172K\/S<\/jats:italic> mutations in the skin in 14\/18 (78%) and 3\/16 (19%) cases, respectively. The <jats:italic toggle=\"yes\">RHOA G17V<\/jats:italic> mutation was identified in a proportion of biopsies with patterns 1 and 2, which represent a diagnostic challenge. The <jats:italic toggle=\"yes\">RHOA G17V<\/jats:italic> mutation was detected both in the skin and lymph node (LN) biopsies in 7\/9 (64%) cases, and in only the skin or the LN of 1 sample each. The frequency of <jats:italic toggle=\"yes\">RHOA G17V<\/jats:italic> mutation was similar to that reported in LNs. It may represent a sensitive diagnostic marker in the skin, helpful in cases with low-density infiltrates.<\/jats:p>","DOI":"10.1097\/pas.0000000000000956","type":"journal-article","created":{"date-parts":[[2017,9,22]],"date-time":"2017-09-22T22:41:27Z","timestamp":1506120087000},"page":"1581-1592","source":"Crossref","is-referenced-by-count":28,"title":["Expression of TFH Markers and Detection of RHOA p.G17V and IDH2 p.R172K\/S Mutations in Cutaneous Localizations of Angioimmunoblastic T-Cell Lymphomas"],"prefix":"10.1097","volume":"41","author":[{"given":"Ariane","family":"Leclaire Alirkilicarslan","sequence":"first","affiliation":[{"name":"Pathology Department, Henri Mondor Hospital, Assistance Publique\u2014H\u00f4pitaux de Paris"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Aur\u00e9lie","family":"Dupuy","sequence":"additional","affiliation":[{"name":"INSERM U955 \u00e9quipe 9, Institut Mondor de Recherche Biom\u00e9dicale"},{"name":"Paris Est Creteil University 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