{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,6,12]],"date-time":"2026-06-12T12:18:04Z","timestamp":1781266684186,"version":"3.54.1"},"reference-count":18,"publisher":"Ovid Technologies (Wolters Kluwer Health)","issue":"9","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Pediatr Emer Care"],"published-print":{"date-parts":[[2018,9]]},"abstract":"<jats:title>Abstract<\/jats:title>\n          <jats:p>An intracranial bleed with a midline shift is a potentially life-threatening clinical condition. We present the unusual case of a 13-year-old boy with sickle cell disease who had numerous emergency department visits for a scalp hematoma and was subsequently determined to have subdural and epidural hematomas with midline shift, associated with a skull bone infarction. We review the pathophysiology of this unusual condition and emphasize the importance of including it in the differential diagnosis of any child with sickle cell anemia presenting with a nontraumatic scalp hematoma.<\/jats:p>","DOI":"10.1097\/pec.0000000000001295","type":"journal-article","created":{"date-parts":[[2017,9,26]],"date-time":"2017-09-26T18:22:25Z","timestamp":1506450145000},"page":"e168-e170","source":"Crossref","is-referenced-by-count":9,"title":["A Teenager With Sickle Cell Disease and Scalp Swelling"],"prefix":"10.1097","volume":"34","author":[{"given":"Courtney E.","family":"Nelson","sequence":"first","affiliation":[{"name":"Division of Emergency Medicine, The Children's Hospital of Philadelphia; and"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Richard J.","family":"Scarfone","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"276","reference":[{"key":"bib3-20230930","doi-asserted-by":"crossref","first-page":"195","DOI":"10.1542\/pir.33.5.195","article-title":"Sickle cell disease","volume":"33","year":"2012","journal-title":"Pediatr Rev"},{"key":"bib4-20230930","doi-asserted-by":"crossref","first-page":"536","DOI":"10.1177\/000992288702601009","article-title":"Proptosis, skull infarction, and retro-orbital and epidural hematomas in a child with sickle cell disease","volume":"26","year":"1987","journal-title":"Clin Pediatr (Phila)"},{"key":"bib5-20230930","doi-asserted-by":"crossref","first-page":"532","DOI":"10.3171\/2009.7.PEDS09219","article-title":"A \u201cneurosurgical crisis\u201d of sickle cell disease","volume":"4","year":"2009","journal-title":"J Neurosurg Pediatr"},{"key":"bib6-20230930","doi-asserted-by":"crossref","first-page":"413","DOI":"10.1097\/00043426-199611000-00017","article-title":"Skull infarction and epidural hematomas in a patient with sickle cell anemia","volume":"18","year":"1996","journal-title":"J Pediatr Hematol Oncol"},{"key":"bib7-20230930","doi-asserted-by":"crossref","first-page":"595","DOI":"10.1016\/j.ajo.2008.05.041","article-title":"Orbital infarction in sickle cell disease","volume":"146","year":"2008","journal-title":"Am J Ophthalmol"},{"key":"bib8-20230930","doi-asserted-by":"crossref","first-page":"189","DOI":"10.1016\/j.jaapos.2013.11.011","article-title":"Orbital compression syndrome complicated by epidural hematoma and wide cephalohematoma in a patient with sickle cell disease","volume":"18","year":"2014","journal-title":"J AAPOS"},{"key":"bib9-20230930","doi-asserted-by":"crossref","first-page":"128","DOI":"10.1016\/j.neucir.2013.08.003","article-title":"Non-traumatic spontaneous acute epidural hematoma in a patient with sickle cell disease","volume":"25","year":"2014","journal-title":"Neurocirugia (Astur)"},{"key":"bib10-20230930","doi-asserted-by":"crossref","first-page":"407","DOI":"10.1007\/s00701-003-0214-z","article-title":"Are spontaneous epidural haematoma in sickle cell disease a rare complication? 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