{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,1]],"date-time":"2026-08-01T09:47:15Z","timestamp":1785577635426,"version":"3.56.0"},"reference-count":51,"publisher":"Ovid Technologies (Wolters Kluwer Health)","issue":"4","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2009,4]]},"DOI":"10.1097\/pas.0b013e31818fbdff","type":"journal-article","created":{"date-parts":[[2009,5,21]],"date-time":"2009-05-21T10:01:25Z","timestamp":1242900085000},"page":"609-619","source":"Crossref","is-referenced-by-count":139,"title":["Melanotic Xp11 Translocation Renal Cancers"],"prefix":"10.1097","volume":"33","author":[{"given":"Pedram","family":"Argani","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Sebastian","family":"Aulmann","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Zarir","family":"Karanjawala","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Robert B.","family":"Fraser","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Marc","family":"Ladanyi","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Maria M.","family":"Rodriguez","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"276","reference":[{"key":"R1-16-20210131","doi-asserted-by":"crossref","first-page":"261","DOI":"10.1111\/j.1440-1827.2004.01617.x","article-title":"Heavily melanotic perivascular epithelioid clear cell tumor of the kidney","volume":"54","author":"Adachi","year":"2004","journal-title":"Pathol Int"},{"key":"R2-16-20210131","first-page":"2000","article-title":"Sternberg's Diagnostic Surgical Pathology","volume":"2","author":"Argani","year":"2004"},{"key":"R3-16-20210131","first-page":"37","article-title":"Pathology and Genetics of Tumors of the Urinary System & Male Genital Organs","author":"Argani","year":"2004"},{"key":"R4-16-20210131","doi-asserted-by":"crossref","first-page":"363","DOI":"10.1016\/j.cll.2005.01.008","article-title":"Translocation carcinomas of the kidney","volume":"25","author":"Argani","year":"2005","journal-title":"Clinics Lab Med"},{"key":"R5-16-20210131","doi-asserted-by":"crossref","first-page":"332","DOI":"10.1309\/EAEJTJGD5J4J3B4F","article-title":"The evolving story of renal translocation carcinomas","volume":"126","author":"Argani","year":"2006","journal-title":"Am J Clin Pathol"},{"key":"R6-16-20210131","doi-asserted-by":"crossref","first-page":"179","DOI":"10.1016\/S0002-9440(10)61684-7","article-title":"Primary renal neoplasms with the ASPL-TFE3 gene fusion of alveolar soft part sarcoma. A distinctive tumor entity previously included among renal cell carcinomas of children and adolescents","volume":"159","author":"Argani","year":"2001","journal-title":"Am J Pathol"},{"key":"R7-16-20210131","doi-asserted-by":"crossref","first-page":"2089","DOI":"10.1016\/S0002-9440(10)64680-9","article-title":"A distinctive pediatric renal neoplasm characterized by epithelioid morphology, basement membrane production, focal HMB45 immunoreactivity, and t(6; 11)(p21.1; q12) chromosome translocation","volume":"158","author":"Argani","year":"2001","journal-title":"Am J Pathol"},{"key":"R8-16-20210131","doi-asserted-by":"crossref","first-page":"1553","DOI":"10.1097\/00000478-200212000-00003","article-title":"PRCC-TFE3 renal carcinomas. Morphologic, immunohistochemical, ultrastructural, and molecular analysis of an entity associated with the t(X;1)(p11.2;q21)","volume":"26","author":"Argani","year":"2002","journal-title":"Am J Surg Pathol"},{"key":"R9-16-20210131","doi-asserted-by":"crossref","first-page":"750","DOI":"10.1097\/00000478-200306000-00005","article-title":"Aberrant nuclear immunoreactivity for TFE3 in neoplasms with TFE3 gene fusions: a sensitive and specific immunohistochemical assay","volume":"27","author":"Argani","year":"2003","journal-title":"Am J Surg Pathol"},{"key":"R10-16-20210131","doi-asserted-by":"crossref","first-page":"5374","DOI":"10.1038\/sj.onc.1206686","article-title":"Cloning of a novel CLTC-TFE3 gene fusion in pediatric renal adenocarcinoma with t(X;17)(p11.2;q23)","volume":"22","author":"Argani","year":"2003","journal-title":"Oncogene"},{"key":"R11-16-20210131","doi-asserted-by":"crossref","first-page":"230","DOI":"10.1097\/01.pas.0000146007.54092.37","article-title":"Renal carcinomas with the t(6;11)(p21;q12). Clinicopathologic features and demonstration of the specific Alpha-TFEB gene fusion by immunohistochemistry, RT-PCR, and DNA-PCR","volume":"29","author":"Argani","year":"2005","journal-title":"Am J Surg Pathol"},{"key":"R12-16-20210131","doi-asserted-by":"crossref","first-page":"1149","DOI":"10.1097\/PAS.0b013e318031ffff","article-title":"Xp11 translocation renal cell carcinoma in adults: expanded clinical, pathologic, and genetic spectrum","volume":"31","author":"Argani","year":"2007","journal-title":"Am J Surg Pathol"},{"key":"R13-16-20210131","doi-asserted-by":"crossref","first-page":"881","DOI":"10.1111\/j.1365-2559.2007.02693.x","article-title":"Detection of the ASPSCR1-TFE3 gene fusion in paraffin-embedded alveolar soft part sarcomas","volume":"50","author":"Aulmann","year":"2007","journal-title":"Histopathology"},{"key":"R14-16-20210131","doi-asserted-by":"crossref","first-page":"77","DOI":"10.1080\/003655902317259427","article-title":"Primary malignant melanoma of the kidney","volume":"36","author":"Bayazit","year":"2002","journal-title":"Scand J Urol Nephrol"},{"key":"R15-16-20210131","doi-asserted-by":"crossref","first-page":"194","DOI":"10.1016\/0090-4295(80)90420-3","article-title":"Hematuria and pleural effusion following parotid tumor","volume":"15","author":"Birkhoff","year":"1980","journal-title":"Urology"},{"key":"R16-16-20210131","doi-asserted-by":"crossref","first-page":"343","DOI":"10.1097\/00125480-199711000-00001","article-title":"The perivascular epithelioid cell and related lesions","volume":"4","author":"Bonetti","year":"1997","journal-title":"Adv Anat Pathol"},{"key":"R17-16-20210131","doi-asserted-by":"crossref","first-page":"656","DOI":"10.1097\/PAS.0b013e3181609914","article-title":"Renal translocation carcinomas. Clinicopathologic, immunohistochemical, and gene expression profiling analysis of 31 cases with a review of the literature","volume":"35","author":"Camparo","year":"2008","journal-title":"Am J Surg Pathol"},{"key":"R18-16-20210131","doi-asserted-by":"crossref","first-page":"273","DOI":"10.1097\/00125480-200109000-00004","article-title":"Diagnostic utility of microphthalmia transcription factor in malignant melanoma and other tumors","volume":"8","author":"Chang","year":"2001","journal-title":"Adv Anat Pathol"},{"key":"R21-16-20210131","doi-asserted-by":"crossref","first-page":"6051","DOI":"10.1073\/pnas.0931430100","article-title":"Cloning of an Alpha-TFEB fusion in renal tumors harboring the t(6;11)(p21;q13) chromosome translocation","volume":"100","author":"Davis","year":"2003","journal-title":"Proc Natl Acad Sci U S A"},{"key":"R22-16-20210131","doi-asserted-by":"crossref","first-page":"473","DOI":"10.1016\/j.ccr.2006.04.021","article-title":"Oncogenic MiTF dysregulation in clear cell sarcoma: defining the MiTF family of human cancers","volume":"9","author":"Davis","year":"2006","journal-title":"Cancer Cell"},{"key":"R23-16-20210131","doi-asserted-by":"crossref","first-page":"634","DOI":"10.1016\/S0022-5347(01)65236-4","article-title":"Clear cell melanoma of the renal pelvis presenting as a primary tumor","volume":"157","author":"Ehara","year":"1997","journal-title":"J Urol"},{"key":"R24-16-20210131","first-page":"221","article-title":"World Health Organization Classification of Tumors. Pathology and Genetics of Tumors of Soft Tissue and Bone","author":"Folpe","year":"2002"},{"key":"R25-16-20210131","doi-asserted-by":"crossref","first-page":"1558","DOI":"10.1097\/01.pas.0000173232.22117.37","article-title":"Perivascular epithelioid cell neoplasms of soft tissue and gynecologic origin. A clinicopathologic study of 26 cases and review of the literature","volume":"29","author":"Folpe","year":"2005","journal-title":"Am J Surg Pathol"},{"key":"R26-16-20210131","doi-asserted-by":"crossref","first-page":"812","DOI":"10.1016\/S0022-5347(17)41823-4","article-title":"Malignant melanoma of the renal pelvis presenting as a primary tumor","volume":"140","author":"Frasier","year":"1988","journal-title":"J Urol"},{"key":"R27-16-20210131","doi-asserted-by":"crossref","first-page":"1887","DOI":"10.1016\/S0022-5347(01)67341-5","article-title":"Solitary renal melanoma? A case with long survival after initial treatment","volume":"153","author":"Fujimoto","year":"1995","journal-title":"J Urol"},{"key":"R28-16-20210131","doi-asserted-by":"crossref","first-page":"117","DOI":"10.1038\/nature03664","article-title":"Integrative genomic analyses identify MiTF as a lineage survival oncogene amplified in malignant melanoma","volume":"436","author":"Garraway","year":"2005","journal-title":"Nature"},{"key":"R30-16-20210131","doi-asserted-by":"crossref","first-page":"788","DOI":"10.1159\/000331848","article-title":"Cytology of pigmented renal cell carcinoma","volume":"42","author":"Hirokawa","year":"1998","journal-title":"Acta Cytol"},{"key":"R31-16-20210131","doi-asserted-by":"crossref","first-page":"75","DOI":"10.1111\/j.1365-2559.2005.02316.x","article-title":"PEComa: what do we know so far?","volume":"48","author":"Hornick","year":"2006","journal-title":"Histopathology"},{"key":"R32-16-20210131","first-page":"1","article-title":"Sclerosing PEComa. Clinicopathologic analysis of a distinctive variant with a predilection for the retroperitoneum","volume":"00","author":"Hornick","year":"2008","journal-title":"Am J Surg Pathol"},{"key":"R33-16-20210131","doi-asserted-by":"crossref","first-page":"374","DOI":"10.1016\/j.anndiagpath.2003.09.006","article-title":"Triple synchronous neoplasms in one kidney: report of a case and review of the literature","volume":"7","author":"Jun","year":"2003","journal-title":"Ann Diagn Pathol"},{"key":"R34-16-20210131","doi-asserted-by":"crossref","first-page":"350","DOI":"10.1097\/00000478-199503000-00013","article-title":"Pigmented renal cell carcinoma","volume":"19","author":"Kamishima","year":"1995","journal-title":"Am J Surg Pathol"},{"key":"R35-16-20210131","doi-asserted-by":"crossref","first-page":"1661","DOI":"10.1093\/hmg\/ddg178","article-title":"Upregulation of the transcription factor TFEB in t(6;11)(p21;q13)-positive renal cell carcinomas due to promoter substitution","volume":"12","author":"Kuiper","year":"2003","journal-title":"Hum Mol Genet"},{"key":"R36-16-20210131","doi-asserted-by":"crossref","first-page":"265","DOI":"10.1097\/00000478-199802000-00018","article-title":"Pigmented (\u201cBlack\u201d) extraadrenal paraganglioma","volume":"22","author":"Lack","year":"1998","journal-title":"Am J Surg Pathol"},{"key":"R37-16-20210131","doi-asserted-by":"crossref","first-page":"48","DOI":"10.1038\/sj.onc.1204074","article-title":"The der t(X;17)(p11.2;q25) of human alveolar soft part sarcoma fuses the TFE3 transcription factor gene to ASPL, a novel gene at 17q25","volume":"20","author":"Ladanyi","year":"2001","journal-title":"Oncogene"},{"key":"R38-16-20210131","doi-asserted-by":"crossref","first-page":"233","DOI":"10.1053\/hupa.2001.22009","article-title":"Pigmented renal clear cell carcinoma with melanocytic differentiation","volume":"32","author":"Lei","year":"2001","journal-title":"Hum Pathol"},{"key":"R39-16-20210131","doi-asserted-by":"crossref","first-page":"610","DOI":"10.5858\/2002-126-0610-OLA","article-title":"Oncocytoma-like angiomyolipoma. A clinicopathologic and immunohistochemical study of 2 cases","volume":"126","author":"Martignoni","year":"2002","journal-title":"Arch Pathol Lab Med"},{"key":"R40-16-20210131","doi-asserted-by":"crossref","first-page":"36","DOI":"10.1097\/PAP.0b013e31802e0dc4","article-title":"Perivascular epithelioid cell tumor (PEComa) in the genitourinary tract","volume":"14","author":"Martignoni","year":"2007","journal-title":"Adv Anat Pathol"},{"key":"R41-16-20210131","doi-asserted-by":"crossref","first-page":"157","DOI":"10.1159\/000108296","article-title":"Molecular mechanisms underlying the MiT translocation subgroup of renal cell carcinomas","volume":"118","author":"Medendorp","year":"2007","journal-title":"Cytogenet Genome Res"},{"key":"R42-16-20210131","doi-asserted-by":"crossref","first-page":"785","DOI":"10.1097\/00000478-200006000-00003","article-title":"Primary malignant melanoma of the urethra. A clinicopathologic analysis of 15 cases","volume":"24","author":"Oliva","year":"2000","journal-title":"Am J Surg Pathol"},{"key":"R43-16-20210131","doi-asserted-by":"crossref","first-page":"349","DOI":"10.1309\/98YE9E442AR7LX2X","article-title":"Pediatric renal cell carcinoma. Clinical, pathologic, and molecular abnormalities associated with the members of the MiT transcription factor family","volume":"126","author":"Ramphal","year":"2006","journal-title":"Am J Clin Pathol"},{"key":"R44-16-20210131","doi-asserted-by":"crossref","first-page":"516","DOI":"10.1053\/hp.2000.6717","article-title":"Malignant pigmented clear cell epithelioid tumor of the kidney: clear cell (\u201csugar\u201d) tumor versus malignant melanoma","volume":"31","author":"Ribalta","year":"2000","journal-title":"Hum Pathol"},{"key":"R45-16-20210131","doi-asserted-by":"crossref","first-page":"202","DOI":"10.1002\/pbc.20305","article-title":"Lack of response of a metastatic renal perivascular epithelial cell tumor (PEComa) to successive courses of DTIC based-therapy and imatinib mesylate","volume":"45","author":"Rigby","year":"2005","journal-title":"Pediatr Blood Cancer"},{"key":"R46-16-20210131","doi-asserted-by":"crossref","first-page":"16","DOI":"10.1177\/1066896907309733","article-title":"PEComa: Another member of the MiT tumor family?","volume":"16","author":"Righi","year":"2008","journal-title":"Int J Surg Pathol"},{"key":"R47-16-20210131","doi-asserted-by":"crossref","first-page":"589","DOI":"10.1097\/00000478-199905000-00014","article-title":"Clear cell sarcoma of soft parts: report of a case primary in the kidney with cytogenetic confirmation","volume":"23","author":"Rubin","year":"1999","journal-title":"Am J Surg Pathol"},{"key":"R48-16-20210131","doi-asserted-by":"crossref","first-page":"2533","DOI":"10.1016\/S0022-5347(05)64188-2","article-title":"Malignant clear cell \u201csugar\u201d tumor of the kidney: clear cell variant of epithelioid angiomyolipoma","volume":"168","author":"Saito","year":"2002","journal-title":"J Urol"},{"key":"R49-16-20210131","doi-asserted-by":"crossref","first-page":"229","DOI":"10.1177\/106689690301100314","article-title":"Oncocytic angiomyolipoma of the kidney: a case report","volume":"11","author":"Sironi","year":"2003","journal-title":"Int J Surg Pathol"},{"key":"R50-16-20210131","doi-asserted-by":"crossref","first-page":"859","DOI":"10.1016\/S0022-5347(17)49927-7","article-title":"Malignant melanoma of the genitourinary tract","volume":"132","author":"Stein","year":"1984","journal-title":"J Urol"},{"key":"R51-16-20210131","doi-asserted-by":"crossref","first-page":"94","DOI":"10.1111\/j.1442-2042.1997.tb00149.x","article-title":"Malignant melanoma of the kidney presenting as a primary tumor","volume":"4","author":"Tajima","year":"1997","journal-title":"Int J Urol"},{"key":"R52-16-20210131","first-page":"496","article-title":"Does alveolar soft part sarcoma exhibit skeletal muscle differentiation? An immunocytochemical and biochemical study of myogenic regulatory protein expression","volume":"9","author":"Wang","year":"1996","journal-title":"Mod Pathol"},{"key":"R53-16-20210131","doi-asserted-by":"crossref","first-page":"66","DOI":"10.1016\/0090-4295(82)90050-4","article-title":"Malignant melanoma presenting as renal tumor","volume":"19","author":"Wirtshafter","year":"1982","journal-title":"Urology"},{"key":"R54-16-20210131","doi-asserted-by":"crossref","first-page":"330","DOI":"10.1016\/j.anndiagpath.2005.04.003","article-title":"C-kit-positive metastatic malignant pigmented clear cell epithelioid tumor arising from the kidney in a child without tuberous sclerosis","volume":"9","author":"Yu","year":"2005","journal-title":"Ann Diagn Pathol"}],"container-title":["American Journal of Surgical Pathology"],"original-title":[],"language":"en","link":[{"URL":"http:\/\/journals.lww.com\/00000478-200904000-00016","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2021,4,10]],"date-time":"2021-04-10T07:04:18Z","timestamp":1618038258000},"score":1,"resource":{"primary":{"URL":"https:\/\/journals.lww.com\/00000478-200904000-00016"}},"subtitle":["A Distinctive Neoplasm With Overlapping Features of PEComa, Carcinoma, and Melanoma"],"short-title":[],"issued":{"date-parts":[[2009,4]]},"references-count":51,"journal-issue":{"issue":"4","published-print":{"date-parts":[[2009]]}},"URL":"https:\/\/doi.org\/10.1097\/pas.0b013e31818fbdff","relation":{},"ISSN":["0147-5185"],"issn-type":[{"value":"0147-5185","type":"print"}],"subject":[],"published":{"date-parts":[[2009,4]]}}}