{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,7]],"date-time":"2026-08-07T16:18:11Z","timestamp":1786119491918,"version":"build-2736575974"},"reference-count":14,"publisher":"Ovid Technologies (Wolters Kluwer Health)","issue":"2","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2010,3]]},"DOI":"10.1097\/scs.0b013e3181cfa7f0","type":"journal-article","created":{"date-parts":[[2010,3,20]],"date-time":"2010-03-20T03:23:37Z","timestamp":1269055417000},"page":"414-418","source":"Crossref","is-referenced-by-count":14,"title":["Management of Craniofacial Hyperostosis in Proteus Syndrome"],"prefix":"10.1097","volume":"21","author":[{"given":"Yoshiaki","family":"Sakamoto","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Hideo","family":"Nakajima","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Kazuo","family":"Kishi","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Ruka","family":"Shimizu","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Tatsuo","family":"Nakajima","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"276","reference":[{"key":"R1-30-20210219","first-page":"291","article-title":"A newly recognized hamartomatous syndrome.","volume":"15","author":"Cohen","year":"1979","journal-title":"Birth Defects Orig Artic Ser"},{"key":"R2-30-20210219","doi-asserted-by":"crossref","first-page":"5","DOI":"10.1007\/BF00661895","article-title":"The Proteus syndrome: partial gigantism of the hands and\/or feet, nevi, hemihypertrophy, subcutaneous tumors, macrocephaly or other skull anomalies and possible growth and visceral affections.","volume":"140","author":"Wiedemann","year":"1983","journal-title":"Eur J Pediatr"},{"key":"R3-30-20210219","doi-asserted-by":"crossref","first-page":"38","DOI":"10.1002\/ajmg.c.30063","article-title":"Proteus syndrome: an update.","volume":"137C","author":"Cohen","year":"2005","journal-title":"Am J Med Genet C Semin Med Genet"},{"key":"R4-30-20210219","doi-asserted-by":"crossref","first-page":"111","DOI":"10.1002\/ajmg.a.30327","article-title":"Reassessment of the Proteus syndrome literature: application of diagnostic criteria to published cases.","volume":"130A","author":"Turner","year":"2004","journal-title":"AM J Med Genet"},{"key":"R5-30-20210219","first-page":"260","article-title":"Understanding Proteus syndrome, unmasking the elephant man, and stemming elephant fever.","volume":"1","author":"Cohen","year":"1988","journal-title":"Neurofibromatosis"},{"key":"R6-30-20210219","first-page":"667","article-title":"Musculoskeletal manifestations of Proteus syndrome: report of two cases with literature review.","volume":"12","author":"Stricker","year":"1992","journal-title":"J Pediatr Orthop"},{"key":"R7-30-20210219","doi-asserted-by":"crossref","first-page":"151","DOI":"10.1097\/00001665-199503000-00014","article-title":"Proteus syndrome: a newly recognized hamartomatous syndrome with significant craniofacial dysmorphology.","volume":"6","author":"Tattelbaum","year":"1995","journal-title":"J Craniofac Surg"},{"key":"R8-30-20210219","doi-asserted-by":"crossref","first-page":"234","DOI":"10.1002\/1096-8628(20000731)93:3<234::AID-AJMG15>3.0.CO;2-9","article-title":"Multiple meningiomas, craniofacial hyperostosis and retinal abnormalities in Proteus syndrome.","volume":"93","author":"Gilbert-Barness","year":"2000","journal-title":"Am J Med Genet"},{"key":"R9-30-20210219","doi-asserted-by":"crossref","first-page":"175","DOI":"10.1097\/00001665-200601000-00034","article-title":"Surgical treatment of an unusual patient with Proteus syndrome.","volume":"17","author":"Ali","year":"2006","journal-title":"J Craniofac Surg"},{"key":"R10-30-20210219","doi-asserted-by":"crossref","first-page":"391","DOI":"10.1016\/j.jcms.2004.06.007","article-title":"Craniofacial hyperotoses in Proteus syndrome-a case report.","volume":"32","author":"Adolphs","year":"2002","journal-title":"J Cranio Maxillo Surg"},{"key":"R11-30-20210219","doi-asserted-by":"crossref","first-page":"233","DOI":"10.1597\/1545-1569(2002)039<0233:CADMOP>2.0.CO;2","article-title":"Craniofacial and dental manifestations of Proteus syndrome: a case report.","volume":"39","author":"Becktor","year":"2002","journal-title":"Cleft Palate Craniofac J"},{"key":"R12-30-20210219","doi-asserted-by":"crossref","first-page":"645","DOI":"10.1002\/ajmg.1320470514","article-title":"Proteus syndrome: clinical evidence for somatic mosaicism and selective review.","volume":"47","author":"Cohen","year":"1993","journal-title":"Am J Med Genet"},{"key":"R13-30-20210219","doi-asserted-by":"crossref","first-page":"87","DOI":"10.1002\/ajmg.1320270110","article-title":"Proteus syndrome in Southern Africa: natural history and clinical manifestations in six individuals.","volume":"27","author":"Viljoen","year":"1987","journal-title":"Am J Med Genet"},{"key":"R14-30-20210219","doi-asserted-by":"crossref","first-page":"283","DOI":"10.1002\/ajmg.1320350228","article-title":"Proteus syndrome: course of a severe case.","volume":"35","author":"Malamitsi-Puchner","year":"1990","journal-title":"Am J Med Genet"}],"container-title":["Journal of Craniofacial Surgery"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/www.ovid.com\/10.1097\/SCS.0b013e3181cfa7f0","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2026,8,6]],"date-time":"2026-08-06T18:17:27Z","timestamp":1786040247000},"score":1,"resource":{"primary":{"URL":"https:\/\/www.ovid.com\/00001665-201003000-00030"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2010,3]]},"references-count":14,"journal-issue":{"issue":"2","published-print":{"date-parts":[[2010]]}},"URL":"https:\/\/doi.org\/10.1097\/scs.0b013e3181cfa7f0","relation":{},"ISSN":["1049-2275"],"issn-type":[{"value":"1049-2275","type":"print"}],"subject":[],"published":{"date-parts":[[2010,3]]}}}